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2016 NUTRICIA PRODUCT REFERENCE GUIDE FOR CLINICIANS • CANADA Nutricia Contacts How to Contact Nutricia My Nutricia sales representative(s): Name:............................................................................... Nutricia’s Customer Service: • Phone: (877) 636-2283 Phone:.............................................................................. Nutricia’s Nutrition Services: Email:................................................................................ • Phone: (877) 636-2283 • Email: [email protected] Name:............................................................................... Phone:.............................................................................. Email:................................................................................ Name:............................................................................... Phone:.............................................................................. Nutricia Metabolics: • Phone: (800) 605-0410 • Email: [email protected] Internet: For information on Nutricia products and other helpful resources, visit www.Nutricia-NA.com. For a complete listing of our websites, see pages 202. You may also visit our Neocate website at www.Neocate.com/Canada or our Metabolics website at www.MedicalFood.com. Email:................................................................................ 2 © 2016 Nutricia North America. All rights reserved. Nutricia and its brands are registered trademarks. See product labels for more specifics. • Nutricia is a Global Health Company • Nutricia Leads the Development and Use of Advanced Medical Nutrition for Specialized Care • Nutricia Products and Services Transform the Daily Lives of Millions of Infants, Children, Adults and Aging Seniors This guide is a convenient reference for clinicians to the full range of Nutricia’s medical nutritional products. Nutricia strives to develop quality products that offer choice and flexibility to today’s patients to enhance diet acceptance. Please note that all of our products require medical supervision. For additional information, please call our Nutrition Services team or visit our web sites at www.Nutricia-NA.com, www.Neocate.com/Canada or www. MedicalFood.com. Our staff is comprised of individuals with the highest level of expertise ready to offer support and reliability to our customers. We look forward to hearing from you. Consumers and Patients: Nutricia products are available for convenient home delivery directly from Nutricia North America. Consumers can call our toll free number or visit one of our websites. See pages 232-233 for a list of our websites. Consumers can also purchase Nutricia products through retail pharmacies. Pharmacies can special order Nutricia products from their wholesaler or directly from Nutricia North America. 3 CONTENTS – Alphabetical Index CONTENTS Ordering Information....................................................... 2-3 Contents by Product Indications..................................... 6-8 Specialized Pediatrics Section...................................... 9-34 Mixing Instructions................................................ 22-23 Household Measurements......................................... 24 Volume Prescription................................................... 25 Dilution Charts...................................................... 26-33 Metabolics Section................................................... 35-158 Household Measurements: Metabolics..................... 144 Mixing Instructions: Metabolics......................... 146-157 Low Protein Foods Section..................................... 159-162 Neurology Section.................................................. 163-172 Directions for Preparation: KetoCal........................... 170 Other Medical Nutritionals Section.......................... 173-190 Resources.............................................................. 191-202 Specialized Pediatrics page 9-34 4 Metabolics Low Protein Foods page 35-158 page 159-162 Neurology page 163-172 Other Nutritionals page 173-190 Periflex Advance...............................................................40 Complete Amino Acid Mix...............................................184 Periflex Infant....................................................................36 Complex Essential MSD Drink Mix....................................80 PKU Periflex Junior Plus....................................................38 Complex Junior MSD Drink Mix.........................................78 Periflex LQ........................................................................42 Complex MSD Amino Acid Bars........................................84 PhenylAde 40 Drink Mix....................................................48 Complex MSD Amino Acid Blend......................................82 PhenylAde 60 Drink Mix....................................................50 Duocal............................................................................180 PhenylAde Amino Acid Bars..............................................54 Essential Amino Acid Mix................................................186 PhenylAde Amino Acid Blends..........................................52 GlutarAde GA-1 Amino Acid Blend..................................106 PhenylAde Essential Drink Mix...........................................44 GlutarAde Essential GA-1 Drink Mix................................104 PhenylAde GMP Drink Mix................................................46 GlutarAde Junior GA-1 Drink Mix....................................102 PhenylAde PheBLOC LNAA..............................................56 HCU Anamix Next...........................................................110 Phlexy-10 Drink Mix..........................................................66 HCU Lophlex LQ.............................................................116 Phlexy-Vits......................................................................188 IVA Anamix Next...............................................................90 PKU Lophlex LQ...............................................................62 KetoCal 4:1 LQ - Vanilla and Unflavoured........................168 Polycal............................................................................182 KetoCal 4:1 Powder........................................................164 TYR Anamix Next............................................................130 KetoCal 4:1 Powder - Coming Soon...............................166 TYR Lophlex LQ..............................................................138 Lanaflex............................................................................68 UCD Anamix Junior.........................................................140 Liquigen..........................................................................178 XLeu Analog......................................................................88 Lophlex Powder................................................................64 XLeu Maxamaid................................................................92 Low Protein Foods...................................................159-162 XLeu Maxamum................................................................94 Methionaid......................................................................118 XLys, XTrp Analog.............................................................96 Milupa lp-foods...............................................................160 XLys, XTrp Maxamaid........................................................98 MMA/PA Anamix Next.....................................................122 XLys, XTrp Maxamum......................................................100 Monogen........................................................................174 XMet Analog...................................................................108 Monogen - Coming Soon................................................176 XMet Maxamaid..............................................................112 MSUD Aid.........................................................................86 XMet Maxamum..............................................................114 MSUD Analog ..................................................................70 XMTVI Analog.................................................................120 MSUD Lophlex LQ............................................................76 XMTVI Maxamaid............................................................124 MSUD Maxamaid..............................................................72 XMTVI Maxamum............................................................126 MSUD Maxamum..............................................................74 XPhe Maxamaid................................................................58 Neocate E028 Splash.......................................................20 XPhe Maxamum................................................................60 Neocate DHA & ARA Infant Formula..................................10 XPhe, XTyr Analog...........................................................128 Neocate Junior..................................................................14 XPhe, XTyr Maxamaid.....................................................132 Neocate Junior with Prebiotic Fibre...................................16 XPHEN, TYR Maxamaid..................................................134 Neocate Nutra...................................................................12 XPHEN, TYR Maxamum..................................................136 Neocate Splash, Unflavoured............................................18 5 CONTENTS – By Indication and Diet Need* Allergy, Cow and Soy Milk/Multiple Food Protein Intolerance Failure-to-Thrive Duocal..................................................................... 180 Neocate E028 Splash................................................ 20 Neocate DHA & ARA Infant Formula........................... 10 Neocate Nutra............................................................ 12 Neocate Junior........................................................... 14 Neocate Junior with Prebiotic Fibre............................ 16 Neocate Splash, Unflavoured..................................... 18 Complete Amino Acid Mix........................................ 184 Duocal..................................................................... 180 Neocate E028 Splash................................................ 20 Neocate DHA & ARA Infant Formula........................... 10 Neocate Nutra............................................................ 12 Neocate Junior........................................................... 14 Neocate Junior with Prebiotic Fibre............................ 16 Neocate Splash.......................................................... 18 Polycal..................................................................... 182 Amino Acid-Based Products Gastrointestinal Tract Impairment/GER Neocate E028 Splash................................................ 20 Neocate DHA & ARA Infant Formula........................... 10 Neocate Nutra............................................................ 12 Neocate Junior........................................................... 14 Neocate Junior with Prebiotic Fibre............................ 16 Neocate Splash, Unflavoured..................................... 18 Nutricia Metabolic Formulas................................ 35-158 Complete Amino Acid Mix........................................ 184 Essential Amino Acid Mix......................................... 186 Single Amino Acids.................................................. 190 Chylothorax Liquigen................................................................... 178 Monogen................................................................. 174 Eosinophilic Esophagitis (EoE) 6 Neocate E028 Splash................................................ 20 Neocate DHA & ARA Infant Formula........................... 10 Neocate Nutra............................................................ 12 Neocate Junior........................................................... 14 Neocate Junior with Prebiotic Fibre............................ 16 Neocate Splash, Unflavoured..................................... 18 Complete Amino Acid Mix........................................ 184 Neocate E028 Splash................................................ 20 Neocate DHA & ARA Infant Formula........................... 10 Neocate Nutra............................................................ 12 Neocate Junior........................................................... 14 Neocate Junior with Prebiotic Fibre............................ 16 Neocate Splash.......................................................... 18 Pepdite Junior............................................................ 22 Complete Amino Acid Mix........................................ 184 Glutaric Acidemia Type I GlutarAde Junior GA-1 Drink Mix............................. 102 GlutarAde Essential GA-1 Drink Mix......................... 104 GlutarAde GA-1 Amino Acid Blend........................... 106 XLys, XTrp Analog...................................................... 96 XLys, XTrp Maxamaid................................................. 98 XLys, XTrp Maxamum............................................... 100 Homocystinuria/Hypermethioninemia XMet Analog............................................................ 108 XMet Maxamaid....................................................... 112 XMet Maxamum....................................................... 114 HCU Anamix Next.................................................... 110 HCU Lophlex LQ...................................................... 116 Milupa lp-foods........................................................ 160 Inborn Errors of Metabolism Nutricia Metabolic Formulas...............................35-158 Low Protein Foods...........................................160-161 Liquigen.................................................................. 178 Monogen................................................................ 174 Duocal.................................................................... 