Download Hemifacial microsomia

Hemifacial microsomia
Hemifacial Microsomia
Characteristics
• Hemi = half, although present in
bilateral condition in up to 15%-16% of
cases
• Unilateral or bilateral underdev of
mandible
• Unilateral or bilateral
underdev/malformations of ear
(microtia, ear tags, etc)
• Unilateral or bilateral reduction in size
and flattening of maxilla
• Narrowing of the opening of the eye
Causes: thought caused by hemorrhage
from artery that produces hematoma in
area of branchial arches (head, neck
area dev from branchial arches).
Occurs during first 6-8 weeks of
pregnancy.
• Inheritance: sporadic; reports of
familial cases. May be auto dominant,
auto recessive, or multifactorial.