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Transcript
Segmental approach to normal
and abnormal situs arrangement
- Echocardiography Jan Marek
Great Ormond Street Hospital
&
Institute of Cardiovascular Sciences,
University College London
No disclosures
How the heart should be imaged?
“European Chaos”
•“Transatlantic”
way
LV
LV
•“Adult” way
•“Dutch” way
LV
SEQUENTIAL SEGMENTAL ANALYSIS
ATRIUMS
ARTERIAL
TRUNKS
ATRIOVENTRICULAR
CONNECTIONS
VENTRICULO-ARTERIAL
CONNECTIONS
VENTRICLES
ANALYSE SEGMENTS
Courtesy RH Anderson & A. Cook
•Abdominal situs
• Atriums - Atrial situs (systemic and
pulmonary venous connections)
• AV connections
• Ventricles
• VA connections
• Arterial trunks (AO arch and PA
branches)
Usual Arrangement (Solitus)
A
R
Liver
ST
IVC
AO
SP
Mirror Imagery (Inversus)
A
R
Right Isomerism (Asplenia)
Liver
Liver
IVC
AO
A
R
Left Isomerism (Polysplenia)
Liver
Liver
AO
AZ
A
R
Left Isomerism (Polysplenia)
Fetus
32 WoG
Isomerism (Polysplenia & Asplenia sy)
Isomerism (Polysplenia & Asplenia sy)
Is the symmetry always what we like to see?
Courtesy Ian Sullivan
Position of the Heart in the Chest
•Levocardia
•Dextrocardia
•Mesocardia
•Dextroversion
•Levoversion
•Dextroposition
•Levoposition
Position of the Heart in the Chest
Levocardia with Apex
pointing to the Left
Dextrocardia with Apex
pointing to the Right
Mesocardia with Apex
pointing to the
Right
Left
Dextrocardia with Apex
pointing to the Left
Levocardia with Apex
pointing to the Right
• Abdominal situs
• Atriums - Atrial situs (systemic and
pulmonary venous connections)
• AV connections
• Ventricles
• VA connections
• Arterial trunks (AO arch and PA
branches)
Usual Arrangement (Solitus)
- Atrial appendages -
Fetus 20. WoG
Right Isomerism (Asplenia)
- Atrial appendages -
Left Isomerism (Polysplenia)
- Atrial appendages -
Atrial appendages
- Juxtaposition -
• Abdominal situs
• Atriums - Atrial situs (systemic and
pulmonary venous connections)
• AV connections
• Ventricles
• VA connections
• Arterial trunk (AO arch and PA
branches)
Atrio-ventricular Connections
•Concordant
•Discordant
•Univentricular AV connections
Absent AV connection
Common AV valve
Double inlet connections
Concordant
Connections
PV
AO
RA
LA
PV
RV
LV
Offsetting
Concordant
AV
connection
Discordant
AV
connection
Discordant Connections
CCTGA
DORV/VI
PA/VSD/VI
Univentricular AV Connections
•Absent AV connection (right / left)
Tricuspid / mitral atresia
•Common AV valve
With single ventricle
•Double inlet ventricle
Connection of both AV valve to the same
ventricle:
Anatomically left
Anatomically right
Undetermined
(rudimentary chamber always present)
Univentricular AV connections
RA
LA
RA
LA
Absent
right AV
connection
*
*
Absent
left AV
connection
LA
RA
*
Common AV valve
RA
RA
*
Double inlet
RA
Absent right AV
connection
Absent left AV
connection
Double inlet
Common AV valve
Univentricular AV connections
Double inlet ventricle versus Ventricular septal defect
LA
DIV
> 50%
RV
S
LV
• Abdominal situs
• Atriums - Atrial situs (systemic and
pulmonary venous connections)
• AV connections
• Ventricles
• VA connections
• Arterial trunks (AO arch and PA
branches)
Ventriculo-arterial connections
•Concordant (=normal)
Ventricular septal defect, tetralogy of Fallot…
• Discordant
Transposition
•Double outlet ventricle
With subaortic VSD
subpulmonary VSD
doubly committed VSD
non-committed VSD
•Solitary arterial trunk
Discordant AV / VA connections
Congenitally Corrected TGA
Overriding aortic valve: 50% rule
VSD
TOF
DORV
TOF or Double outlet right ventricle?
RV
TOF vs Double outlet right ventricle
Ao
Pa
Ao
RV
TOF
Pa
Ao
LV
Double outlet right ventricle
Courtesy RH Anderson & A. Cook
Double conus = Double outlet right ventricle?
Double conus does not determine DORV!
How to diagnose....
Correct description of disease?
•Transposition? Congenitally Corrected Transposition?
• Malposition? Corrected malposition? L- Transposition?
• Ventricular inversion? Right/Left? D- Transposition
AV concordance
&
VA discordance
TGA
Right/Left
ventricle
with
two outlets
AV discordance
&
VA discordance
AV discordance
&
VA concordance
DORV
DOLV
CCTGA
CCMGA
AV concordance & VA concordance
with malposition of the great arteries
Segmental approach
•Important to understand situs arrangement
•Provides complete coverage of lesion
•Minimises potential errors
•Easy for reading and interpretation
Sequential Segmental
Approach
KISS
Keep
It
Simple,
Stupid