180 Polycal.................................................................... 182 Complete Amino Acid Mix....................................... 184 Essential Amino Acid Mix........................................ 186 Phlexy-Vits.............................................................. 188 Single Amino Acids................................................. 190 Isovaleric Acidemia IVA Anamix Next....................................................... 90 XLeu Analog.............................................................. 88 XLeu Maxamaid........................................................ 92 XLeu Maxamum........................................................ 94 Ketogenic Diet KetoCal 4:1 LQ - Vanilla and Unflavoured................ 168 KetoCal 4:1 Powder................................................ 174 Liquigen.................................................................. 178 Long Chain Fatty Acid Oxidation Disorders Liquigen.................................................................. 178 Monogen................................................................ 174 Low Protein Diets Low Protein Foods...........................................160-161 Duocal.................................................................... 180 Malabsorption Duocal.................................................................... 180 Neocate DHA & ARA Infant Formula.......................... 10 Neocate Nutra........................................................... 12 Neocate Junior.......................................................... 14 Neocate Junior with Prebiotic Fibre........................... 16 Neocate Splash, Unflavoured.................................... 18 Liquigen.................................................................. 178 Polycal.................................................................... 182 Complete Amino Acid Mix....................................... 184 Maple Syrup Urine Disease Complex Junior MSD Drink Mix................................. 78 Complex Essential MSD Drink Mix............................ 80 Complex MSD Amino Acid Bars................................ 84 MSUD Analog........................................................... 70 MSUD Maxamaid...................................................... 72 MSUD Maxamum...................................................... 74 MSUD Lophlex LQ.................................................... 76 MSUD Aid................................................................. 86 Modular Diets Duocal.................................................................... 180 Liquigen.................................................................. 178 Polycal.................................................................... 182 Complete Amino Acid Mix....................................... 184 Essential Amino Acid Mix........................................ 186 Phlexy-Vits.............................................................. 188 Phenylketonuria Periflex Infant............................................................ 36 PKU Periflex Junior Plus............................................ 38 Periflex LQ................................................................ 42 Periflex Advance....................................................... 40 PhenylAde 40 Drink Mix............................................ 48 PhenylAde 60 Drink Mix............................................ 50 PhenylAde Amino Acid Bars...................................... 54 PhenylAde Amino Acid Blends.................................. 52 PhenylAde Essential Drink Mix................................... 44 PhenylAde GMP Drink Mix........................................ 46 PhenylAde PheBLOC LNAA...................................... 56 XPhe Maxamaid........................................................ 58 XPhe Maxamum Powder........................................... 60 Lophlex Powder........................................................ 64 Phlexy-10 Drink Mix.................................................. 66 PKU Lophlex LQ....................................................... 62 Lanaflex.................................................................... 68 Propionic/Methylmalonic Acidemia MMA/PA Anamix Next............................................. 122 XMTVI Analog......................................................... 120 XMTVI Maxamaid.................................................... 124 XMTVI Maxamum.................................................... 126 *Not a complete listing 7 Protein-Energy Malnutrition (PEM) Duocal.................................................................... 180 Polycal.................................................................... 182 Renal Failure Low Protein Foods...........................................160-161 Duocal.................................................................... 180 Polycal.................................................................... 182 Short Bowel Syndrome Liquigen.................................................................. 178 Neocate E028 Splash............................................... 20 Neocate DHA & ARA Infant Formula.......................... 10 Neocate Nutra........................................................... 12 Neocate Junior.......................................................... 14 Neocate Junior with Prebiotic Fibre........................... 16 Neocate Splash, Unflavoured.................................... 18 Complete Amino Acid Mix....................................... 184 Tyrosinemia XPhe, XTyr Analog................................................... 128 XPhe, XTyr Maxamaid............................................. 132 XPHEN, TYR Maxamaid.......................................... 134 XPHEN, TYR Maxamum.......................................... 136 TYR Anamix Next.................................................... 130 TYR Lophlex LQ...................................................... 138 Unintentional Weight Loss Duocal.................................................................... 180 Urea Cycle Disorders 8 UCD Anamix Junior................................................. 140 Essential Amino Acid Mix........................................ 186 Pe d ia tric s Specialized Pediatrics ed Spe c z i a li 9 A nutritionally complete, powdered amino acid-based infant formula containing iron and DHA and ARA. Nutrition Information: Nutrients Energy, kcal (kJ) 67.0 (279) Minerals Per 100 mL 522 82.5 392 61.9 13.0 2.1 Phosphorus, mg 49.3 7.8 Magnesium, mg Fat, g 19.1 3.0 2.9 0.45 346 Per 100 g Calcium, mg Carbohydrate, g a-Linolenic Acid, mg Specialized Pediatrics 421 (1766) Ingredients: Per 100 mL Protein Equivalent, g Linoleic Acid, g 10 Per 100 g 52.0 8.2 Iron, mg 7.8 1.2 Zinc, mg 7.0 1.1 55.0 Manganese, mg 0.380 0.060 Main Features: Indications: Arachidonic Acid, mg 63.7 10.1 Copper, mg 0.520 0.0822 •Hypoallergenic • With DHA and ARA • 100% non-allergenic free amino acids • Nutritionally complete • Over 100 publications and counting support Neocate • Standard dilution = 0.67 kcal/mL • Osmolality (at 0.67 kcal/mL): 375 mOsm/kg • Energy distribution: Protein 12% Carbohydrate47% Fat (MCT 33% / LCT 67%)41% • Displacement 0.7 mL/g • • • Docosahexaenoic Acid, mg 36.4 5.8 Iodine, mg 0.0650 0.0103 Ash, mg 0.54 Molybdenum, mg 0.020 0.0032 Vitamins Chromium, mg 0.0150 0.0024 Vitamin A, IU 1648 0.0157 Vitamin D3, IU 252 Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) • Malabsorption • Gastroesophageal reflux • Other GI disorders 3.4 260 39.8 4.8 0.76 Potassium, mg 653 0.0370 0.0058 Chloride, mg 325 Thiamine, mg 0.31 0.05 0.09 0.58 Vitamin B6, mg 0.52 0.08 Vitamin B12, mg 0.0011 0.0002 For guidance on monitoring micronutrients, please see page 34. Niacin, mg 6.5 1.0 Folic Acid, mg 0.0430 0.0068 Pantothenic Acid, mg 2.6 0.41 Ordering Information: Biotin, mg 0.0130 0.0021 Calories Per Can 1684 157 Vitamin K1, mg Riboflavin, mg Product Packaging 4 x 400 g Sodium, mg Vitamin E, IU For details on administration and household measurements, please see pages 22-33. Product Code 60722 Selenium, mg Vitamin C, mg 39.0 Choline, mg 55.0 8.7 Inositol, mg 98.0 15.5 0.0025 24.8 103 51.4 Corn Syrup Solids, Refined Vegetable Oil (Modified Coconut and/or Palm Kernel Oil (Medium Chain Triglycerides), High Oleic Sunflower Oil, Soy Oil), Calcium Phosphate, L-Arginine L-Aspartate, Tripotassium Citrate, L-Leucine, L-Lysine Acetate, L-Glutamine, L-Proline, L-Valine, Glycine, L-Isoleucine, Citric Acid Esters of Mono- and Diglycerides, L-Threonine, L-Phenylalanine, L-Tyrosine, L-Serine, L-Histidine, L-Alanine, Sodium Chloride, L-Cystine, L-Tryptophan, L-Methionine, Magnesium Acetate, Magnesium L-Aspartate, Potassium Chloride, Mortierella Alpina Oil*, Choline Bitartrate, Inositol, Crypthecodinium Cohnii Oil**, Ascorbic Acid (Vitamin C), Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Sunflower Oil, Niacinamide, DL-α-Tocopheryl Acetate (Vitamin E), Calcium D-Pantothenate, Cupric Sulfate, Manganese Sulfate, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Thiamine Chloride Hydrochloride, Ascorbyl Palmitate, Potassium Iodide, Chromium Sulfate, Mixed Tocopherols, DL-α-Tocopherol (Vitamin E), Phylloquinone (Vitamin K1), Sodium Molybdate, Folic Acid, Sodium Hydrogen Selenite, Biotin, Cholecalciferol (Vitamin D3), Cyanocobalamin (Vitamin B12). Neocate DHA & ARA Infant Formula Neocate® DHA & ARA Infant Formula * A Source of Arachidonic Acid (ARA) ** A Source of Docosahexaenoic Acid (DHA) 6.2 * Standard Dilution = .67 kcal/mL 11 Neocate Nutra Specialized Pediatrics The first and only amino acid-based semi-solid food for special medical purpose for children and infants over 6 months of age. 12 Main Features: Indications: • Smooth, spoonable consistency • Hypoallergenic • Made with 100% non-allergenic amino acids • Milk protein- and gluten-free • High in calcium, vitamin D, zinc and iron • Free from artificial flavours, colours and preservatives • Energy distribution: Protein 7% Carbohydrate57% Fat (MCT 4% / LCT 96%)36% • • • Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy-associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) • Malabsorption • Gastroesophageal reflux • Other GI disorders For details on administration and household measurements, please see pages 22-33. Ordering Information: Product Code 66739 Note: Not suitable as sole source of nutrition. Not for bottle or tube feeding. Product Packaging 4 x 400 g Calories Per Can 1888 Ingredients: Per Suggested Per Suggested Corn Syrup Solids, Rice Starch, Refined Serving Serving Vegetable Oil (Non-Hydrogenated Nutrients Per 100 g (37 g Powder) Minerals Per 100 g (37 g Powder) Coconut, High Oleic Sunflower, Canola, Energy, kcal (kJ) 472 (1978) 175 (733) Calcium, mg 668 247 Sunflower), Sugar, Calcium Phosphate Tribasic, L-Arginine L-Aspartate, L-Leucine, Protein Equivalent, g 8.2 3.0 Phosphorus, mg 340 126 L-Lysine Acetate, Citric Acid Esters of Carbohydrate, g 67.4 24.9 Magnesium, mg 21.0 7.8 Mono- and Diglycerides, L-Glutamine, L-Proline, L-Valine, Glycine, L-Isoleucine, Fat, g 18.8 7.0 Iron, mg 5.9 2.2 L-Threonine, L-Phenylalanine, L-Tyrosine, Linoleic Acid, mg 3.2 1.2 Zinc, mg 4.1 1.5 L-Serine, L-Histidine, L-Alanine, L-Cystine, Vitamins L-Tryptophan, L-Methionine, Choline Manganese, mg 0.310 0.115 Bitartrate, Magnesium L-Aspartate, Vitamin A, IU 649 240 Copper, mg 0.310 0.115 Magnesium Acetate, M-Inositol, L-Ascorbic Vitamin D3, IU 172 63.6 Iodine, mg 0.414 0.0153 Acid, Ferrous Sulfate, Taurine, Zinc Sulfate, Vitamin E, IU 3.4 1.3 L-Carnitine, DL-Alpha Tocopheryl Acetate, Molybdenum, mg 0.0088 0.0033 Calcium D-Pantothenate, Niacinamide, Vitamin C, mg 23.0 8.5 Chromium, mg 0.0010 0.0004 Manganese Sulfate, Cupric Sulfate, Thiamine Thiamine, mg 0.250 0.093 Chloride Hydrochloride, Pyridoxine Selenium, mg 0.0113 0.0042 Riboflavin, mg 0.250 0.093 Hydrochloride, Riboflavin, Vitamin A Sodium, mg 38.0 14.1 Niacin, mg 1.1 0.40 Acetate, Potassium Iodide, Chromium Chloride, Folic Acid, Sodium Selenite, Vitamin B6, mg 0.250 0.093 Potassium, mg <20.0 <10.0 Sodium Molybdate, Phylloquinone, D-Biotin, Folic Acid, mg 0.0275 0.0102 Chloride, mg 44.0 16.3 Cholecalciferol, Cyanocobalamin. Vitamin B12, mg 0.0006 0.0002 Pantothenic Acid, mg 1.4 0.52 Vitamin K, mg 0.0185 0.0068 Biotin, mg 0.0091 Neocate Nutra Nutrition Information: ® 0.0034 Choline, mg 45.0 16.7 Inositol, mg 49.0 18.1 13 Neocate Junior ® Specialized Pediatrics A nutritionally complete, powdered amino acid-based food for special medical purpose for individuals over 1 year of age. 14 Main Features: Indications: •Hypoallergenic • 100% non-allergenic free amino acids • Nutritionally complete • Available in unflavoured and tropical • Standard dilution = 1 kcal/mL • Osmolality (mOsm/kg): Dilution Unflavoured Tropical 1 kcal/mL 550 630 • Free water: Unflavoured Tropical Dilution 1 kcal/mL 84.9% 84.0% • Energy distribution: Unflavoured Tropical Protein 13%14% Carbohydrate 42% 44% 42% Fat (MCT 35% / LCT 65%)45% • • • • Displacement: 0.72 mL/g Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy-associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) • Malabsorption • Gastroesophageal reflux • Other GI disorders For details on administration and household measurements, please see pages 22-33. For guidance on monitoring micronutrients, please see page 34. Ordering Information: Product Code 11790 - Unflavoured 12124 - Tropical Product Packaging 4 x 400 g 4 x 400 g Calories Per Can 1912 1804 Unflavoured Tropical Nutrients Per 100 g Per 100 mL* Per 100 g Per 100 mL* Energy, kcal (kJ) 478 (2002) 100 (418) 451 (1891) 100 (420) Protein Equivalent, g 16.0 3.3 16.0 3.5 Carbohydrate, g 49.5 10.4 49.5 11.0 Fat, g 24.0 5.0 21.0 4.7 Linoleic Acid, g 2.6 0.54 2.3 0.51 Vitamins Vitamin A, IU 956 200 902 200 Vitamin D3, IU 380 79.4 360 79.8 Vitamin E, IU 10.0 2.1 9.4 2.1 Vitamin C, mg 44.6 9.3 44.6 9.9 Thiamine, mg 0.48 0.10 0.48 0.11 Riboflavin, mg 0.96 0.20 0.90 0.20 Niacin, mg 4.3 0.90 4.3 0.95 0.48 0.10 0.48 0.11 Vitamin B6, mg Folic Acid, mg 0.1430 0.0299 0.1430 0.0317 0.0019 0.0004 0.0018 0.0004 Vitamin B12, mg Pantothenic Acid, mg 1.9 0.40 1.9 0.42 Vitamin K, mg 0.0192 0.0040 0.0192 0.0043 Biotin, mg 0.0144 0.0030 0.0135 0.0030 Choline, mg 143 29.9 143 31.7 Inositol, mg 105 22.0 105 23.3 Minerals Calcium, mg 565 118 540 120 Phosphorus, mg 382 79.9 359 79.6 Magnesium, mg 76.5 16.0 76.5 17.0 Iron, mg 7.4 1.6 7.4 1.6 Zinc, mg 4.7 0.98 4.7 1.0 Iodine, mg 0.0852 0.0178 0.0852 0.0189 Manganese, mg 0.62 0.13 0.62 0.14 Copper, mg 0.53 0.11 0.53 0.12 Molybdenum, mg 0.0215 0.0045 0.0215 0.0048 Chromium, mg 0.018 0.0038 0.018 0.004 Selenium, mg 0.0192 0.0040 0.018 0.004 Sodium, mg 239 50.0 225 49.9 Potassium, mg 653 137 653 145 Chloride, mg 364 76.2 343 76.1 * Standard Dilution = 1 kcal/mL Ingredients: Corn Syrup Solids, Refined Vegetable Oils (Modified Coconut and/or Palm Kernel Oil (Medium Chain Triglycerides), Canola Oil, High Oleic Safflower Oil), L-Arginine, L-Glutamine, L-Lysine, L-Aspartate, Tripotassium Citrate, Calcium Phosphate Dibasic, L-Leucine, L-Phenylalanine, L-Proline, Silicon Dioxide, L-Valine, Glycine, L-Isoleucine, N-Acetyl-L-Methionine, L-Threonine, Mono- and Diglycerides, Sodium Chloride, L-Histidine, L-Serine, L-Alanine, Magnesium Acetate, Calcium Phosphate Tribasic, Choline Bitartrate, L-Tryptophan, L-Tyrosine, Diacetyl Tartaric Acid Esters of Mono- and Diglycerides, Inositol, L-Ascorbic Acid, L-Cystine, Propylene Glycol Alginate, Taurine, Ferrous Sulphate, L-Carnitine, Zinc Sulphate, DL-Alpha-Tocopheryl Acetate, Niacinamide, Calcium D-Pantothenate, Manganese Sulphate, Cupric Sulphate, Riboflavin, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Molybdate, Sodium Selenite, Phylloquinone, Biotin, Cholecalciferol, Cyanocobalamin. Neocate Junior Nutrition Information: Tropical flavoured version also contains: Artificial Flavour, Citric Acid. Artificial Sweetener contains Acesulfame Potassium 11.2 mg/100 mL (standard dilution). Please see individual product can labels for exact order of ingredients. 