Urea cycle defects and other metabolic emergencies
... – Symptoms independents of intercurrent events or nutritional intake – some neonatal presentations, but most less acute than other disorders – Includes lysosomal storage disorders (sphingolipidoses, mucopolysaccharidoses, cystinosis), peroxysomal disorders (Zellweger, x-ALD, Refsum, etc), congenital ...
... – Symptoms independents of intercurrent events or nutritional intake – some neonatal presentations, but most less acute than other disorders – Includes lysosomal storage disorders (sphingolipidoses, mucopolysaccharidoses, cystinosis), peroxysomal disorders (Zellweger, x-ALD, Refsum, etc), congenital ...
Active Transport of Amino Acids by Membrane
... T 967), and NADH oxidation may not be coupled with oxidative phosphorylation (Henipfling & Vishniac, 1965 ; Johnson & Abraham, I 969). However, Tlziobacillus nea/-’olitanus and Thiobacillus thioparus possess high concentrations of the enzymes of carbohydrate metabolism (Johnson & Abraham, 1969; Mati ...
... T 967), and NADH oxidation may not be coupled with oxidative phosphorylation (Henipfling & Vishniac, 1965 ; Johnson & Abraham, I 969). However, Tlziobacillus nea/-’olitanus and Thiobacillus thioparus possess high concentrations of the enzymes of carbohydrate metabolism (Johnson & Abraham, 1969; Mati ...
The Origin of the Genetic Code
... represent more than one amino acid. Of course, it is known that mutations can produce errors in the translation mechanism and so make certain codons ambiguous, but it is not known whether ambiguity occurs "normally". Again in what follows I shall assume that this is not usually the case for present- ...
... represent more than one amino acid. Of course, it is known that mutations can produce errors in the translation mechanism and so make certain codons ambiguous, but it is not known whether ambiguity occurs "normally". Again in what follows I shall assume that this is not usually the case for present- ...
Krebs Cycle - cloudfront.net
... Any form of reproduction of this book in any format or medium, in whole or in sections must include the referral attribution link http://www.ck12.org/saythanks (placed in a visible location) in addition to the following terms. Except as otherwise noted, all CK-12 Content (including CK-12 Curriculum ...
... Any form of reproduction of this book in any format or medium, in whole or in sections must include the referral attribution link http://www.ck12.org/saythanks (placed in a visible location) in addition to the following terms. Except as otherwise noted, all CK-12 Content (including CK-12 Curriculum ...
Inhibitors are structural analogs of true substrate
... enzyme of tricarboxylic acid cycle participates in reaction of substrate phosphorylation? In a patient are manifested symptoms of intoxication with arsenic compounds. What metabolic process is damaged taking into account that arsen containing substances inactivate lipoic acid? ...
... enzyme of tricarboxylic acid cycle participates in reaction of substrate phosphorylation? In a patient are manifested symptoms of intoxication with arsenic compounds. What metabolic process is damaged taking into account that arsen containing substances inactivate lipoic acid? ...
Arabidopsis Branched-Chain Aminotransferase 3
... From the progeny of both wild-type and mutant plants, levels of free amino acids were measured in rosette leaves of about 3-week-old plants and in seeds (data not shown). In the latter no significant differences were observed in the levels of free amino acids. This also holds true for most amino aci ...
... From the progeny of both wild-type and mutant plants, levels of free amino acids were measured in rosette leaves of about 3-week-old plants and in seeds (data not shown). In the latter no significant differences were observed in the levels of free amino acids. This also holds true for most amino aci ...
Carbohydrate Metabolism
... by EM pathways is called “glycolysis”. Glycolysis occurs in all tissues. b- HMP shunt: An alternative pathway for oxidation of glucose. It is not meant for energy. The pathway provides : (1) NADPH which is used for reductive synthesis. (2) Pentoses which is used for nucleic acids synthesis. This pat ...
... by EM pathways is called “glycolysis”. Glycolysis occurs in all tissues. b- HMP shunt: An alternative pathway for oxidation of glucose. It is not meant for energy. The pathway provides : (1) NADPH which is used for reductive synthesis. (2) Pentoses which is used for nucleic acids synthesis. This pat ...
File
... 52) Brown fat cells produce a protein called thermogenin in their mitochondrial inner membrane. Thermogenin is a channel for facilitated transport of protons across the membrane. What will occur in the brown fat cells when they produce thermogenin? A) ATP synthesis and heat generation will both dec ...
