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Clinical Biochemistry II
Mid. II
Q1. Put (√ ) or ( X ) , Correct ( X ) one.
1. Isoleucine produces acetyl CoA and acetoacetyl CoA and thus, classified as
glucogenic a.à . ( )
2. In Cystinuria , Ion exchange chromatography shows abnormal blood a.à pattern and
normal level of basic a.à in urine. ( )
3. PKU occur due to deficiency of enzyme L- Phenylalanine transaminase. (
4. Albinism is due to reduced activity of tyrosinase enzyme. (
5. Bile acid and bile salts are the same . (
)
)
)
6. ALP is found in a number of tissues , but its used most often in the clinical
diagnosis of kidney and liver. ( )
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Q2. Fill in the Blanks:
1. Branched Chain a.à are ………………. , ………………….. and …………………..
The catabolism of these compounds initiate in ………………… and yields NADH
and FADH2
2.The main neurological problems in Maple Syrup Urine Disease are due to poor
formation of ………………. In the ……………………………..
3. Sharing in ………………………..….. and ………………………………………
are some of the a.à functions.
4. Because of …………………… of Phenylalanine prevents ………………………,
early detection of PKU has been emphasized.
5. Tyrosinosis occur due to reduced activity of ……………………………………….
as well as reduced ……………………………………………………………………. .
6. The only manifestation of Alkaptouria early in life is the …………………………..
………………………………………………………………………………………….
Q3. Compare between Renal Aminoaciduria and Over flow Aminoaciduria .
GOOD LUCK