15 Neocate® Junior with Prebiotic Fibre Specialized Pediatrics A nutritionally complete, powdered amino acid-based food for special medical purpose with prebiotic fibre for individuals over 1 year of age. 16 Main Features: Indications: •Hypoallergenic • Contains prebiotic fibre to help support total gut health • 100% non-allergenic free amino acids • Nutritionally complete • Available in unflavoured, vanilla & strawberry • Standard dilution= 1 kcal/mL • Osmolality (mOsm/kg): Unflavoured Vanilla Strawberry Dilution 550650 630 1 kcal/mL • Free water: Unflavoured Vanilla Strawberry Dilution 1 kcal/mL 84.5% 84.5% 84.9% • Energy distribution: • • • Unflavoured Vanilla Strawberry Protein 13% 14%14% Carbohydrate 42% 45% 45% Fat (MCT 35% / LCT 65%) 45% 41%41% •Displacement: UnflavouredVanilla Strawberry 0.74 mL/g 0.71 mL/g 0.71 mL/g Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) • Malabsorption • Gastroesophageal reflux • Other GI disorders For details on administration and household measurements, please see pages 22-33. For guidance on monitoring micronutrients, please see page 34. Ordering Information: Product Code 12912 - Unflavoured 60627 - Vanilla 86456 - Strawberry Product Packaging 4 x 400 g 4 x 400 g 4 x 400 g Calories Per Can 1912 1836 1876 Unflavoured Vanilla Strawberry Nutrients Per 100g Per 100 mL* Per 100g Per 100 mL* Per 100g Per 100 mL* Energy, kcal (kJ) 478 (2002) 100 (418) 459 (1923) 100 (419) 469 (1965) 100 (419) Protein Equivalent, g 16.0 3.3 16.0 3.5 16.0 3.4 Carbohydrate, g 49.510.4 51.4 11.2 52.911.3 Fat, g 24.05.0 21.0 4.6 1.90.4 Linoleic Acid, g 2.6 0.54 2.3 0.5 21.5 4.6 Fibre, g 1.90.40 1.9 0.41 2.30.5 Vitamins Vitamin A, IU 956 200 916 200 956 204 Vitamin D3, IU 380 79.4 364 79.3 372 79.3 Vitamin E, IU 10.0 2.1 9.5 2.1 10.0 2.1 Vitamin C, mg 44.6 9.3 44.6 9.7 44.6 9.5 Thiamine, mg 0.480.10 0.48 0.10 0.480.10 Riboflavin, mg 0.960.20 0.92 0.20 0.960.20 Niacin, mg 4.30.90 4.3 0.94 4.30.92 Vitamin B6, mg 0.480.10 0.48 0.10 0.480.10 Folic Acid, mg 0.1430 0.0299 0.1430 0.0312 0.143 0.0305 Vitamin B12, mg 0.00190.0004 0.0018 0.0004 0.00190.0004 Pantothenic Acid, mg 1.9 0.40 1.9 0.41 1.9 0.41 Vitamin K, mg 0.0192 0.0040 0.0192 0.0042 0.0192 0.0041 Biotin, mg 0.01440.0030 0.0138 0.0030 0.01440.0031 Choline, mg 14329.9143 31.214330.5 Inositol, mg 10522.0105 22.910522.4 Minerals Calcium, mg 565118 542 118 565120 Phosphorus, mg 38279.9367 80.038281.5 Magnesium, mg 76.516.0 76.5 16.7 76.516.3 Iron, mg 7.41.6 7.4 1.6 7.41.6 Zinc, mg 4.70.98 4.7 1.0 4.71.0 Iodine, mg 0.08520.0178 0.0852 0.0186 0.08520.0182 Manganese, mg 0.62 0.13 0.620 0.135 0.620 0.132 Copper, mg 0.53 0.11 0.530 0.0115 0.530 0.113 Molybdenum, mg 0.02150.0045 0.0215 0.0047 0.02150.0046 Chromium, mg 0.01800.0038 0.0180 0.0039 0.01800.0038 Selenium, mg 0.01920.0040 0.0184 0.0040 0.01920.0041 Sodium, mg 23950.0230 50.123951.0 Potassium, mg 653137 653 142 653139 Chloride, mg 36476.2349 76.036477.6 * Standard Dilution = 1 kcal/mL Ingredients: Corn Syrup Solids, Refined Vegetable Oils (Modified Coconut and/or Palm Kernel Oil (Medium Chain Triglycerides), Canola Oil, High Oleic Safflower Oil), L-Arginine, L-Glutamine, L-Lysine, L-Aspartate, Tripotassium Citrate, Calcium Phosphate Dibasic, L-Leucine, L-Phenylalanine, Fructooligosaccharide (FOS), Chicory Root Inulin, L-Proline, L-Valine, Glycine, L-Isoleucine, N-Acetyl-L-Methionine,Silicon Dioxide, L-Threonine, Mono- and Diglycerides, Sodium Chloride, L-Histidine, L-Serine, L-Alanine, Magnesium Acetate, Calcium Phosphate Tribasic, Choline Bitartrate, L-Tryptophan, L-Tyrosine, Diacetyl Tartaric Acid Esters of Mono- and Diglycerides, Inositol, L-Ascorbic Acid, L-Cystine, Propylene Glycol Alginate, Taurine, Ferrous Sulphate, L-Carnitine, Zinc Sulphate, DL-Alpha-Tocopheryl Acetate, Niacinamide, Calcium D-Pantothenate, Manganese Sulphate, Cupric Sulphate, Riboflavin, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Molybdate, Sodium Selenite, Phylloquinone, Biotin, Cholecalciferol, Cyanocobalamin. Neocate Junior with Prebiotic Fibre Nutrition Information: Vanilla and Strawberry flavoured versions also contain: Sugar, Artificial Flavour, Artificial Sweetener. Vanilla flavoured version also contains Sucralose 10.5 mg/100 mL (standard dilution). Strawberry flavoured version also contains Sucralose 12.7 mg/100 mL (standard dilution) and Citric Acid. Please see individual product can labels for exact order of ingredients. 17 Specialized Pediatrics 18 Indications: •Hypoallergenic • 100% non-allergenic free amino acids • Nutritionally complete • Convenient ready-to-feed 237 mL drink boxes • Gluten- and casein-free • Available in unflavoured • Energy density = 1 kcal/mL • Energy distribution: Protein 12% Carbohydrate42% Fat (MCT 35% / LCT 65%)46% • Osmolality: 670 mOsm/kg • Free water: 84.6% • • • Product Packaging 27 x 237 mL (8 fl oz) Calories Per Box 237 Per drink box (237 mL) Calcium, mg 280 Phosphorus, mg 190 Carbohydrate, g 24.9 10.5 Magnesium, mg Fat, g 12.1 5.1 Per 100 mL 118 80.0 37.9 16.0 Iron, mg 3.6 1.5 Zinc, mg 2.3 0.98 Vitamins Iodine, mg 0.0422 0.0178 Vitamin A, IU 474 Manganese, mg 0.308 0.130 Vitamin D3, IU 190 Copper, mg 0.237 0.100 2.1 Molybdenum, mg 0.0107 0.0045 9.3 Chromium, mg 0.0090 0.0038 0.0095 Vitamin C, mg Ordering Information: 237 (991) 100 (418) Minerals 3.0 Vitamin E, IU For details on administration, please see pages 22-33. Per 100 mL 7.1 Protein Equivalent, g Linoleic Acid, mg Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy-associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) •Malabsorption • Gastroesophageal reflux • Other GI disorders Product Code 84451 - Unflavoured Energy, kcal (kJ) Per drink box (237 mL) 291 5.0 22 690 200 80.0 Thiamine, mg 0.24 0.10 Selenium, mg Riboflavin, mg 0.47 0.20 Sodium, mg 119 Niacin, mg 2.1 0.90 Potassium, mg 325 Vitamin B6, mg 0.24 0.10 Chloride, mg 180 Folic Acid, mg 0.0709 0.0299 Vitamin B12, mg 0.0009 0.0004 Pantothenic Acid, mg 0.948 0.400 Vitamin K, mg 0.0095 0.0040 Biotin, mg 0.0071 0.0040 50.0 137 76.0 Water, Maltodextrin, Sugar, Refined Vegetable Oils (High Oleic Sunflower Oil, Modified Palm Kernel and/or Coconut Oil (Medium Chain Triglycerides), Canola Oil, L-Arginine, Calcium Glycerophosphate, L-Lysine L-Aspartate, Microcrystalline Cellulose, L-Leucine, L-Phenylalanine, Tripotassium Citrate, Trisodium Citrate, Diacetyl Tartaric Acid Esters of Mono & Diglycerides, Mono and Diglycerides, L-Proline, L-Valine, Glycine, L-Isoleucine, N-Acetyl L-Methionine, Calcium Chloride, L-Threonine, Citric Acid, L-Histidine, L-Serine, L-Ascorbic Acid, Dipotassium Phosphate, L-Alanine, Magnesium Acetate, Choline Bitartrate, L-Tryptophan, L-Tyrosine, Cellulose Gum, M-Inositol, L-Cystine, Taurine, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Niacinamide, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Riboflavin, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Molybdate, Sodium Selenite, Phylloquinone, D-Biotin, Cholecalciferol, Cyanocobalamin. Neocate Splash, Unflavoured Nutrients The first and only unflavoured ready-to-feed hypoallergenic amino acid-based food for special medical purpose for individuals over 1 year of age. Main Features: Ingredients: Nutrition Information: Neocate® Splash, Unflavoured 0.0030 Choline, mg 70.9 29.9 Inositol, mg 52.1 22.0 19 Neocate® E028 Splash A ready-to-feed amino acid-based food for special medical purpose for individuals over 1 year of age. Nutrients Energy, kcal (kJ) Protein Equivalent, g Specialized Pediatrics Carbohydrate, g 20 Main Features: Indications: •Hypoallergenic • 100% non-allergenic free amino acids • Convenient ready-to-feed 237 mL drink boxes • Available in 3 great flavours: • Grape • Tropical Fruit • Orange-Pineapple • Energy density = 1 kcal/mL • Osmolality (at 1 kcal/mL): 820 mOsm/kg • Free water: • • • Grape Tropical Fruit Orange-Pineapple 77.8% 80.5% 80.5% • Energy distribution: Protein 10% Carbohydrate58% Fat (MCT 35% / LCT 65%)32% Ordering Information: Product Code 12670 - Grape 12666 - Tropical Fruit 11050 - Orange-Pineapple Product Packaging 27 x 237 mL (8 fl oz) 27 x 237 mL (8 fl oz) 27 x 237 mL (8 fl oz) Calories Per Box 237 237 237 Minerals Calcium, mg 147 62.0 5.9 2.5 Phosphorus, mg 147 62.0 34.6 14.6 Magnesium, mg 8.3 3.5 9.0 Iron, mg 1.8 0.77 Zinc, mg 1.8 0.77 Vitamins Iodine, mg 0.0014 0.0060 Vitamin A, IU Manganese, mg 0.0002 0.0001 Copper, mg 0.240 0.100 Linoleic Acid, mg For details on administration, please see pages 22-33. 237 (991) 100 (418) Per drink box (237 mL) Per 100 mL* 21.3 Fat, g Cow milk allergy and soy milk allergy Multiple food protein intolerance Food allergy associated conditions: • Short bowel syndrome (SBS) • Eosinophilic esophagitis (EoE) • Gastroesophageal reflux • Other GI disorders Per drink box (237 mL) Per 100 mL* 626 277 264 117 Vitamin D3, IU 73.5 Vitamin E, IU 1.9 0.82 Molybdenum, mg 0.0083 0.0035 Vitamin C, mg 7.4 3.1 Chromium, mg 0.0071 0.0030 Thiamine, mg 0.13 0.06 Selenium, mg 0.0037 Riboflavin, mg 0.15 0.07 Sodium, mg Niacin, mg 2.1 0.90 Potassium, mg Vitamin B6, mg 0.19 0.08 Chloride, mg Folic Acid, mg 0.0142 0.0060 31.0 Vitamin B12, mg 0.0002 0.0001 Pantothenic Acid, mg 0.57 0.24 Vitamin K, mg 0.0036 0.0015 Biotin, mg 0.0047 47.4 220 83.0 0.0020 Choline, mg 43.4 18.3 Inositol, mg 4.3 1.8 * Standard Dilution = 1 kcal/mL 0.0015 20.0 93.0 35.0 Water, Maltodextrin, Sugar, Fractionated Coconut Oil, Canola Oil, High Oleic Sunflower Oil, L-Arginine, L-Lysine L-Aspartate, Microcrystalline Cellulose, Calcium Glycerophosphate, L-Leucine, L- Phenylalanine, L-Proline, L-Valine, Glycine, L-Isoleucine, Mono and Diglycerides, Diacetyl Tartaric Acid Esters of Mono and Diglycerides, N-Acetyl L-Methionine, L-Threonine, Dispotassium Phosphate, L-Histidine, L-Serine, L-Alanine, Tripotassium Citrate, Fractionated Coconut Oil, Palm Kernel Oil, Magnesium Acetate, L-Tryptophan, Choline Bitartrate, Calcium Chloride, L-Tyrosine, Trisodium Citrate, L-Ascorbic Acid, Sodium Chloride, Acesulfame Potassium*, L-Cystine, Taurine, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, M-Inositol, Niacinamide, Manganese Sulfate, Cupric Sulfate, Calcium-D-Pantothenate, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Palmitate, Thiamin Mononitrate, Chromium Sulfate, Sodium Molybdate, Potassium Iodide, Folic Acid, Sodium Hydrogen Selenite, D-Biotin, Phylloquinone, Vitamin D3, Cyanocobalamin. Grape flavoured version of this product contains 2% or less of each of the following: Malic Acid, Artificial Flavour, Vitamin E Acetate. Tropical Fruit flavoured version of this product contains 2% or less of each of the following: Artificial Flavour, Citric Acid, Vitamin E Acetate. Orange-Pineapple flavoured version of this product contains 2% or less of each of the following: Artificial Flavours, Citric Acid, Corn Syrup Solids, Malic Acid, DL-alpha Tocopherol Acetate. * Contains Acesulfame Potassium 23.7 mg/237 mL. Please see individual product case labels for exact order of ingredients. Neocate E028 Splash Ingredients: Nutrition Information: 21 • Intake to be determined by a healthcare professional and is dependent on the age, body weight and medical condition of the patient. Intended for use under medical supervision. • All formulas can be taken orally or tube fed. Not for parenteral use. (Neocate Nutra is a semi-solid food and is not for bottle or tube feeding.) • Do not boil formula or use a microwave to prepare or warm formula. • If taken orally, formulas for beyond 1 year of age are best served chilled. • Once formula is prepared or drink box is opened, formula should be stored in a refrigerator and kept no longer than 24 hours from the time of preparation (time of opening for liquids). Shake or stir formula immediately before use. Specialized Pediatrics • Tube feeding hang time: Nutricia recommends formula can be safely kept at room temperature for up to 4 hours, at which time unused formula should be discarded. 22 Neocate DHA & ARA Refer to product labels for full preparation instructions. Directions for Preparation: At standard dilution (0.67 kcal/mL), 1 level unpacked scoop (4.75 g powder) makes 30 mL of prepared formula. 1.Wash hands with soap and water. For low birth weight or immune-compromised infants consult your healthcare professional. 2.Clean and sanitize working surface. 5.Measure required amount of powder with the 3.Sterilize bottles, nipples, caps and other equipment by provided scoop and add to bottle(s). placing in water which is then brought to a rolling boil for 2 minutes and cool. Store covered until ready for use. 6.Add appropriate amount of water to bottle(s). 4.Bring fresh water to a rolling boil for 2 minutes and cool. 7.Cap bottle(s). Shake well for 15-20 seconds For healthy, full-term infants cool to room temperature. or until powder dissolves. Neocate Junior Directions for Preparation: 2. Add the prescribed amount of Neocate Junior to 1. Measure the required amount of warm or cool water the water. into a container. 