... 52) Brown fat cells produce a protein called thermogenin in their mitochondrial inner membrane. Thermogenin is a channel for facilitated transport of protons across the membrane. What will occur in the brown fat cells when they produce thermogenin? A) ATP synthesis and heat generation will both dec ...
(C) Chronic peripheral neuropathy
... deficiency (45 cases of "acute" peripheral neuropathy and 1 case of lymphoepithelioma with associated cachexia), and (b) 22 cases associated with an elevation in temperature. The first group is readily explained by the fact that thiamin, or more particularly thiamin pyrophosphate, is necessary for t ...
... deficiency (45 cases of "acute" peripheral neuropathy and 1 case of lymphoepithelioma with associated cachexia), and (b) 22 cases associated with an elevation in temperature. The first group is readily explained by the fact that thiamin, or more particularly thiamin pyrophosphate, is necessary for t ...
The Minimal Nutritional Requirements of Organisms
... strains of pertussis were examined for their minimal nutritional requirements in defined media. All strains showed an absolute requirement for nicotinic acid and no other vitamin was required for growth. Amino acids were essential for parapertussis and pertussis, but bronchiseptica would grow in eit ...
... strains of pertussis were examined for their minimal nutritional requirements in defined media. All strains showed an absolute requirement for nicotinic acid and no other vitamin was required for growth. Amino acids were essential for parapertussis and pertussis, but bronchiseptica would grow in eit ...
The Photoassimilation of Organic Compounds by
... The blue-green algae are a ubiquitous group of procaryotic micro-organisms which grow photosynthetically and, unlike the photosynthetic bacteria, produce oxygen. Apart from studies on their photosynthetic activities and, with certain species, also on their nitrogen-fixing activities, surprisingly fe ...
... The blue-green algae are a ubiquitous group of procaryotic micro-organisms which grow photosynthetically and, unlike the photosynthetic bacteria, produce oxygen. Apart from studies on their photosynthetic activities and, with certain species, also on their nitrogen-fixing activities, surprisingly fe ...
Stereochemical imperative in enzymic decarboxylations
... Isolation of Acetone from the Coupled Enzymatic Reaction and Its Conversion to Acetate. 3-Hydroxybutyrate dehydrogenase (3-HBDH) is known to catalyze the oxidation of only 3(R)-hydroxybutyrate to acetoacetate." Therefore, as the cis tritiation introduced label at the 2-position of hydroxybutyrate wi ...
... Isolation of Acetone from the Coupled Enzymatic Reaction and Its Conversion to Acetate. 3-Hydroxybutyrate dehydrogenase (3-HBDH) is known to catalyze the oxidation of only 3(R)-hydroxybutyrate to acetoacetate." Therefore, as the cis tritiation introduced label at the 2-position of hydroxybutyrate wi ...
The Photoassimilation of Organic Compounds by Autotrophic Blue
... The blue-green algae are a ubiquitous group of procaryotic micro-organisms which grow photosynthetically and, unlike the photosynthetic bacteria, produce oxygen. Apart from studies on their photosynthetic activities and, with certain species, also on their nitrogen-fixing activities, surprisingly fe ...
... The blue-green algae are a ubiquitous group of procaryotic micro-organisms which grow photosynthetically and, unlike the photosynthetic bacteria, produce oxygen. Apart from studies on their photosynthetic activities and, with certain species, also on their nitrogen-fixing activities, surprisingly fe ...
E. Transport of certain drugs
... Nucleic acids are required for the storage and expression of genetic information. There are two chemically distinct types of nucleic acids: deoxyribonucleic acid (DNA) and ribonucleic acid (RNA). DNA is present not only in chromosomes in the nucleus of eukaryotic organisms, but also in mitochondria ...
... Nucleic acids are required for the storage and expression of genetic information. There are two chemically distinct types of nucleic acids: deoxyribonucleic acid (DNA) and ribonucleic acid (RNA). DNA is present not only in chromosomes in the nucleus of eukaryotic organisms, but also in mitochondria ...
Lactic Acid Bacteria
... From sugars occurring in foods, hexose is most often the substrate for lactic acid bacteria. The end-product of fermentation of glucose under normal conditions (excess sugar and limited access of oxygen) is lactic acid. This means that homofermentative lactic acid bacteria theoretically produce two ...
... From sugars occurring in foods, hexose is most often the substrate for lactic acid bacteria. The end-product of fermentation of glucose under normal conditions (excess sugar and limited access of oxygen) is lactic acid. This means that homofermentative lactic acid bacteria theoretically produce two ...
