Survey
* Your assessment is very important for improving the workof artificial intelligence, which forms the content of this project
* Your assessment is very important for improving the workof artificial intelligence, which forms the content of this project
Neuromuscular conditions Cerebral Palsy Dr. Mohammed M. Zamzam Associate Professor & Consultant Pediatric Orthopedic Surgeon Definition Non progressive, cerebral damage occurring before brain maturation (1-2 years) resulting in muscle weakness, spasticity and other symptoms Incidence 0.5-2/1000 in premature deliveries Causes Prenatal : Maternal disease/ Toxemia Cerebral deformity/ Hemorrhage Inborn error of metabolism Perinatal : Labour/ Respiratory complications Perinatal infections Causes Postnatal : Infection Violence Convulsion Classification Topographic Classification Diplegia : (Arms & Legs much more in legs), most patients eventually walk Tetraplegia : (Arms & Legs & Trunk) High mortality rate, most pts unable to walk. IQ is low Classification Topographic Classification Hemiplegia : Upper & lower limbs on one side (upper more than lower limbs), with spasticity, patients eventually walks Bilateral Hemiplegia Paraplegia (Legs) Monoplegia Triplegia Classification Physiological Classification Spastic : Commonest 50-60% Most important for the Orthopedic Surgeon Increased muscle tone (Jack knife spasticity) Slow restricted movements Increased reflexes Babinski +ve Classification Physiological Classification Athetosis : 20-25% ? Kernicterus Involuntary, uncontrolled slow movement Normal reflexes +/- Muscle rigidity or tremors NOT FOR SURGERY Classification Physiological Classification Ataxia : 1-5% Inability to control /coordinate movement when they start Intention tremor Nystagmus / unbalanced gait NOT FOR SURGERY Classification Physiological Classification Rigidity : 5-7 % Lead pipe rigidity Mixed type : A combination of spasticity and athetosis with whole body involvement Presentation 3 year- old boy Presented with Inability to stand or walk Deformities Upper limb : Shoulder adduction/internal rotation Elbow flexion Forearm pronation Wrist and fingers flexion Deformities Lower limb : Hip adduction/flexion/internal rotation Knee flexion Feet equinus / varus or valgus Gait scissoring Spine : kyphoscoliosis The two most important x-rays during follow up Management Aim of treatment : AS INDEPENDENT AS POSSIBLE Avoid pain (hip arthritis) Maintain sitting posture Maintain spinal stability Social benefit Management Multidisciplinary : Orthotics before and after surgery Physiotherapy/Occupational therapy Orthopedic Surgery Neurosurgery/ Pediatric Neurology Speech therapy Management History Exam Investigation Treatment The degree of retardation is of great importance in treatment planning Management Exercise : Start early (1st month) when suspected Qualified Physiotherapist/ PARENTS Prevent contractures Develop coordination Mental exercise Use Orthotics/POP/Casts if needed Management Surgery : Best in Spastic Hemiplegics and severe deformities Contraindicated in Athetoid & Ataxic Management Goal of Surgery : Decrease spasm Release of contractures Correct deformities Rebalance muscles Stabilize flail joints Management Options of Surgery : Neurectomy Tenotomy Tenoplasty Muscle lengthening (Recession) Tendon Transfer Bony surgery Osteotomy/Fusion Spinal surgery Management Intramuscular botulinum toxin: Temporarily It reduces dynamic spasticity is thought that its use promotes normal muscle growth and avoids the development of soft tissue contracture