3. Cover and shake until the powder has dissolved. • Discard formula left in bottle or cup 1 hour after feeding starts. Neocate Nutra • All provided scoops should be unpacked and level. Use a scale for the most accurate results. Household measures are not recommended for measuring powdered Nutricia products. Directions for Preparation and Use: Storage: Cans: Store unopened cans at room temperature. Avoid extreme temperatures. Cover opened can with provided lid and and store in a cool, dry place (not a refrigerator). Use within one month. Liquids: Store unopened product in a cool, dry place. Once opened, store in a refrigerator and keep no longer than 24 hours. Do not freeze. The suggested serving is 8 scoops (37 g) of powder plus 60 mL to give a spoonable consistency. A smaller serving size can be prepared by adding 30 mL of water to 4 scoops of powder (18.5 g). For infants: Consult your baby’s healthcare team about the need to use cooled, boiled water for mixing. 1. Wash hands thoroughly and clean the preparation area. 3. Gradually add the required amount of water while stirring with a clean spoon. Mix until thickened. To alter 2. Add the recommended number of scoops of Neocate the consistency, add more or less water as required. Nutra to a clean bowl. Neocate Nutra should be prepared immediately prior to feeding. Any prepared product remaining should be discarded if not used within one hour. The product will further thicken if refrigerated. Neocate Nutra can be added to cooked dishes. Do not add to very hot foods. Do not warm prepared product. Not suitable as a sole source of nutrition. Not for bottle or tube feeding. Neocate Splash and E028 Splash Directions for Preparation: Shake well before use. Specialized Pediatrics Mixing Instructions DIRECTIONS FOR PREPARATION AND USE: 23 Specialized Pediatrics 24 Measure Weight Neocate Infant DHA & ARA Infant Formula 1 scoop 4.75 g 1/2 tsp 1.0 g 1 tsp 2.0 g 1 Tbsp 7.0 g 1/4 cup 30.0 g 1/3 cup 35.0 g 1/2 cup 57.0 g 1 cup 114 g Neocate Junior, Unflavoured and Tropical 1 scoop 8.2 g 1/2 tsp 1.2 g 1 tsp 2.4 g 1 Tbsp 7.3 g 1/4 cup 29.0 g 1/3 cup 38.7 g 1/2 cup 58.0 g 1 cup 116 g Neocate Junior with Prebiotics Fibre, Unflavoured 1 scoop 8.2 g 1/2 tsp 1.4 g 1 tsp 2.7 g 1 Tbsp 8.1 g 1/4 cup 32.3 g 1/3 cup 43.0 g 1/2 cup 64.5 g 1 cup 129 g Measure Weight Neocate Nutra 1 scoop 4.6 g 1/2 tsp 1.3 g 1 tsp 2.6 g 1 Tbsp 7.9 g 1/4 cup 31.5 g 1/3 cup 42.0 g 1/2 cup 63.0 g 1 cup 126 g Neocate Junior with Prebiotic Fibre, Vanilla 1 scoop 8.2 g 1/2 tsp 1.3 g 1 tsp 2.5 g 1 Tbsp 7.5 g 1/4 cup 30.0 g 1/3 cup 40.0 g 1/2 cup 60.0 g 1 cup 120 g Neocate Junior with Prebiotics Fibre, Strawberry 1 scoop 8.0 g 1/2 tsp 1.2 g 1 tsp 2.3 g 1 Tbsp 6.9 g 1/4 cup 27.8 g 1/3 cup 37.0 g 1/2 cup 55.5 g 1 cup 111 g Household measures are based on standard dry household measures.* All measures are level and unpacked. These values are approximations only and have been provided for convenience: results can vary significantly based on the individual, device, and method. Nutricia North America recommends using a scale for greatest accuracy. The scoops Nutricia provides are validated for use with Nutricia formulas, so are preferable to household measures. *Dry measures: 1 cup = 240 mL; 1/2 cup = 120 mL; 1/3 cup = 80 mL; 1/4 cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; 1/2 tsp = 2.5 mL. Volume Prescription Neocate DHA & ARA Infant Formula Volume/day 590 mL 710 mL 830 mL 945 mL 1 Liter 1.2 Liters Total Volume/can 0.67 kcal/mL (# cans/month) 7 9 10 12 13 15 2.5 L 0.73 kcal/mL (# cans/month) 8 10 11 13 15 16 2.3 L 0.80 kcal/mL (# cans/month) 9 11 12 14 16 18 2.1 L 0.87 kcal/mL (# cans/month) 10 12 14 15 17 19 1.9 L 0.93 kcal/mL (# cans/month) 10 12 14 16 18 20 1.8 L 1 kcal/mL (# cans/month) 11 13 15 18 20 22 1.7 L Neocate Nutra Servings/day Suggested serving size Half serving 8 scoops Nutra (175 kcal) 4 scoops Nutra (88 kcal) 10 servings/can 21 servings/can (# cans/month) (# cases/month) (# cans/month) (# cases/month) 1 Serving 2 Servings 3 Servings 4 Servings 3 6 9 12 1 2 3 3 2 3 5 6 1 1 2 2 Volume/day Neocate Junior Unflavoured 590 mL 710 mL 830 mL 945 mL 1 Liter 1.2 Liters 1 kcal/mL (# cans/month) (# cs/month) 10 3 12 3 14 4 16 4 17 5 19 5 Neocate Junior Flavoured Neocate Splash & E028 Splash 1 kcal/mL (# cans/month) (# cs/month) 10 3 12 3 14 4 16 4 18 5 20 5 1 kcal/mL (# boxes/month) (# cs/month) 76 3 92 4 107 4 122 5 137 6 152 6 Number of cases per month (30 days) are rounded up to the nearest whole number. Specialized Pediatrics Household Measurements Household Measures 25 Specialized Pediatrics Nutrient Dilution Chart (0.67 - 0.83 kcal/mL) 26 Nutrients per 100 mL Dilution, kcal/mL 0.67 0.70 0.73 0.77 0.80 0.83 Dilution, kcal/fl oz 20 21 22 23 24 25 Energy, kcal 66.770.073.376.7 80.083.3 Energy, kJ 279294308322 336350 Protein Equivalent, g 2.12.22.32.4 2.52.6 Carbohydrate, g 7.88.28.69.0 9.49.8 Fat, g 3.03.23.33.5 3.63.8 Linoleic Acid, g 0.45 0.48 0.51 0.53 0.55 0.57 ARA, mg 10.1 10.6 11.1 11.6 12.1 12.6 DHA, mg 5.8 6.1 6.3 6.6 6.9 7.2 Ash, g 0.540.570.590.62 0.650.67 Vitamins Vitamin A, IU 260274287300 313326 Vitamin D3, IU 39.841.943.945.9 47.949.9 Vitamin E, IU 0.760.800.840.87 0.910.95 Vitamin K, mg 0.00580.00620.00640.0067 0.00700.0073 Thiamine, mg 0.050.050.050.06 0.060.06 Riboflavin, mg 0.090.100.100.11 0.110.11 Vitamin B6, mg 0.080.090.090.09 0.100.10 Vitamin B12, mg 0.00020.00020.00020.0002 0.00020.0002 Niacin, mg 1.01.11.11.2 1.21.3 Folic Acid, mg 0.00680.00710.00750.0078 0.00820.0085 Pantothenic Acid, mg 0.410.430.450.47 0.490.51 Biotin, mg 0.00210.00220.00230.0024 0.00250.0026 Vitamin C, mg 6.26.56.87.1 7.47.7 Choline, mg 8.79.19.6 10.010.5 10.9 Inositol, mg 15.516.317.117.8 18.619.4 Minerals00 00 Calcium, mg 82.586.890.995.1 99.2 103 Phosphorus, mg 61.965.268.371.4 74.577.6 Magnesium, mg 8.28.69.19.5 9.9 10.3 Iron, mg 1.21.31.41.4 1.51.5 Zinc, mg 1.11.21.21.3 1.31.4 Manganese, mg 0.06000.06320.06620.0692 0.07220.0752 Copper, mg 0.08220.08650.09060.0947 0.09880.1029 Iodine, mg 0.01030.01080.01130.0118 0.01240.0129 Molybdenum, mg 0.00320.00330.00350.0036 0.00380.0040 Chromium, mg 0.00240.00250.00260.0027 0.00290.0030 Selenium, mg 0.00250.00260.00270.0029 0.00300.0031 Sodium, mg 24.826.127.328.6 29.831.1 Potassium, mg 103109114119 124129 Chloride, mg 51.454.056.659.2 61.864.3 Neocate® DHA & ARA Nutrient Dilution Chart (0.87 - 1.0 kcal/mL) Nutrients per 100 mL Dilution, kcal/mL 0.87 0.90 0.93 0.97 1.00 Dilution, kcal/fl oz 26 27 28 29 30 Energy, kcal 86.7 90.0 93.3 96.7 100 Energy, kJ 364 378 392 405 419 Protein Equivalent, g 2.7 2.8 2.9 3.0 3.1 Carbohydrate, g 10.1 10.5 10.9 11.3 11.7 Fat, g 3.9 4.1 4.2 4.4 4.5 Linoleic Acid, g 0.60 0.62 0.64 0.67 0.69 ARA, mg 13.1 13.6 14.1 14.6 15.1 DHA, mg 7.5 7.8 8.1 8.4 8.6 Ash, g 0.70 0.73 0.75 0.78 0.81 Vitamins Vitamin A, IU 339 352 365 378 391 Vitamin D3, IU 51.9 53.9 55.9 57.9 59.9 Vitamin E, IU 0.99 1.0 1.1 1.1 1.1 Vitamin K, mg 0.0076 0.0079 0.0082 0.0085 0.0088 Thiamine, mg 0.06 0.07 0.07 0.07 0.07 Riboflavin, mg 0.12 0.12 0.13 0.13 0.14 Vitamin B6, mg 0.11 0.11 0.12 0.12 0.12 Vitamin B12, mg 0.0002 0.0002 0.0002 0.0003 0.0003 Niacin, mg 1.3 1.4 1.4 1.5 1.5 Folic Acid, mg 0.0089 0.0092 0.0095 0.0099 0.0102 Pantothenic Acid, mg 0.54 0.56 0.58 0.60 0.62 Biotin, mg 0.0027 0.0028 0.0029 0.0030 0.0031 Vitamin C, mg 8.0 8.3 8.6 9.0 9.3 Choline, mg 11.3 11.8 12.2 12.6 13.1 Inositol, mg 20.2 21.0 21.7 22.5 23.3 Minerals 0 00 0 0 Calcium, mg 107 112 116 120 124 Phosphorus, mg 80.7 83.8 86.9 90.0 93.1 Magnesium, mg 10.7 11.1 11.5 11.9 12.4 Iron, mg 1.6 1.7 1.7 1.8 1.9 Zinc, mg 1.4 1.5 1.6 1.6 1.7 Manganese, mg 0.0782 0.0812 0.0842 0.0873 0.0903 Copper, mg 0.1070 0.1112 0.1153 0.1194 0.1235 Iodine, mg 0.0134 0.0139 0.0144 0.0149 0.0154 Molybdenum, mg 0.0041 0.0043 0.0044 0.0046 0.0048 Chromium, mg 0.0031 0.0032 0.0033 0.0034 0.0036 Selenium, mg 0.0032 0.0034 0.0035 0.0036 0.0037 Sodium, mg 32.3 33.6 34.8 36.0 37.3 Potassium, mg 134 140 145 150 155 Chloride, mg 66.9 69.5 72.1 74.6 77.2 Specialized Pediatrics Dilution Charts Neocate® DHA & ARA 27 Neocate® Junior, Unflavoured Dilution Charts 0.67 kcal/mL (Standard dilution) Amount of Neocate Powder scoops grams 4 19.0 8 38.0 10 47.5 13 61.8 17 80.8 20 95.0 24 114.0 28 133.0 33 156.8 35 166.3 Volume Approximate of Water† Final Volume* mL fl oz mL fl oz 105 3.5 120 4.0 210 7.0 240 8.0 270 9.0 305 10.1 345 11.5 390 12.9 450 15.0 505 16.9 540 18.0 605 20.2 630 21.0 720 24.0 750 25.0 845 28.1 870 29.0 980 32.7 930 31.0 1045 34.9 Specialized Pediatrics 0.73 kcal/mL 28 Amount of Volume Approximate Neocate Powder of Water† Final Volume* scoops grams mL fl oz mL fl oz 5 23.8 120 4.0 135 4.6 7 33.3 165 5.5 190 6.3 10 47.5 240 8.0 275 9.1 14 66.5 330 11.0 375 12.6 18 85.5 435 14.5 495 16.5 21 99.8 510 17.0 580 19.3 26 123.5 630 21.0 715 23.9 31 147.3 750 25.0 855 28.4 36 171.0 870 29.0 990 33.0 43 204.3 1020 34.0 1165 38.8 0.80 kcal/mL Amount of Neocate Powder scoops grams 7 33.3 9 42.8 11 52.3 14 66.5 20 95.0 25 118.75 29 137.8 33 156.75 39 185.25 42 199.5 Volume Approximate of Water† Final Volume* mL fl oz mL fl oz 150 5.0 175 5.8 195 6.5 225 7.5 240 8.0 275 9.2 300 10.0 345 11.6 435 14.5 500 16.7 540 18.0 625 20.8 630 21.0 725 24.2 720 24.0 830 27.7 840 28.0 970 32.3 900 30.0 1040 34.7 0.93 kcal/mL Amount of Neocate Powder scoops grams 5 23.8 9 42.8 14 66.5 18 85.5 23 109.3 28 133.0 33 156.8 40 190.0 45 213.8 53 251.8 0.87 kcal/mL Amount of Neocate Powder scoops grams 3 14.3 6 28.5 12 57.0 15 71.3 21 99.8 26 123.5 32 152.0 36 171.0 43 204.3 49 232.8 Volume Approximate of Water† Final Volume* mL fl oz mL fl oz 60 2.0 70 2.3 120 4.0 140 4.7 240 8.0 280 9.3 300 10.0 350 11.7 420 14.0 490 16.3 510 17.0 595 19.9 630 21.0 735 24.5 720 24.0 840 28.0 840 28.0 985 32.8 960 32.0 1125 37.4 Volume Approximate of Water† Final Volume* mL fl oz mL fl oz 90 3.0 105 3.6 165 5.5 195 6.5 255 8.5 300 10.1 330 11.0 390 13.0 420 14.0 495 16.5 510 17.0 605 20.1 600 20.0 710 23.7 720 24.0 855 28.4 810 27.0 960 32.0 960 32.0 1135 37.9 1 kcal/mL Amount of Neocate Powder scoops grams 8 38 10 47.5 16 76.0 20 95 25 118.75 31 147.25 36 171.0 41 194.75 49 232.75 58 275.5 Volume Approximate of Water† Final Volume* mL fl oz mL fl oz 135 4.5 160 5.4 165 5.5 200 6.6 270 9.0 325 10.8 330 11.0 395 13.2 420 14.0 505 16.8 510 17.0 615 20.4 600 20.0 720 24.0 690 23.0 825 27.5 810 27.0 975 32.4 960 32.0 1155 38.4 * This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 4.75 grams powder and provides 22.22 kcal. 1 gram provides 4.83 kcal and displaces ~0.70 mL water. For household measures, see page 24. Dilution Charts 0.67 kcal/mL 0.93 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 105 2 16.4 3.9117 7.0 210 4 32.8 7.8234 10.5 315 6 49.2 11.7 350 21.0 630 12 98.4 23.4 701 30.0 900 17 139 33.31000 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 6.0 180 5 41.0 7.0210 12.0 360 10 82.0 14.0 419 18.0 540 15 123 21.0 629 24.0 720 20 164 27.9 838 30.0 900 25 205 34.91048 Water Volume* Neocate Powder Final Volume* fl oz mL scoops grams fl oz mL 8.0 240 5 41.0 9.0270 11.0 330 7 57.4 12.4 371 16.0 480 10 82.0 18.0 539 19.0 570 12 98.4 21.4 641 30.0 900 19 156 33.71012 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 100 3 24.6 4.0120 6.5 200 6 49.2 8.0240 10.0 300 9 73.8 11.8 353 20.0 600 18 148 24.0 715 28.0 840 25 205 32.9 988 0.73 kcal/mL † 0.80 kcal/mL Water Volume* Neocate Powder Final Volume* fl oz mL scoops grams fl oz mL 8.5 255 6 49.2 9.7290 11.5 345 8 65.6 13.1 392 16.0 480 11 90.2 18.2 545 20.0 600 14 115 22.8 683 30.0 900 21 172 34.11024 † 0.87 kcal/mL Water Volume* Neocate Powder Final Volume* fl oz mL scoops grams fl oz mL 4.0 120 3 24.6 4.6138 8.0 240 6 49.2 9.2275 12.0 360 9 73.8 13.8 413 17.0 510 13 107 19.6 587 29.0 870 22 180 33.31000 † 1 kcal/mL (Standard dilution) 1.07 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 12.5 375 12 98.4 14.9 446 15.5 465 15 123 18.5 554 18.5 555 18 148 22.0 661 21.5 645 21 172 25.6 769 28.0 840 27 221 33.3 999 Specialized Pediatrics Dilution Charts Neocate® DHA & ARA 1.13 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 8.5 255 9 73.8 10.3308 11.5 345 12 98.4 13.9 416 14.5 435 15 123 17.5 524 21.0 630 22 180 25.3 760 27.0 810 28 230 32.5 975 *This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 8.2 grams powder and provides 39.2 kcal. 1 gram provides 4.78 kcal and displaces ~0.72 mL water. For household measures, see page 24. 29 0.67 kcal/mL Dilution Charts 0.67 kcal/mL Dilution Charts 0.93 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 6.0 180 5 41.0 7.0210 9.5 285 8 65.6 11.1334 17.0 510 14 115 19.8 595 23.0 690 19 156 26.8 805 28.0 840 23 189 32.7 980 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.0 150 3 24.6 5.6167 10.0 300 6 49.2 11.2 335 15.0 450 9 73.8 16.7 502 20.0 600 12 98.4 22.3 670 29.0 870 17 139 32.3 969 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 105 3 24.6 4.1122 7.0 210 6 49.2 8.2245 14.0 420 12 98.4 16.3 490 21.0 630 18 148 24.5 735 28.0 840 24 197 32.7 980 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 8.0 240 5 41.0 9.0270 11.0 330 7 57.4 12.4 372 14.0 420 9 73.8 15.8 475 19.0 570 12 98.4 21.4 643 30.0 900 19 156 33.81015 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 100 3 24.6 4.0120 6.5 200 6 49.2 8.0240 11.0 330 10 82.0 13.0 391 20.0 600 18 148 24.0 715 28.0 840 25 205 33.1 992 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.5 135 3 24.6 5.1152 9.0 270 6 49.2 10.2305 15.0 450 10 82.0 16.9 508 21.0 630 14 115 23.7 712 29.0 870 19 156 32.7 981 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.0 120 4 32.8 5.0150 7.5 225 7 57.4 9.0270 14.0 420 13 107 16.5 496 21.0 630 20 164 25.0 750 28.0 840 26 213 33.0 991 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 8.5 255 6 49.2 9.7291 11.5 345 8 65.6 13.1 394 16.0 480 11 90.2 18.2 547 20.0 600 14 115 22.8 685 29.0 870 20 164 33.0 991 Water Volume* fl oz mL 14.5 435 17.5 525 21.5 645 25.5 765 28.0 840 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.5 165 4 32.8 6.3188 9.5 285 7 57.4 10.9326 14.0 420 10 82.0 15.9 478 21.0 630 15 123 23.9 717 29.0 870 21 172 33.1 992 Water Volume* fl oz mL 15.5 465 18.5 555 22.5 675 26.5 795 30.0 900 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 6.5 195 5 41.0 7.5225 9.0 270 7 57.4 10.4312 13.0 390 10 82.0 15.0 451 21.0 630 16 131 24.2 727 29.0 870 22 180 33.41003 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 7.5 225 8 65.6 9.1274 10.5 315 11 90.2 12.7 382 15.0 450 16 131 18.2 547 20.0 600 21 172 24.2 727 26.0 780 27 221 31.5 944 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.0 150 4 32.8 5.8173 10.0 300 8 65.6 11.6 347 15.0 450 12 98.4 17.3 520 20.0 600 16 131 23.1 693 28.0 840 22 180 32.3 968 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.5 165 6 49.2 6.7200 10.0 300 11 90.2 12.1 364 15.5 465 17 139 18.8 564 20.0 600 22 180 24.3 728 28.0 840 31 254 34.01020 0.80 kcal/mL Specialized Pediatrics 0.93 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 105 2 16.4 3.9117 7.0 210 4 32.8 7.8234 12.5 375 7 57.4 13.9 417 21.0 630 12 98.4 23.4 703 30.0 900 17 139 33.41003 0.73 kcal/mL 30 Neocate® Junior with Prebiotic Fibre, Vanilla 0.87 kcal/mL 1 kcal/mL (Standard dilution) 1.07 kcal/mL Neocate Powder† scoops grams 14 115 17 139 21 172 25 205 27 221 1.13 kcal/mL Final Volume* fl oz mL 17.3 520 20.9 628 25.7 772 30.6 917 33.51004 *This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 8.2 grams powder and provides 39.2 kcal. 1 gram provides 4.78 kcal and displaces ~0.74 mL water. For household measures, see page 24. 