Slide 1
... 6.9 The citric acid cycle completes the oxidation of organic molecules, generating many NADH and FADH2 molecules The citric acid cycle – is also called the Krebs cycle (after the German-British researcher Hans Krebs, who worked out much of this pathway in the 1930s), – completes the oxidation of ...
... 6.9 The citric acid cycle completes the oxidation of organic molecules, generating many NADH and FADH2 molecules The citric acid cycle – is also called the Krebs cycle (after the German-British researcher Hans Krebs, who worked out much of this pathway in the 1930s), – completes the oxidation of ...
Murine model of obesity-induced type II diabetes by
... altered in the skeletal muscle and the brain in the transgenic mice. Further PPP1R3G overexpression reduces hepatic triglyceride in the fed state (15). 2. Function of GADD34 in metabolism. PPP1R15A has been extensively studied as GADD34. Because GADD34 has multiple substrate-targeting domains (19), ...
... altered in the skeletal muscle and the brain in the transgenic mice. Further PPP1R3G overexpression reduces hepatic triglyceride in the fed state (15). 2. Function of GADD34 in metabolism. PPP1R15A has been extensively studied as GADD34. Because GADD34 has multiple substrate-targeting domains (19), ...
Free Amino Acid and Reducing Sugar Composition of Pandan
... samples added with reducing sugars added. The volatile 4-vinylphenol has medicinal and phenolic aroma characteristic with the odor threshold of 10 ppb. It is possible that high amounts of free amino acid present in the mixture could lead to an offflavor. The concentrations of 4-vinylphenol in the sa ...
... samples added with reducing sugars added. The volatile 4-vinylphenol has medicinal and phenolic aroma characteristic with the odor threshold of 10 ppb. It is possible that high amounts of free amino acid present in the mixture could lead to an offflavor. The concentrations of 4-vinylphenol in the sa ...
Print - Circulation Research
... and aspartate-glutamate exchange carriers, labeled I and II, respectively, are located in the inner mitochondrial membrane. Two key metabolic branch points at citrate synthetase and a-ketoglutarate dehydrogenase are identified by asterisks. By partitioning total metabolic flux between the malate-asp ...
... and aspartate-glutamate exchange carriers, labeled I and II, respectively, are located in the inner mitochondrial membrane. Two key metabolic branch points at citrate synthetase and a-ketoglutarate dehydrogenase are identified by asterisks. By partitioning total metabolic flux between the malate-asp ...
Plant and Soil
... with the organic acids utilization mutants will show some evidence supporting the repression hypothesis. Cells grown on any substrate had glucosedependent 02 consumption, which support the previous observation indicating the presence of a constitutive glucose transport system in R. meliloti (Theodor ...
... with the organic acids utilization mutants will show some evidence supporting the repression hypothesis. Cells grown on any substrate had glucosedependent 02 consumption, which support the previous observation indicating the presence of a constitutive glucose transport system in R. meliloti (Theodor ...
Citrate Cycle Supplemental Reading Key Concepts
... considered the "hub" of cellular metabolism because it not only links the oxidation of metabolic fuels (carbohydrate, fatty acids and proteins) to ATP synthesis, but it also provides shared metabolites for numerous other metabolic pathways as shown in figure 1. Unlike glycolysis which occurs in the ...
... considered the "hub" of cellular metabolism because it not only links the oxidation of metabolic fuels (carbohydrate, fatty acids and proteins) to ATP synthesis, but it also provides shared metabolites for numerous other metabolic pathways as shown in figure 1. Unlike glycolysis which occurs in the ...
Bio426Lecture28Apr10
... Rhizobium is attracted to legumes through signaling by isoflavanoids released from roots. ...
... Rhizobium is attracted to legumes through signaling by isoflavanoids released from roots. ...
CELLULAR RESPIRATION Getting energy to make atp
... *energy released –> captured by ADP to make ATP *energized H released ->captured by NAD to make NADH & H+ or captured by FAD to make FADH2 NAD is like catcher’s mitt– catches fastball/high energy H ...
... *energy released –> captured by ADP to make ATP *energized H released ->captured by NAD to make NADH & H+ or captured by FAD to make FADH2 NAD is like catcher’s mitt– catches fastball/high energy H ...
Fatty acid synthesis
Fatty acid synthesis is the creation of fatty acids from acetyl-CoA and malonyl-CoA precursors through action of enzymes called fatty acid synthases. It is an important part of the lipogenesis process, which – together with glycolysis – functions to create fats from blood sugar in living organisms.