0.73 kcal/mL 0.80 kcal/mL 0.87 kcal/mL 1 kcal/mL (Standard dilution) 1.07 kcal/mL Neocate Powder† scoops grams 16 131 19 156 23 189 27 221 31 254 1.13 kcal/mL Final Volume* fl oz mL 18.6 558 22.2 666 27.0 809 31.7 952 36.01080 *This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 8.2 grams powder and provides 37.64 kcal. 1 gram provides 4.59 kcal and displaces ~0.71 mL water. For household measures, see page 24. Specialized Pediatrics Dilution Charts Neocate® Junior with Prebiotic Fibre, Unflavoured 31 0.67 kcal/mL Dilution Charts 0.67 kcal/mL Dilution Charts 0.93 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.5 105 3 24.0 4.1122 7.0 210 6 48.0 8.1244 10.5 315 9 72.0 12.2 366 22.0 660 19 152 25.6 768 28.0 840 24 192 32.5 976 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.0 150 3 24.6 5.6168 10.0 300 6 49.2 11.2 335 15.0 450 9 73.8 16.8 503 20.0 600 12 98.4 22.4 671 30.0 900 18 148 33.51006 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 8.0 240 7 57.4 9.4281 12.5 375 11 90.2 14.7 440 16.0 480 14 115 18.8 563 20.0 600 18 148 23.5 706 27.0 810 24 197 31.7 952 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.0 90 2 16.0 3.4101 7.5 225 5 40.0 8.4253 12.0 360 8 64.0 13.5 405 20.0 600 13 104 22.5 674 29.0 870 19 152 32.6 978 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.0 120 4 32.0 5.0150 7.5 225 7 56.0 9.0270 11.5 345 11 88.0 13.6 407 21.0 630 20 160 25.0 750 28.0 840 26 208 32.9 988 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 3.0 90 2 16.4 3.4102 6.0 180 4 32.8 6.8204 12.0 360 8 65.6 13.6 407 19.0 570 13 107 21.6 647 28.0 840 19 156 31.7 952 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.0 120 4 32.8 5.0145 7.0 210 7 57.4 8.0255 11.5 345 11 90.2 13.7 410 20.0 600 20 164 24.0 730 28.0 840 27 221 33.3 999 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.5 165 4 32.0 6.3188 9.5 285 7 56.0 10.8325 12.5 375 9 72.0 14.2 426 22.0 660 16 128 25.0 751 29.0 870 21 168 33.0 989 Water Volume* fl oz mL 15.5 465 19.5 585 24.5 735 29.5 885 34.5 1035 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.0 120 3 24.6 4.6138 8.0 240 6 49.2 9.2275 15.0 450 11 90.2 17.2 515 19.0 570 14 115 21.8 653 28.0 840 21 172 32.1 964 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 9.5 285 10 82.0 11.5344 12.5 375 13 107 15.1 452 15.5 465 16 131 18.6 559 20.0 600 21 172 24.1 724 28.0 840 29 238 33.71011 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 2.5 75 2 16.0 2.9 86 7.5 225 6 48.0 8.6259 10.0 300 8 64.0 11.5 345 20.0 600 16 128 23.0 691 28.0 840 22 176 32.2 965 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.5 165 6 48.0 6.6199 10.0 300 11 88.0 12.1 362 15.5 465 17 136 18.7 562 20.0 600 22 176 24.2 725 26.5 795 29 232 32.0 960 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 8.5 255 7 57.4 9.9296 11.0 330 9 73.8 12.8 383 16.0 480 13 107 18.6 557 21.0 630 17 139 24.3 730 28.0 840 23 189 32.5 976 Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 4.5 135 5 41.0 5.5165 9.0 270 10 82.0 11.0329 15.0 450 17 139 18.3 550 22.0 660 25 205 26.9 808 27.0 810 30 246 32.9 987 0.80 kcal/mL Specialized Pediatrics 0.93 kcal/mL Water Volume* Neocate Powder† Final Volume* fl oz mL scoops grams fl oz mL 5.0 150 3 24.0 5.6167 8.5 255 5 40.0 9.4283 15.0 450 9 72.0 16.7 501 22.0 660 13 104 24.5 734 32.0 960 19 152 35.61068 0.73 kcal/mL 32 Neocate® Junior, Tropical 0.87 kcal/mL 1 kcal/mL (Standard dilution) 1.07 kcal/mL Neocate Powder† scoops grams 16 128 20 160 25 200 30 240 35 280 1.13 kcal/mL Final Volume* fl oz mL 18.5 556 23.3 699 29.2 877 35.21055 41.11234 *This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 8.0 grams powder and provides 37.5 kcal. 1 gram provides 4.69 kcal and displaces ~0.71 mL water. For household measures, see page 24. 0.73 kcal/mL 0.80 kcal/mL 0.87 kcal/mL 1 kcal/mL (Standard dilution) 1.07 kcal/mL 1.13 kcal/mL *This chart assumes 1 fl oz = 30 mL. Water volumes are exact, but final volume of prepared formula may vary slightly. † Scoops should be level and unpacked. While the scoops Nutricia provides are validated for use with Nutricia formulas, weighing powder using a scale provides greatest accuracy. 1 level, unpacked scoop yields 8.2 grams powder and provides 37.0 kcal. 1 gram provides 4.51 kcal and displaces ~0.72 mL water. For household measures, see page 24. Specialized Pediatrics Dilution Charts Neocate® Junior with Prebiotic Fibre, Strawberry 33 Update on Monitoring Micronutrients Serum levels of micronutrients, particularly phosphorus, should be routinely monitored by clinicians when Neocate is used as a primary or sole source of nutrition for patients with complex systemic disease involving multiple diagnoses and intestinal disease,* especially in combination with tube feeding and/or a history of prematurity. Neocate** formulas are intended for use under medical supervision. Specialized Pediatrics * A retrospective review identified case studies of patients on primary or sole source nutrition with diagnoses covering multiple systems, including congenital gastrointestinal anomalies and GI surgeries (such as necrotizing enterocolitis, esophageal atresia, tracheoesophageal fistula); neurological conditions (such as seizures, intraventricular hemorrhage, hydrocephalus); respiratory (lung disease, tracheostomy, aspiration); cardiac (congenital heart disease); and other systemic conditions, often in conjunction with tube feeding and/or a history of prematurity. 34 ** Neocate is an amino acid-based formula for dietary management of cow milk allergy, multiple food protein allergies, and related GI and allergic conditions for which an amino acid-based diet is indicated. bo li c s Metabolics Me ta For samples, visit www.MedicalFood.com. 35 Metabolics A phenylalanine-free powdered infant formula containing iron, DHA and ARA, for the dietary management of phenylketonuria (PKU). 36 Main Features: Indications: •Phenylalanine-free • Includes DHA and ARA • Unflavoured powder • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, and minerals • Periflex Infant provides 13 g of protein equivalent per 100 g of powder • Standard dilution = 67 kcal/100 mL • Osmolality (standard dilution) = 375 mOsm/kg H2O • Displacement: 0.68 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118326 Product Packaging 6 x 400 g Calories Per Can 1684 Ingredients: Nutrients Per 100 g Per 100 mL Vitamins Per 100 g Per 100 mL Energy, kcal (kj) 421.(1766)67.(279) Vitamin A, IU 1648 260 Protein Equivalent, g 13 2.1 252 39.8 Vitamin D3, IU Carbohydrate, g 49.3 7.8 Vitamin, E IU 4.8 0.76 Fat, g 19.1 3 0.0370 0.0058 Vitamin K1, mg Linoleic Acid, g 2.9 0.45 Thiamine, mg 0.39 0.06 Arachidonic Acid, mg 63.4 10 Riboflavin, mg 0.58 0.09 Docosahexaenoic Acid, mg 36.3 5.7 Niacin, mg 6.5 1 Ash, g 3.4 0.54 0.52 0.08 Vitamin B6, mg Amino Acids, g 0.0011 0.0002 Vitamin B12, mg L-Alanine 0.620.48 Folic Acid, mg 0.043 0.0068 L-Arginine 1.090.84 Pantothenic Acid, mg 2.6 0.41 L-Aspartic Acid 1.02 0.78 Biotin, mg 0.013 0.0021 L-Cystine 0.410.32 Vitamin C, mg 39 6.2 Glycine 0.960.74 Choline, mg 55 8.7 L-Histidine 0.630.48 Inositol, mg 98 15.5 L-Isoleucine 0.960.74 Calcium, mg 522 82.5 L-Leucine 1.651.27 Phosphorus, mg 392 61.9 L-Lysine 1.110.85 Magnesium, mg 52 8.2 L-Methionine 0.260.20 Iron, mg 7.8 1.2 L-Phenylalanine Nil Added Nil Added Zinc, mg 7 1.1 L-Proline 1.100.85 Manganese, mg 0.38 0.06 L-Serine 0.720.55 Copper, mg 0.52 0.0822 L-Threonine 0.810.62 Iodine, mg 0.065 0.0103 L-Tryptophan 0.310.24 Molybdenum, mg 0.02 0.0032 L-Tyrosine 1.441.11 Chromium, mg 0.015 0.0024 L-Valine 1.050.81 Selenium, mg 0.0157 0.0025 L-Carnitine 0.010.01 Sodium, mg 157 24.8 Taurine 0.020.02 Potassium, mg 653 103 L-Glutamine 1.280.98 Chloride, mg 325 51.4 Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower Oil, Soy Oil, Coconut Oil), Calcium Phosphate, L-Arginine L-Aspartate, Tripotassium Citrate, L-Leucine, L-Lysine Acetate, L-Tyrosine, L-Glutamine, Lproline, L-Valine, Glycine, L-Isoleucine, Citric Acid Esters Of Mono- And Diglycerides, L-Threonine, L-Serine, Lhistidine, L-Alanine, Sodium Chloride, L-Cystine, L-Tryptophan, L-Methionine, Magnesium Acetate, Magnesium Laspartate, Potassium Chloride, Mortierella Alpina Oil*, Choline Bitartrate, Inositol, Crypthecodinium. Cohnii Oil**, Ascorbic Acid (Vitamin C), Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Niacinamide, Sunflower Oil, Dl-Alpha Tocopherol Acetate (Vitamin E), Calcium-DPantothenate, Cupric Sulfate, Manganese Sulfate, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate , Thiamine Chloride Hydrochloride, Ascorbyl Palmitate, Potassium Iodide, Chromium Sulfate, Mixed Tocopherols, Dl-Alpha Tocopherol (Vitamin E), Phylloquinone (Vitamin K1), Sodium Molybdate, Folic Acid, Sodium Hydrogen Selenite, Biotin, Cholecalciferol (Vitamin D3), Cyanocobalamin (Vitamin B12) Periflex Infant Periflex® Infant Nutrition Information: * A Source of Arachidonic Acid (ARA) ** A Source of Docosahexaenoic Acid (DHA) 37 PKU Periflex Junior Plus Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in children over 1 year of age. 38 Main Features: Indications: •Phenylalanine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate (including a multi-fiber blend), fat (including DHA), vitamins, minerals and trace elements • Age-appropriate DRI formulation • Provides 28 g protein equivalent and 12.5 g fat per 100 g of powder • Available in plain, vanilla, berry and orange • Osmolality (mOsm/kg): 1340 (at 1 kcal/mL) • Displacement: 0.72 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 89477 - Plain 89478 - Vanilla 89474 - Berry 89476 - Orange Product Packaging 6 x 400 g (14.1 oz) 6 x 400 g (14.1 oz) 6 x 400 g (14.1 oz) 6 x 400 g (14.1 oz) Calories Per Can 1540 1508 1508 1508 Per 10 g Nutrients Per 100 g Protein Equivalent Calories (flavours) 385.(377)138.(136) Protein Equivalent, g 28 10 Fat, g 12.5 4.5 Saturates, g 2 0.71 Monounsaturates, g 8.2 2.9 Polyunsaturates, g 1.8 0.64 DHA, mg 180 64.3 Carbohydrate, g (flavours) 43.2 (41.2) 15.4 (14.8) Of which Fiber, g 11.2 4 Soluble 8 2.9 Insoluble 3.2 1.1 Amino Acids, g L-Alanine 4.761.7 L-Arginine 1.740.62 L-Aspartic Acid 0.42 0.15 L-Cystine 1.90.68 L-Glutamine 3.361.2 Glycine 4.591.6 L-Histidine 0.70.25 L-Isoleucine 1.40.50 L-Leucine 2.240.80 L-Lysine 1.850.66 L-Methionine 0.730.26 L-Phenylalanine Nil Added Nil Added L-Proline 2.240.80 L-Serine 1.20.43 L-Threonine 2.520.90 L-Tryptophan 0.420.15 L-Tyrosine 2.661.0 L-Valine 1.680.60 L-Carnitine 0.020.01 Taurine 0.050.02 Ingredients: Per 10 g Vitamins Per 100 g ProteinEquivalent Vitamin A, IU (mcg RE) 1399.(420)500.(150) Vitamin D, IU (mcg) 840.(21.0)300.(7.5) 12.5 (8.4) 4.5 (3) Vitamin E, IU (mg α TE) Vitamin K, mcg 14 5 Thiamin, mg 0.93 0.33 Riboflavin, mg 0.73 0.26 0.73 0.26 Vit. B6, mg 1.3 0.46 Vit. B12, mcg Niacin, mg 2.0 0.71 Folic Acid, mg 210 75 Pantothenic Acid, mg 4.2 1.5 Biotin, mcg 11.2 4 Vitamin C, mg 42 15 Choline, mg 224 80 Inositol, mg 56 20 Minerals Calcium, mg 980 350 Phosphorus, mg 641 228.9 Magnesium, mg 113 40.4 Iron, mg 10 3.6 Zinc, mg 4.9 1.75 Manganese, mcg 920 328.6 Copper, mcg 560 200 Iodine, mcg 139 49.6 Molybdenum, mcg 25.5 9.1 Chromium, mcg 10.2 3.6 Selenium, mcg 28.2 10.1 Sodium, mg 280 100 Potassium, mg 445 158.9 Chloride, mg 406 145 Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Chain Triglycerides (Palm Kernel and/or Coconut Oil), Sunflower), L-Alanine, Glycine, Fructooligosaccharides, L-Glutamine, Inulin, Corn Starch, L-Tyrosine, Calcium Phosphate Dibasic, L-Lysine Acetate, L-Threonine, Microcrystalline Cellulose, L-Leucine, L-Proline, Artificial Flavour, Gum Arabic, L-Cystine, L-Arginine, L-Valine, L-Isoleucine, Tripotassium Citrate, Trisodium Citrate, L-Serine, Calcium Chloride, L-Methionine, L-Histidine, Maltodextrin, Choline Bitartrate, Magnesium Hydrogen Phosphate, Magnesium L-Aspartate, CAEM (an emulsifier), C. Cohnii Oil**, L-Tryptophan, Tricalcium Citrate, L-Ascorbic Acid, Soy Fiber, M-Inositol, Taurine, Ferrous Sulfate, Sunflower Lecithin, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Ascorbyl Palmitate, Folic Acid, Potassium Iodide, Mixed Tocopherols, Sodium Molybdate, Sodium Selenite, Chromium Chloride, DL-alpha Tocopherol, Vitamin D3, Phylloquinone, D-Biotin, Cyanocobalamin Berry version also contains: Natural Flavour, Malic Acid, Artificial Sweetener: Sucralose, Artificial Color (Beet Red). Vanilla version also contains: Artificial Sweetener: Sucralose. Orange version also contains: Citric Acid, Natural Flavour, Artificial Sweetener: Sucralose, Artificial Colors (Beta Carotene, Beet Red). PKU Periflex Junior Plus Nutrition Information: ® Please see individual product label for exact order of ingredients. **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) 39 Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in older children and adults, including pregnant women and women of child-bearing age. 40 Main Features: Indications: •Phenylalanine-free • Low in saturated fat • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements • Excellent balance of linoleic acid and a-linolenic acid, providing a preferable 4:1 ratio of n-6 to n-3 • Age-appropriate DRI formulation • Periflex Advance provides 35 g of protein equivalent and 12.6 g of fat per 100 g of powder • Meets protein requirements in lower volume • Pleasant taste, smell and texture • Available in unflavoured and orange • Osmolality (mOsm/kg): Dilution UnflavouredOrange 1 to 5 830 890 1 to 4 1060 1100 •Phenylketonuria • Displacement: 0.60 mL/g For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118305 - Unflavoured 118307 - Orange Product Packaging 6 x 454 g (1 lb) 6 x 454 g (1 lb) Calories Per Can 1748 1675 Per 10 g Nutrients Per 100 g Protein Equivalent Calories (orange) 385.(369) 110 (105.4) Protein Equivalent, g 35 10 Fat, g 12.6 3.6 Saturated, g 1.4 0.4 Monounsaturated, g 7.9 2.3 Polyunsaturated, g 2.7 0.8 Linoleic Acid, mg 2064 590 α-Linolenic Acid, mg 535 153 Carbohydrate, g (orange) 33.(29) 9.4 (8.3) Amino Acids, g L-Alanine1.4 0.40 L-Arginine2.6 0.74 L-Aspartic Acid 2.5 0.71 L-Cystine0.96 0.27 Glycine2.5 0.71 L-Histidine1.5 0.43 L-Isoleucine2.4 0.69 L-Leucine 4.0 1.14 L-Lysine 3.1 0.89 L-Methionine 0.64 0.18 L-Phenylalanine Nil Added Nil Added L-Proline2.8 0.80 L-Serine1.8 0.51 L-Threonine1.9 0.54 L-Tryptophan0.78 0.22 L-Tyrosine3.5 1.00 L-Valine2.5 0.71 L-Carnitine0.03 0.01 Taurine0.12 0.03 L-Glutamine4.3 1.23 Ingredients: Per 10 g Protein Equivalent Vitamins Per 100 g Vitamin A, IU (mcg R.E.) 1951 (586) 557.4 (167.4) 292 (7.3) Vitamin D3, IU (mcg) 83.4 (2.1) Vitamin E, IU (mg α T.E.) 16.2 (10.9) 4.6 (3.1) Vitamin K, mcg 71.8 20.5 Thiamin, mg 0.8 0.2 Riboflavin, mg 0.85 0.2 1.4 0.4 Vitamin B6, mg 2.7 0.8 Vitamin B12, mcg Niacin, mg 5 1.4 Folic Acid, mcg 430 122.9 Pantothenic Acid, mg 4.3 1.2 Biotin, mcg 21.4 6.1 Vitamin C, mg 54.3 15.5 Choline, mg 376 107.4 Inositol, mg 70 20 Minerals Calcium, mg 1035 296 Phosphorus, mg 995 284 Magnesium, mg 268 76.6 Iron, mg 12.9 3.7 Zinc, mg 7.9 2.3 Manganese, mg 1.6 0.5 Copper, mcg 720 0.2 Iodine, mcg 115 32.9 Molybdenum, mcg 32.4 9.3 Chromium, mcg 22.8 6.5 Selenium, mcg 50.8 14.5 Sodium, mg (mEq) 490 (21.3) 1 40 (6.1) Potassium, mg (mEq) 613 (15.7) 175.1 (4.5) Chloride, mg (mEq) 490 (14) 140 (4.0) Corn Syrup Solids, High Oleic Safflower Oil, Canola Oil, L-Lysine, L-Aspartate, L-Glutamine, L -Leucine, L-Tyrosine, L-Proline, L -Arginine, L-Valine, Glycine, L-Isoleucine, Magnesium Hydrogen Phosphate, L-Threonine, and 2% or less of each of the following: L-Serine, Disodium Hydrogen Phosphate, L-Histidine, L-Alanine, Potassium Chloride, Choline Hydrogen Tartrate, L-Cystine, L-Tryptophan, Sugar, L-Methionine, Fractionated Coconut Oil, L-Lysine Acetate, CAEM (An Emulsifier), Tripotassium Citrate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopherol Acetate, Manganese Sulfate, Niacinamide, Calcium D-Panthothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. Unflavoured version also contains: Tricalcium Citrate and 2% or less of Tricalcium Phosphate. Orange flavoured version also contains: Artificial Flavour, Citric Acid, Tricalcium Phosphate and 2% or less of each of the following: Tricalcium Citrate, Guar Gum, Xanthan Gum, Artificial Sweetener: Sucralose, Artificial Colors (Beet Red, Beta Carotene). Periflex Advance Nutrition Information: Periflex® Advance Please see individual product label for exact order of ingredients. 41 Metabolics A phenylalanine-free, ready-to-drink formula for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. 42 Main Features: Indications: •Phenylalanine-free • Contains a balanced mixture of other amino acids, carbohydrate, vitamins and minerals • Can easily be used along with or in place of PKU Periflex Junior Plus or Advance • No measuring or mixing • Great addition to any daily PKU diet plan • Periflex LQ provides 15 g of protein equivalent per 250 mL container • Available in orange crème and berry crème flavours • Osmolality (mOsm/kg): Dilution Orange Berry 0.64 kcal/mL 1080 1030 • Free water: 84% •Phenylketonuria For details on administration, please see pages 146-161. Ordering Information: Product Code 80177 - Orange Crème Product Packaging 18 x 250 mL (8.5 fl oz) Calories Per Container 160 80176 - Berry Crème 18 x 250 mL (8.5 fl oz) 160 Per 10 g Vitamins Per 250 mLProtein Equivalent Per 10 g 555.(167) Nutrients Per 250 mL Protein Equivalent Vitamin A, IU (mcg R.E.) 833.(250) Calories 160107Vitamin D, IU (mcg) 130.(3.3)87.(2.2) 4.7.(3.2) Protein Equivalent, g 15 10 7.(4.8) Vitamin E, IU (mg α T.E.) Fat, g 5 3.3 Vitamin K, mcg 30.8 21 Saturated, g 0.75 0.5 Thiamin, mg 0.35 0.23 Monounsaturated, g 3 22 Riboflavin, mg 0.38 0.25 Polyunsaturated, g 1 0.7 0.6 0.4 Vitamin B6, mg Carbohydrate, g 13.8 9.2 1.2 0.8 Vitamin B12, mcg Amino Acids, g Niacin, mg 2.1 1.4 123 L-Alanine 0.680.45 Folic Acid, mcg 184 L-Arginine 1.280.85 Pantothenic Acid, mg 1.9 1.3 L-Aspartic Acid 1.2 0.80 Biotin, mcg 9.3 6.2 L-Cystine 0.480.32 Vitamin C, mg 23.3 16 107 Glycine 1.230.82 Choline, mg 161 20 L-Histidine 0.730.49 Inositol, mg 30 L-Isoleucine 1.130.75 Minerals 267 L-Leucine 1.951.30 Calcium, mg 400 192 L-Lysine 1.51.00 Phosphorus, mg 288 76 L-Methionine 0.330.22 Magnesium, mg 114 L-Phenylalanine Nil Added Nil Added Iron, mg 5.5 3.7 L-Proline 1.380.92 Zinc, mg 3.5 2 L-Serine 0.850.57 Manganese, mg 0.7 0.5 207 L-Threonine 0.950.63 Copper, mcg 310 33 L-Tryptophan 0.380.25 Iodine, mcg 49 9 L-Tyrosine 1.731.15 Molybdenum, mcg 14 L-Valine 1.250.83 Chromium, mcg 9.8 7 L-Carnitine 0.010.01 Selenium, mcg 21.8 15 Taurine 0.080.05 Sodium, mg (mEq) 210.(9.3)140.(6.2) L-Glutamine Nil Added Nil Added Potassium, mg (mEq) 263.(6.8)175.(4.5) Chloride, mg (mEq) 210.(6) 140.(4) Ingredients: Water, Sugar, and less than 2% of each of the following: Calcium Glycerophosphate, High Oleic Sunflower Oil, L-Lysine Acetate, Canola Oil, L-Leucine, L-Tyrosine, Artificial Flavour, L-Proline, L-Arginine, L-Valine, Glycine, L-Aspartic Acid, L-Isoleucine, MicroCrystalline Cellulose, Citric Acid, L-Threonine, L-Serine, Magnesium Acetate, Tripotassium Citrate, L-Histidine, L-Alanine, L-Cystine, Choline Hydrogen Tartrate, N-Acetyl, L-Methionine, Sodium Chloride, L-Tryptophan, Trisodium Citrate, Soybean Oil, L-Ascorbic Acid, Diacetyl Tartaric Acid Esters of Monoglycerides, Mono- and Diglycerides, Guar Gum, Xanthan Gum, Artificial Sweetener: Acesulfame Potassium, Taurine, M-Inositol, Ferrous Sulphate, Tricalcium Phosphate, Carnitine, Zinc Sulfate, DL-Alpha Tocopherol Acetate, Niacinamide, Manganese Sulphate, Calcium-D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Cholecalciferol, Folic Acid, Cyanocobalamin. Periflex LQ Nutrition Information: Periflex® LQ Please see individual product label for exact order of ingredients. 43 Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. 44 Main Features: Indications: •Phenylalanine-free • Complete with essential vitamins and minerals • Contains a 4:1 ratio of omega-6 to omega-3 fatty acids • PhenylAde Essential Drink Mix provides 25 g of protein equivalent and 13 g of fat per 100 g of powder • Available in chocolate, vanilla, orange creme, strawberry, and unflavoured • Suitable for individuals over 1 year of age • Available in cans and pouches • Osmolalilty (mOsm/kg): 800 Based on standard dilution of 40 g powder to 210 mL of water (7 fl oz) • Displacement: 0.75 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code CANS 9501 - Chocolate 9502 - Vanilla 9503 - Orange Creme 9504 - Strawberry 9508 - Unflavoured POUCHES 95014 - Chocolate 95024 - Vanilla 95034 - Orange Creme 95044 - Strawberry 95084 - Unflavoured Product Packaging Calories Per Can/Pouch 4 x 454 g (1 lb) 4 x 454 g (1 lb) 4 x 454 g (1 lb) 4 x 454 g (1 lb) 4 x 454 g (1 lb) 1784 1784 1784 1784 1784 16 x 40 g (1.4 oz) 16 x 40 g (1.4 oz) 16 x 40 g (1.4 oz) 16 x 40 g (1.4 oz) 16 x 40 g (1.4 oz) 157 157 157 157 157 Ingredients: Nutrition Information: Per 10 g Protein Equivalent Per 10 g Protein Equivalent Nutrients Per 100 g (1 scoop/pouch) Vitamins Per 100 g (1 scoop/pouch) Calories 393157 Vitamin A, IU (mcg R.E.) 1700 (637) (25% as beta-carotene) Protein Equivalent, g 25 10 Vitamin D, IU (mcg) 600 (15) Carbohydrate, g 46 18 Vitamin E, IU (mg α T.E.) 19 (12.7) Fat, g 13 5 Vitamin K, mcg 61 Saturated Fat, g 2.5 1 Thiamin, mg 1.5 Monounsaturated Fat, g 7.9 3.1 Riboflavin, mg 1.5 Polyunsaturated Fat, g 2.7 1.1 1.4 Vitamin B6, mg Linoleic Acid, mg 2178 871 3.0 Vitamin B12, mcg α-Linolenic Acid, mg 545 218 Niacin, mg 17 Amino Acids, g 300 L-Alanine 2.320.93Folic Acid, mcg 4 L-Arginine 1.970.79Pantothenic Acid, mg 30 L-Asparagine 3.491.40Biotin, mcg 60 L-Cystine 0.340.14Vitamin C, mg 210 L-Glutamine 3.891.56Choline, mg Inositol, mg 50 0.61 Glycine1.52 Minerals 0.63 0.25 L-Histidine Calcium, mg 822 0.42 L-Isoleucine1.04 Phosphorus, mg 788 0.90 L-Leucine2.24 Magnesium, mg 210 0.73 L-Lysine1.82 Iron, mg 11 0.61 0.24 L-Methionine Zinc, mg 10 L-Phenylalanine Nil Added Nil Added Manganese, mg 1.3 0.61 L-Proline1.52 Copper, mg 1 0.90 L-Serine2.24 Iodine, mcg 100 0.46 L-Threonine1.15 Molybdenum, mcg 45 0.58 0.23 L-Tryptophan Chromium, mcg 30 L-Tyrosine 2.691.08 Selenium, mcg 40 0.67 L-Valine1.7 Sodium, mg 388 0.04 0.01 L-Carnitine Potassium, mg 872 0.08 0.03 Taurine Chloride, mg 475 680 (255) 240 (6) 7.6 (5.1) 24 0.6 0.6 0.56 1.2 6.8 120 1.6 12 24 84 20 329 315 84 4.4 4 0.52 0.4 40 18 12 16 155 349 190 Sugar†, Modified Food Starch, Canola Oil, Maltodextrin, Safflower Oil, Dextrin, L-Asparagine Monohydrate, L-Glutamine, L-Tyrosine, Natural and Artificial Flavour, L-Lysine Acetate, L-Alanine, L-Leucine, L-Serine, L-Arginine, Monocalcium Phosphate, Corn Syrup Solids, L-Valine, Dicalcium Phosphate, Sodium Citrate, Glycine, L-Proline, Potassium Citrate, Coconut Oil, Soybean Oil, L-Threonine, L-Isoleucine, Potassium Chloride, L-Histidine, L-Methionine, Choline Bitartrate, L-Tryptophan, Flaxseed Oil, Magnesium Oxide, L-Cystine, Titanium Dioxide (Vanilla Flavoured), Ascorbyl Palmitate, Mixed Tocopherols, Rosemary Extract, Silicon Dioxide, Tricalcium Phosphate, Sodium Chloride, Taurine, Ascorbic Acid, Inositol, Ferric Orthophosphate, Vitamin E Acetate, L-Carnitine, Niacinamide, Calcium Phosphate, Zinc Oxide, Copper Gluconate, Vitamin K1, Vitamin D3, Vitamin A Palmitate, D-Calcium Pantothenate, Manganese Sulfate, Mono- and Diglycerides, D-Biotin, Beta-Carotene, Pyridoxine Hydrochloride, Riboflavin, Thiamin Mononitrate, Potassium Iodide, Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride, Sodium Molybdate, FD&C Yellow #6 (Orange Creme Flavoured), FD&C Red #40 (Chocolate, Strawberry Flavoured), FD&C Blue #1 (Strawberry Flavoured), FD&C Blue #2 and Yellow #5 (Chocolate Flavoured). PhenylAde Essential Drink Mix PhenylAde™ Essential Drink Mix † Unflavoured contains corn syrup solids instead of sugar. Please see individual product label for exact order of ingredients. 45 PhenylAde GMP Drink Mix Per 10 g Protein Equivalent Per 10 g Protein Equivalent Whey Protein Concentrate* (from milk), Nutrients Per 100 g (1 scoop) Vitamins Per 100 g (1 scoop) Sugar, Refined Vegetable Oils (Canola, Metabolics A phenylalanine-low, vanilla-flavoured powdered formula containing a balanced mix of glycomacropeptide (GMP), essential and non-essential amino acids, carbohydrates, fat (including docosahexaenoic acid (DHA)), vitamins, minerals and trace elements in individuals with PKU over 1 year of age. 46 Main Features: Indications: • Low in Phenylalanine •Complete with essential vitamins and minerals • With added DHA •PhenylAde GMP Drink Mix provides 30 g of protein equivalent and 12 g of fat per 100 g of powder • Available in vanilla flavour •Suitable for individuals with PKU over 1 year of age •Available in cans •Osmolalilty (mOsm/kg): 460 Based on standard dilution of 33.3 g powder to 150 mL of water (5 fl oz) •Displacement: 0.9 mL/g •Phenylketonuria Ordering Information: Product Code CANS 6831-CAN - Vanilla Product Packaging Calories Per Can/Pouch 4 x 400 g (14.1 oz) 1584 Calories Protein Equivalent, g Phenylalanine, mg Fat, g DHA, mg Carbohydrate, g Amino Acids, g L-Alanine L-Arginine L-Aspartic acid L-Cystine L-Glutamic acid L-Glycine L-Histidine L-Isoleucine L-Leucine L-Lysine L-Methionine L-Phenylalanine L-Proline L-Serine L-Threonine L-Tryptophan L-Tyrosine L-Valine L-Carnitine Taurine 396132 30.0 10.0 46.0 15.3 12.0 4.0 155 51.6 42.0 14.0 1.3 0.44 1.4 0.47 1.9 0.63 0.93 0.31 4.1 1.4 2.2 0.75 1.5 0.49 2.30.76 2.3 0.78 1.3 0.44 0.440.15 0.050.02 2.6 0.86 1.6 0.54 3.71.2 0.720.24 3.7 1.2 1.8 0.61 0.040.01 0.09 0.03 Vitamin A, IU (mcg R.E.) 2040.(765) 680.(255) Vitamin D, IU (mcg) 900.(22.5) 300.(7.5) Vitamin E, IU (mg α T.E.) 22.8 (15.3) 7.6.(5.1) Vitamin K, mcg 72 24 Thiamin, mg 1.8 0.6 Riboflavin, mg 1.8 0.6 1.7 Vitamin B6, mg 0.56 3.6 Vitamin B12, mcg 1.2 Niacin, mg 15.0 5.0 Folic Acid, mcg 360 120 Pantothenic Acid, mg 4.8 1.6 Biotin, mcg 36 12 Vitamin C, mg 72 24 Choline, mg 300 100 Inositol, mg 60 20 Minerals Calcium, mg Phosphorus, mg Magnesium, mg Iron, mg Zinc, mg Manganese, mg Copper, mcg Iodine, mcg Molybdenum, mcg Chromium, mcg Selenium, mcg Sodium, mg Potassium, mg Chloride, mg 1050 945 252 13.2 10.2 1.6 1200 135 54 36 48 465 1047 569 350 315 84 4.4 3.4 0.52 400 45 18 12 16 155 349 190 Safflower, Coconut and Soybean), Modified Corn Starch, Dextrin, Maltodextrin, L-Tyrosine, Tricalcium Phosphate, Natural and Artificial Flavours. Contains 2 % or less of the following: L-Glycine, Magnesium Phosphate, L-Leucine, L-Histidine, L-Arginine, Potassium Chloride, L-Cystine, Choline Bitartrate, Dicalcium Phosphate, L-Tryptophan, C. Cohnii Oil**, Glucose Syrup Solids, Potassium Citrate, Ascorbyl Palmitate, Mixed Tocopherols, Silicon Dioxide, Rosemary Extract, Sodium Chloride, Ascorbic Acid, Taurine, Inositol, Mannitol, Vitamin E Acetate, Ferrous Sulfate, L-Carnitine, Glycerol Mono and Distearate, High Oleic Sunflower Oil, Sodium Polyphosphate, Sunflower Lecithin, Niacinamide, Zinc Oxide, Sodium Ascorbate, Vitamin D3, Vitamin A Palmitate, Copper Gluconate, Manganese Sulfate, D-Calcium Pantothenate, D-Biotin, Beta-Carotene, Thiamin Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Potassium Iodide, Vitamin K1, Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride and Sodium Molybdate. PhenylAde GMP Drink Mix Ingredients: Nutrition Information: ™ *Contains 15.3 mg of phenylalanine/10 g protein equivalent **A source of docosahexaenoic acid (DHA) 47 PhenylAde 40 Drink Mix Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. 48 Main Features: Indications: •Phenylalanine-free • Complete with essential vitamins and minerals • Only 0.5 g of fat and 83 calories per serving • PhenylAde 40 Drink Mix provides 40 g of protein equivalent per 100 g of powder • Available in citrus and unflavoured single serve pouches • Suitable for individuals with PKU over 1 year of age • Osmolalilty (mOsm/kg): 1110 Based on standard dilution of 25 g powder to 120 mL of water (4 fl oz) • Displacement: 0.48 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 95404 - Unflavoured 95414 - Citrus Product Packaging 20 x 25 g (0.88 oz) 20 x 25 g (0.88 oz) Ingredients: Per 10 g Protein Equivalent Per 10 g Protein Equivalent Corn Syrup Solids, Sugar, L-Glutamine, Nutrients Per 100 g (1 pouch) Vitamins Per 100 g (1 pouch) L-Asparagine Monohydrate, L-Serine, Calories Per Can/Pouch 83 83 Calories Protein Equivalent, g Carbohydrate, g Fat, g Saturated Fat, g Monounsaturated Fat, g Polyunsaturated Fat, g Amino Acids, g L-Alanine L-Arginine L-Asparagine L-Cystine L-Glutamine Glycine L-Histidine L-Isoleucine L-Leucine L-Lysine L-Methionine L-Phenylalanine L-Proline L-Serine L-Threonine L-Tryptophan L-Tyrosine L-Valine L-Carnitine Taurine 33083 Vitamin A, IU (mcg R.E.) 1557.(584)389.(146) (25% as beta-carotene) 40 10 38 9.5 Vitamin D, IU (mcg) 347.(8.7) 87.(2.2) 2 0.5 15.4 (10.3) 3.9 (2.6) Vitamin E, IU (mg α T.E.) 0.32 0.08 Vitamin K, mcg 60 15 1.2 0.31 Thiamin, mg 1.4 0.35 0.42 0.11 Riboflavin, mg 1.3 0.32 1.5 0.38 Vitamin B6, mg 3.850.96 2.8 0.7 Vitamin B12, mcg 3.270.82 Niacin, mg 16.4 4.1 5.041.26 Folic Acid, mcg 468 117 0.550.14 Pantothenic Acid, mg 5.8 1.5 6.341.59 Biotin, mcg 35 8.8 2.470.62 Vitamin C, mg 75 18.9 1.020.26 Choline, mg 284 71 1.640.41 Inositol, mg 86 22 3.640.91 Minerals 2.980.75 Calcium, mg 894 224 1.080.27 Phosphorus, mg 809 202 Nil Added Nil Added Magnesium, mg 209 52 2.470.62 Iron, mg 12 3 4.081.02 Zinc, mg 8 2 1.920.48 Manganese, mg 1.8 0.45 0.610.15 Copper, mg 0.87 0.22 3.780.95 Iodine, mcg 133 33 2.740.69 Molybdenum, mcg 40 10 0.060.01 Chromium, mcg 27 6.7 0.120.03 Selenium, mcg 56 13.9 Sodium, mg 424 106 Potassium, mg 776 194 Chloride, mg 1322 331 L-Alanine, L-Tyrosine, L-Lysine Monohydrochloride, L-Leucine, L-Arginine, L-Valine, Citric Acid (Citrus Flavoured), Tricalcium Phosphate, Glycine, L-Proline, Natural Flavour (Citrus Flavoured), L-Threonine, L-Isoleucine, Magnesium Phosphate, L-Methionine, Sodium Citrate, L-Histidine, Dipotassium Phosphate, Modified Food Starch, Canola Oil, Maltodextrin, Safflower Oil, Choline Bitartrate, Potassium Chloride, L-Tryptophan, L-Cystine, Sodium Chloride, Coconut Oil, Soybean Oil, Taurine, Silicon Dioxide, Inositol, Ascorbic Acid, L-Carnitine, Ascorbyl Palmitate, Mixed Tocopherols, Rosemary Extract, Ferric Orthophosphate, Vitamin E Acetate, Zinc Sulfate, Niacinamide, Sucralose, D-Calcium Pantothenate, Vitamin K1, Manganese Sulfate, Vitamin A Palmitate, D-Biotin, Vitamin D3, Beta-carotene, Copper Sulfate, Pyridoxine Hydrochloride, Potassium Iodide, Thiamin Mononitrate, Riboflavin, FD&C Yellow #5 (Citrus Flavoured), Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride and Sodium Molybdate. PhenylAde40 Drink Mix Nutrition Information: ™ Please see individual product label for exact order of ingredients. 49 PhenylAde™ 60 Drink Mix Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. 50 Main Features: Indications: •Phenylalanine-free • Complete with essential vitamins and minerals • Only 49 calories per serving • PhenylAde 60 Drink Mix provides 60 g of protein equivalent per 100 g of powder • Available in vanilla and unflavoured • Suitable for individuals with PKU over 1 year of age • Available in cans or single serve pouches • Osmolalilty (mOsm/kg): 1256 Based on standard dilution of 16.7 g powder to 90 mL of water (3 fl oz) • Displacement: 0.54 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 9560 - Unflavoured 9562 - Vanilla POUCHES 95604 - Unflavoured 95624 - Vanilla Ingredients: Per 10 g Protein Equivalent Per 10 g Protein Equivalent L-Asparagine Monohydrate, L-Glutamine, Nutrients Per 100 g (1 scoop/pouch) Vitamins Per 100 g (1 scoop/pouch) Sugar, L-Tyrosine, L-Lysine Acetate, Product Packaging 4 x 454 g (1 lb) 4 x 454 g (1 lb) Calories Per Can/Pouch 1335 1335 30 x 16.7 g (0.59 oz) 30 x 16.7 g (0.59 oz) 49 49 Calories 29449 Vitamin A, IU (mcg R.E.) 2331.(874)389.(146) (25% as beta-carotene) Protein Equivalent, g 60 10 Vitamin D, IU (mcg) 520.(13)87.(2.2) Carbohydrate, g 11 2 3.8 (2.6) Vitamin E, IU(mg α T.E.) 23 (15.4) Fat, g 1 0.17 Vitamin K, mcg 90 15 Saturated Fat, g <0.5 <0.1 Thiamin, mg 2.1 0.35 Monounsaturated Fat, g <0.5 <0.1 Riboflavin, mg 1.9 0.32 Polyunsaturated Fat, g <0.5 <0.1 2.3 0.38 Vitamin B6, mg Amino Acids, g 4.2 0.7 Vitamin B12, mcg L-Alanine 5.560.93 Niacin, mg 25 4.1 L-Arginine 4.720.79 Folic Acid, mcg 700 117 L-Asparagine 8.361.39 Pantothenic Acid, mg 8.7 1.5 L-Cystine 0.810.13 Biotin, mcg 53 8.8 L-Glutamine 9.311.55 Vitamin C. mg 113 19 Glycine 3.630.61 Choline, mg 425 71 L-Histidine 1.510.25 Inositol, mg 129 22 L-Isoleucine 2.490.42 Minerals L-Leucine 5.370.90 Calcium, mg 1300 217 L-Lysine 4.360.73 Phosphorus, mg 1194 199 L-Methionine 1.450.24 310 52 L-Phenylalanine Nil Added Nil Added Magnesium, mg Iron, mg 18 3 L-Proline 3.630.61 Zinc, mg 12 2 L-Serine 5.370.90 Manganese, mg 2.7 0.45 L-Threonine 2.760.46 Copper, mg 1.3 0.22 L-Tryptophan 1.380.23 Iodine, mcg 180 30 L-Tyrosine 6.451.08 Molybdenum, mcg 60 10 L-Valine 4.010.67 Chromium, mcg 40 6.7 L-Carnitine 0.090.01 Selenium, mcg 83 14 Taurine 0.180.03 Sodium, mg 600 100 Potassium, mg 1162 194 Chloride, mg 900 150 L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Tricalcium Phosphate, Glycine, L-Proline, L-Threonine, Natural and Artificial Flavour (Vanilla Flavoured), L-Isoleucine, Magnesium Phosphate, Sodium Citrate, L-Histidine, L-Methionine, L-Tryptophan, Dipotassium Phosphate, Potassium Chloride, Choline Bitartrate, Soy Lecithin, L-Cystine, Sodium Chloride, Taurine, Ascorbic Acid, Inositol, Silicon Dioxide, L-Carnitine, Ferric Orthophosphate, Sucralose, Vitamin E Acetate, Zinc Sulfate, Niacinamide, D-Calcium Pantothenate, Vitamin K1, Manganese Sulfate, Vitamin A Palmitate, D-Biotin, Vitamin D3, Beta-carotene, Copper Sulfate, Pyridoxine Hydrochloride, Potassium Iodide, Thiamin Mononitrate, Riboflavin, Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride and Sodium Molybdate. PhenylAde60 Drink Mix Nutrition Information: Unflavoured also contains: Corn Syrup Solids, Modified Food Starch, Canola Oil, Maltodextrin, Safflower Oil, Coconut Oil, Soybean Oil, Ascorbyl Palmitate, Mixed Tocopherols and Rosemary Extract. Please see individual product label for exact order of ingredients. 51 PhenylAde™ Amino Acid Blends Metabolics A phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. 52 Main Features: Indications: •Phenylalanine-free • Only 40 calories per serving • 100 g of powder provides 80 g ª of protein equivalent • PhenylAde MTE Amino Acid Blend contains added calcium, phosphorus, magnesium, chromium, molybdenum, and selenium • Suitable for individuals with PKU over 1 year of age • Available in cans and single-serve pouches •Phenylketonuria • Displacement: MTE is 0.47 mL/g and non-MTE is 0.48 mL/g ª MTE is 78 g and non-MTE is 81 g per 100 g. For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code CANS 9500 - Unflavoured 9596 - MTE Unflavoured POUCHES 95004 - Unflavoured 95964 - MTE Unflavoured Product Packaging Calories Per Can/Pouch 4 x 454 g (1 lb) 4 x 454 g (1 lb) 1466 1421 30 x 12.4 g (0.44 oz) 30 x 12.8 g (0.45 oz) 40 40 Per 10 g Protein Equivalent Nutrients Per 100 g (1 scoop/pouch) Calories 32340 Protein Equivalent, g 81 10 Carbohydrate, g 0 0 Fat, g 0 0 Amino Acids, g L-Alanine 7.460.93 L-Arginine 6.330.79 L-Asparagine 11.221.40 L-Cystine 1.080.14 L-Glutamine 12.51.55 Glycine 4.870.61 L-Histidine 2.030.25 L-Isoleucine 3.340.42 L-Leucine 7.200.90 L-Lysine 5.840.73 L-Methionine 1.950.24 L-Phenylalanine Nil Added Nil Added L-Proline 4.870.61 L-Serine 7.200.90 L-Threonine 3.700.46 L-Tryptophan 1.850.23 L-Tyrosine 8.651.08 L-Valine 5.380.67 L-Carnitine 0.120.01 Taurine 0.240.03 Ingredients: Amino Acid Blend: L-Asparagine MTE Amino Acid Blend Unflavoured Monohydrate, L-Glutamine, L-Tyrosine, Per 10 g Protein Equivalent Nutrients Per 100 g (1 scoop/pouch) L-Lysine Acetate, L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Glycine, Calories 31240 L-Proline, L-Threonine, L-Isoleucine, Protein Equivalent, g 78 10 L-Histidine, L-Methionine, L-Tryptophan, Carbohydrate, g 0 0 L-Cystine, Silicon Dioxide, Taurine and Fat, g 0 0 L-Carnitine. Amino Acids, g L-Alanine 7.230.93 MTE Amino Acid Blend: L-Asparagine L-Arginine 6.13 0. 79 Monohydrate, L-Glutamine, L-Tyrosine, L-Asparagine 10.871.40 L-Lysine Acetate, L-Alanine, L-Leucine, L-Cystine 1.05 0. 14 L-Serine, L-Arginine, L-Valine, Glycine, L-Glutamine 12.111.55 L-Proline, L-Threonine, L-Isoleucine, Glycine 4.72 0. 61 Dicalcium Phosphate, L-Histidine, L-Histidine 1.96 0. 25 L-Methionine, L-Tryptophan, L-Cystine, L-Isoleucine 3.24 0. 42 Magnesium Phosphate (Dibasic), Silicon L-Leucine 6.98 0. 90 Dioxide, Taurine, L-Carnitine, Calcium L-Lysine 5.67 0. 73 Citrate, Chromium Chloride, Sodium L-Methionine 1.89 0. 24 Selenite and Sodium Molybdate. L-Phenylalanine Nil Added Nil Added L-Proline 4.72 0. 61 Note: Must combine with an appropriate L-Serine 6.98 0. 90 vitamin & mineral supplement when taken L-Threonine 3.59 0. 46 as the sole source of amino acid protein. L-Tryptophan 1.79 0. 23 L-Tyrosine 8.391.08 L-Valine 5.22 0. 67 L-Carnitine 0. 11 0.01 Taurine 0. 24 0.03 Minerals Calcium, mg 570 73 Chloride, mg Trace Trace Chromium, mcg 23 3 Magnesium, mg 123 15.8 Molybdenum, mcg 23 3 Phosphorus, mg 570 73 Sodium, mg Trace Trace Selenium, mcg 26 3.3 PhenylAde Amino Acid Blends Nutrition Information: Amino Acid Blend Unflavoured 53 PhenylAde Amino Acid Bars ™ A phenylalanine-free metabolic formula in bar format for the dietary management of phenylketonuria (PKU) in children, adults, including pregnant women and women of child-bearing age. Main Features: Indications: •Phenylalanine-free •Phenylketonuria • Available in chocolate, chocolate crispy, and white chocolate flavours (naturally and artificially flavoured) • PhenylAde Amino Acid Bar provides 10 g of protein equivalent per bar Metabolics • Suitable for individuals with PKU over 1 year of age 54 Ordering Information: Product Code Product Packaging Calories Per Bar 9570 White Chocolate 9580 Chocolate Crispy 9590 Chocolate 12 x 47 g (1.66 oz) 12 x 47 g (1.66 oz) 12 x 47 g (1.66 oz) 265 255 265 Chocolate, White Chocolate Chocolate Crispy Per 10 g Protein Nutrients Per 100 g Equivalent (1 bar) Calories 564265 Protein Equivalent, g 21 10 Carbohydrate, g 34 16 Sugars, g 33 15 Fat, g 38 18 Saturated Fat, g 33 15.5 Monounsaturated Fat, g 4.7 2.2 Polyunsaturated Fat, g 0.76 0.36 Trans Fat, g 0 0 Amino Acids, g L-Alanine 1.980.93 L-Arginine 1.680.79 L-Asparagine 2.971.40 L-Cystine 0.290.14 L-Glutamine 3.311.55 Glycine 1.290.61 L-Histidine 0. 54 0.25 L-Isoleucine 0. 89 0.42 L-Leucine 1.910.90 L-Lysine 1.550.73 L-Methionine 0. 52 0.24 L-Phenylalanine Nil Added Nil Added L-Proline 1.290.61 L-Serine 1.910.90 L-Threonine 0. 98 0.46 L-Tryptophan 0. 49 0.23 L-Tyrosine 2.291.08 L-Valine 1.420.67 L-Carnitine 0.030.01 Taurine 0.060.03 Per 10 g Protein Nutrients Per 100 g Equivalent (1 bar) Calories 541255 Protein Equivalent, g 21 10 Carbohydrate, g 37 17 Sugars, g 31 14 Fat, g 34 16 Saturated Fat, g 30 14 Monounsaturated Fat, g 3.7 1.7 Polyunsaturated Fat, g 0.67 0.31 Trans Fat, g 0 0 Amino Acids, g L-Alanine 2.00.94 L-Arginine 1.70 0. 80 L-Asparagine 2.971.40 Aspartic Acid 0.03 0.02 L-Cystine 0.290.14 Glutamic Acid 0.07 0.03 L-Glutamine 3.311.55 Glycine 1.310.61 L-Histidine 0. 55 0.26 L-Isoleucine 0. 90 0.42 L-Leucine 1.940.91 L-Lysine 1.550.73 L-Methionine 0.520.25 L-Phenylalanine0.02 0.01 L-Proline 1.310.61 L-Serine 1.930.91 L-Threonine 0.990.47 L-Tryptophan0.500.23 L-Tyrosine 2.311.08 L-Valine 1.450.68 L-Carnitine 0.030.01 Taurine 0.060.03 Chocolate Flavoured Ingredients: Sugar, Palm Kernel Oil, Amino Acids (L-Asparagine Monohydrate, L-Glutamine, L-Tyrosine, L-Lysine Acetate, L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Glycine, L-Proline, L-Threonine, L-Isoleucine, L-Histidine, L-Methionine, L-Tryptophan, L-Cystine), Palm Oil, Cocoa Butter, Natural and Artificial Flavour, Artificial Color (Red 40 Lake, Yellow 6 Lake, Blue 1 Lake), Soy Lecithin (Emulsifier), Taurine, L-Carnitine. White Chocolate Flavoured Ingredients: Sugar, Palm Kernel Oil, Amino Acids (L-Asparagine Monohydrate, L-Glutamine, L-Tyrosine, L-Lysine Acetate, L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Glycine, L-Proline, L-Threonine, L-Isoleucine, L-Histidine, L-Methionine, L-Tryptophan, L-Cystine), Palm Oil, Cocoa Butter, Natural and Artificial Flavour, Soy Lecithin (Emulsifier), Taurine, L-Carnitine. Chocolate Flavoured Crispy Ingredients: Sugar, Palm Kernel Oil, Amino Acids (L-Asparagine Monohydrate, L-Glutamine, L-Tyrosine, L-Lysine Acetate, L-Alanine, L-Leucine, L-Serine, L-Arginine, L-Valine, Glycine, L-Proline, L-Threonine, L-Isoleucine, L-Histidine, L-Methionine, L-Tryptophan, L-Cystine), Crisp Rice, Palm Oil, Cocoa Butter, Natural and Artificial Flavour, Artificial Color (Red 40 Lake, Yellow 6 Lake, Blue 1 Lake), Soy Lecithin (Emulsifier), Taurine, L-Carnitine. PhenylAde Amino Acid Bars Ingredients: Nutrition Information: Note: Must combine with an appropriate vitamin & mineral supplement when taken as the sole source of amino acid protein. *Crisp rice adds a small amount of natural protein, including PHE. 55 ™ A phenylalanine-free powdered formula containing the remaining essential amino acids (large neutral amino acids and lysine) for the dietary management of phenylketonuria (PKU) in individuals over 12 years of age. Main Features: Indications: •Phenylalanine-free •Phenylketonuria • Provides full compliment of essential amino acids (without phenylalanine) For details on administration and household measurements, please see pages 146-161. • Simplifies diet management Ordering Information: • Available in powder Product Code POUCHES 95504 Metabolics • Suitable for individuals with PKU over 12 years of age 56 Product Packaging Calories 110 x 3 g (0.11 oz) 1100/case Nutrition Information: Ingredients: Per Pouch Per 2 Pouches Nutrients (3g Powder) (6g Powder) Calories 1020 Protein Equivalent, g 2.2 4.4 Carbohydrate, g 0.34 0.68 Fat, g 0 0 Minerals Calcium, mg 0 0 Phosphorus, mg 0 0 Sodium, mg trace trace Chloride, mg 28 56 Amino Acids, g L-Arginine 0.170.34 L-Histidine 0.160.31 L-Isoleucine 0.160.32 L-Leucine 0.150.31 L-Lysine 0.120.23 L-Methionine 0.250.50 L-Phenylalanine Nil Added Nil Added L-Threonine 0.160.33 L-Tryptophan 0.310.61 L-Tyrosine 0.981.97 L-Valine 0.160.32 Powder Ingredients: L-Tyrosine, Maltodextrin, L-Tryptophan, L-Methionine, L-Arginine, L-Threonine, L-Valine, L-Isoleucine, L-Histidine, L-Leucine and L-Lysine Monohydrochloride PhenylAde PheBLOC LNAA PhenylAde PheBLOC LNAA ™ Precautions: • Not for use when planning or during pregnancy •Seek medical advice before using with serotonergic medications 57 XPhe Maxamaid® Metabolics A phenylalanine-free powdered formula for the dietary management of phenylketonuria (PKU) in toddlers and young children. 58 Main Features: Indications: •Phenylalanine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XPhe Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in unflavoured, orange and strawberry flavours • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161 Ordering Information: Product Code 117792 - Orange 117793 - Unflavoured Product Packaging 6 x 454 g (1 lb) 6 x 454 g (1 lb) Calories Per Can 1471 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine1.03 0.41 L-Arginine2.21 0.88 L-Aspartic Acid 1.85 0.74 L-Cystine0.71 0.28 Glycine1.77 0.71 L-Histidine1.27 0.51 L-Isoleucine1.70 0.68 L-Leucine2.91 1.16 L-Lysine2.22 0.89 L-Methionine0.48 0.19 L-Phenylalanine Nil Added Nil Added L-Proline2.05 0.82 L-Serine1.26 0.50 L-Threonine1.42 0.57 L-Tryptophan0.57 0.23 L-Tyrosine2.56 1.02 L-Valine1.85 0.74 L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1665 (500) 6 66 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) (10) 232 Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.1) Ingredients: Corn Syrup Solids, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, L-Lysine Acetate, L-Leucine, L-Tyrosine, Tripotassium Citrate, L-Proline, and 2% or less of each of the following: L-Valine, Glycine, L-Isoleucine, L-Glutamine, L-Threonine, L-Serine, L-Histidine, Maltodextrin, L-Alanine, Disodium Hydrogen Phosphate, Sodium Chloride, Magnesium Acetate, L-Cystine, Choline Bitartrate, N-Acetyl L-Methionine, L-Tryptophan, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XPhe Maxamaid Nutrition Information: Unflavoured version also contains: 2% or less of Sugar. Orange flavoured version also contains: Sugar, Citric Acid, and 2% or less of each of the following: Artificial Flavours, Artificial Colors (Beta Carotene, Beet Red). Please see individual product label for exact order of ingredients. 59 Metabolics A phenylalanine-free powdered formula for the dietary management of phenylketonuria (PKU) in older children and adults, including pregnant women and women of childbearing age. 60 Main Features: Indications: •Phenylalanine-free • Easy transition from XPhe Maxamaid • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XPhe Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in unflavoured and orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Available in cans or or single serve sachets • Displacement: 0.60 mL/g •Phenylketonuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118324 - Orange (cans) 118323 - Unflavoured (cans) 12312 - Orange (sachets) 12311 - Unflavoured (sachets) Product Packaging 6 x 454 g (1 lb) 6 x 454 g (1 lb) 30 x 50 g (1.8 oz) 30 x 50 g (1.8 oz) Calories Per Can/Sachet 1385 1385 153 153 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 305 76 Protein Equivalent, g 40 10 Fat, g <1 <0.25 Carbohydrate, g 34 8.5 Amino Acids, g L-Alanine1.6 0.40 L-Arginine3 0.75 L-Aspartic Acid 2.8 0.70 L-Cystine1.1 0.28 Glycine2.8 0.70 L-Histidine1.7 0.43 L-Isoleucine2.7 0.68 L-Leucine4.6 1.15 L-Lysine3.5 0.88 L-Methionine0.73 0.18 L-Phenylalanine Nil Added Nil Added L-Proline3.2 0.80 L-Serine2 0.50 L-Threonine2.2 0.55 L-Tryptophan0.89 0.22 L-Tyrosine4 1.00 L-Valine2.9 0.73 L-Carnitine0.039 0.01 Taurine0.14 0.04 L-Glutamine4.9 1.23 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 2228 (669) 5 57 (167) Vitamin D, IU (mcg) 332 (8.3) 83 (2.1) Vitamin E, IU (mg α T.E.) 18.3 (12.3) 4.6 (3.1) Vitamin K, mcg 82 21 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 Vitamin B6, mg 0.4 3.1 Vitamin B12, mcg 0.8 Niacin, mg 5.7 1.4 Folic Acid, mcg 491 123 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 Vitamin C, mg 62 16 Choline, mg 430 108 Inositol, mg 80 20 Minerals Calcium, mg 1183 296 Phosphorus, mg 1137 284 Magnesium, mg 306 77 Iron, mg 14.7 3.7 Zinc, mg 9 2 Manganese, mg 1.8 0.5 Copper, mcg 820 205 Iodine, mcg 131 33 Molybdenum, mcg 37 9 Chromium, mcg 26 7 Selenium, mcg 58 15 Sodium, mg (mEq) 560 (24.3) 140 (6.1) Potassium, mg (mEq) 700 (17.9) 175 (4.5) Chloride, mg (mEq) 560 (16) 140 (4) Ingredients: Sugar, L-Arginine L-Aspartate, L-Lysine Acetate, L-Glutamine, L-Leucine, L-Tyrosine, Calcium Glycerophosphate, L-Proline, L-Valine, Glycine, L-Isoleucine, L-Threonine, Tripotassium Citrate, Magnesium Hydrogen Phosphate, and 2% or less of each of the following: L-Serine, L-Histidine, L-Alanine, Calcium Phosphate Dibasic, Choline Bitartrate, L-Cystine, Tricalcium Phosphate, Sodium Chloride, N-Acetyl L-Methionine, Trisodium Citrate, L-Tryptophan, Soy Lecithin, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XPhe Maxamum Nutrition Information: XPhe Maxamum® Orange flavoured version also contains: Citric Acid, and 2% or less of each of the following: Artificial Flavour, Artificial Sweetener: Acesulfame Potassium, Artificial Colors (Beta Carotene, Beet Red). Please see individual product label for exact order of ingredients. 61 Metabolics A phenylalanine-free*, ready-to-drink formula containing amino acids, vitamins and minerals, based on fruit juice (from concentrate) with natural flavour; for the dietary management of proven phenylketonuria (PKU) in individuals 4 years and older, including pregnant women and women of child-bearing age. 62 Main Features: Indications: •Phenylalanine-free • Low volume; provides 20 g PE in just 125 mL (4.2 fl oz) • Convenient ready-to-drink • Made with real fruit juice from concentrate • Contains a balanced mixture of other essential and non-essential amino acids, carbohydrates, vitamins and minerals • Contains 150 mg of DHA per pouch • Available in juicy tropical, mixed berry blast and juicy orange flavours • Osmolality: 2460 mOsm/kg •Phenylketonuria For details on administration, please see pages 146-161. Ordering Information: Product Code 86051 Juicy Orange 86021 Mixed Berry Blast 86055 Juicy Tropical *May contain traces of phenylalanine (PHE) from fruit juice (from concentrate). Product Packaging 30 x 4.2 fl oz (125 mL) 30 x 4.2 fl oz (125 mL) 30 x 4.2 fl oz (125 mL) Calories Per Pouch 120 120 120 Per Pouch Per 10 g Nutrients (125 mL) Protein Equivalent Calories 12060 Protein Equivalent, g 20 10 Fat, g 0.44 0.2 DHA, mg 150 75 Carbohydrate, g 9.3 4.7 Of which Fiber, g 0.5 0.25 Amino Acids, g L-Alanine 1.160.58 L-Arginine 21 L-Aspartic Acid 1.75 0.88 L-Cystine 0.510.26 Glycine 1.880.94 L-Histidine 0.790.40 L-Isoleucine 1.240.62 L-Leucine 2.131.1 L-Lysine 1.630.82 L-Methionine 0.340.17 L-Phenylalanine tracetrace L-Proline 21 L-Serine 1.090.55 L-Threonine 1.040.52 L-Tryptophan 0.410.21 L-Tyrosine 1.880.94 L-Valine 1.380.69 L-Carnitine 0.010.01 Taurine 0.10.05 Ingredients: Per Pouch Per 10 g Vitamins (125 mL) Protein Equivalent Vitamin A, IU (mcg RE) 949.(285)475.(143) Vitamin D, IU (mcg) 320.(8)160.(4) 4.8 (3.2) 2.4 (1.6) Vitamin E, IU (mg α TE) Vitamin K, mcg 24.9 12.5 Thiamin, mg 0.54 0.27 Riboflavin, mg 0.5 0.25 Vit. B6, mg 0.58 0.29 Vit. B12, mcg 1.8 0.90 Niacin, mg 7.1 3.6 Folic Acid, mg 120 60 Pantothenic Acid, mg 1.8 0.9 Biotin, mcg 53.4 26.7 Vitamin C, mg 17.8 8.9 Choline, mg 153 76.5 Inositol, mg 40.6 20.3 Minerals Calcium, mg 319 160 Phosphorus, mg 244 122 Magnesium, mg 96.3 48.2 Iron, mg 5.1 2.6 Zinc, mg 3.8 1.9 Manganese, mcg 0.56 0.28 Copper, mcg 563 282 Iodine, mcg 56.3 28.2 Molybdenum, mcg 25 12.5 Chromium, mcg 10.8 5.4 Selenium, mcg 26.8 13.4 Sodium, mg <25 (<10) <12.5 (<5) Potassium, mg 90 (2.3) 45 (1.2) Chloride, mg <25 (<10) <12.5 (<5) Water, and less than 2% of each of the following: L-Leucine, Citric Acid, L-Proline, L-Arginine, Glycine, L-Tyrosine, L-Lysine Acetate, L-Valine, L-Aspartic Acid, L-Isoleucine, Dicalcium Phosphate, L-Alanine, L-Serine, L-Threonine, L-Histidine, L-Lysine, L-Aspartate, Maltodextrin, Magnesium Acetate, L-Cystine, Choline Bitartrate, L-Tryptophan, Sugar, C. Cohnii Oil**, N-Acetyl L-Methionine, Microcrystalline Cellulose, L-Ascorbic Acid, Taurine, L-Methionine, Guar Gum, Sunflower Lecithin, Xanthan Gum, M-Inositol, Potassium Sorbate (preservative to delay spoilage), Ferrous Lactate, Cellulose Gum, Artificial Sweetener: Acesulfame Potassium, L-Carnitine, Sodium Benzoate (preservative to delay spoilage), Zinc Sulfate, Niacinamide, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Riboflavin, Folic Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. **A Source Of Docosahexaenoic Acid (DHA) Juicy Orange flavoured version also contains: Orange Juice from Concentrate (45.5%), Corn Syrup Solids, and less than 2% of the following: Natural Flavour, Artificial Sweetener: Sucralose. Mixed Berry Blast flavoured version also contains: Apple Juice from Concentrate (34.1%), Grape Juice from Concentrate (6.9%), Blackcurrant Juice from Concentrate (2.5%), and less than 2% of the following: Elderberry Juice from Concentrate (0.6%), Natural Flavour, Concentrate (Apple, Blackcurrant, Radish), Artificial Sweetener: Sucralose. Juicy Tropical flavoured version also contains: Orange Juice from Concentrate (18%), Mango Puree from Concentrate (6.4%), Mandarin Juice from Concentrate (4.0%), Corn Syrup Solids, and less than 2% of the following: Artificial Flavour. Juicy Orange contains 45.5% juice. Mixed Berry Blast contains 44.1% juice. Juicy Tropical contains 28.4% juice. Please see individual product label for exact order of ingredients. PKU Lophlex LQ Nutrition Information: PKU Lophlex® LQ 63 Metabolics A low volume, phenylalanine-free, powdered formula for the dietary management of phenylketonuria (PKU) in older children and adults, including pregnant women and women of child-bearing age. 64 Main Features: Indications: •Phenylalanine-free • Low volume and low calorie • Contains vitamins, minerals, and trace elements • Age-appropriate DRI formulation • Lophlex provides 10 g of protein equivalent per single serve sachet • Available in berry and orange flavours • Osmolality (mOsm/kg): Dilution OrangeBerry 1 to 5 1390 1340 • Displacement: 0.64 mL/g •Phenylketonuria For details on administration, please see pages 146-161. Ordering Information: Product Code 12169 - Berry Product Packaging 30 x 14.3 g (0.5 oz) Calories Per Sachet 41 12167 - Orange 30 x 14.3 g (0.5 oz) 41 Nutrition Information: Ingredients: Nutrients Per sachet (14.3 g) Per 100 g Vitamins Per sachet (14.3 g) Per 100 g Calories 41286 Vitamin A, IU (mcg R.E.) 557 (167) 3896 (1170) Protein Equivalent, g 10 70 Vitamin D, IU (mcg) 82.9 (2.1) 580 (14.5) Fat, g 0.03 0.2 32 (21.5) Vitamin E, IU (mg α T.E.) 4.6 (3.1) Carbohydrate, g 0.14 1 Vitamin K, mcg 20.4 143 Amino Acids, g Thiamin, mg 0.23 1.6 L-Alanine 0.473.3 Riboflavin, mg 0.24 1.7 L-Arginine 0.835.8 0.4 2.8 Vitamin B6, mg L-Aspartic Acid 0.77 5.4 0.79 5.5 Vitamin B12, mcg L-Cystine 0.312.2 Niacin, mg 1.4 10 Glycine 0.735.1 Folic Acid, mcg 123 860 L-Histidine 0.473.3 Pantothenic Acid, mg 1.2 8.6 L-Isoleucine 0.735.1 Biotin, mcg 6.1 43 L-Leucine 1.248.7 Vitamin C, mg 15.7 110 L-Lysine 0.845.9 Choline, mg 103 720 L-Methionine 0.201.4 Inositol, mg 20 140 L-Phenylalanine Nil Added Nil Added Minerals L-Proline 0.896.2 Calcium, mg 296 2070 L-Serine 0.543.8 Phosphorus, mg 285 1990 L-Threonine 0.614.3 Magnesium, mg 76.5 535 L-Tryptophan 0.241.7 Iron, mg 3.7 25.7 L-Tyrosine 1.127.8 Zinc, mg 2.3 15.8 L-Valine 0.805.6 Manganese, mg 0.44 3.1 L-Carnitine 0.010.06 Copper, mcg 204 1430 Taurine 0.020.11 Iodine, mcg 32.7 229 L-Glutamine 0.563.95 Molybdenum, mcg 9.3 65 Chromium, mcg 6.6 46 Selenium, mcg 14.4 101 Sodium, mg (mEq) <3 (<1) <20 (<1) Potassium, mg (mEq) <6 (<1) <40 (<1) Chloride, mg (mEq) <1 (<1) <1 (<1) Berry: L-Leucine, L-Tyrosine, L-Proline, L-Lysine, L-Arginine, L-Valine, Tricalcium Phosphate, L-Aspartic Acid, Glycine, L-Isoleucine, L-Threonine, Magnesium Hydrogen Phosphate, L-Glutamine, L-Serine, L-Histidine, L-Alanine, Citric Acid, L-Cystine, Choline Bitartrate, and 2% or less of each of the following: L-Tryptophan, Calcium Phosphate, L-Methionine, Artificial Flavour, Guar Gum, Soy Lecithin, L-Ascorbic Acid, M-Inositol, Acesulfame Potassium, Taurine, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium-DPantothenate, Copper Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Color (Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. Lophlex Powder Lophlex® Powder Orange flavoured version also contains: 2% or less of Artificial Color (Beta Carotene). Please see individual product label for exact order of ingredients. 65 Metabolics A phenylalanine-free powdered formula for the dietary management of phenylketonuria (PKU) in individuals over 1 year of age, including pregnant women and women of child-bearing age. 66 Main Features: Indications: •Phenylalanine-free • Available as black currant/apple and tropical surprise flavour • Each unit (one drink mix sachet) provides 10 g of amino acids, equivalent to 8.33 g of protein • Osmolality (mOsm/kg): Dilution Blackcurrant/Tropical Apple Surprise 1 to 5 1172 1140 •Phenylketonuria For details on administration, please see pages 146-161. Ordering Information: Product Code 11467 - Drink Mix (Blackcurrant/Apple) 11910 - Drink Mix (Tropical Surprise) Product Packaging 30 x 20 g (0.7 oz) 30 x 20 g (0.7 oz) Calories 69/sachet 69/sachet Nutrition Information: Ingredients: Phlexy-10 Drink Mix (blackcurrant/ apple): Sucrose, L-Lysine Aspartate, L-Leucine, L-Tyrosine, Artificial Flavours, L-Proline, L-Arginine, L-Valine, L-Isoleucine, Glycine, Malic Acid, L-Threonine, L-Glutamine, Corn Syrup Solids, L-Serine, L-Histidine, L-Alanine, L-Cystine, N-Acetyl L-Methionine, L-Tryptophan, Soy Lecithin, Taurine, L-Carnitine, Artificial Sweetener: Acesulfame Potassium, Artificial Color. Phlexy-10 Drink Mix Nutrients (Per 20 g sachet) Calories 69 Protein Equivalent, g 8.33 Fat, g <1 g Carbohydrate, g 8.8 Dietary Fiber, g Nil Added Amino Acids, g L-Alanine 0.41 L-Arginine0.72 L-Aspartic Acid 0.68 L-Cystine0.27 Glycine0.64 L-Histidine0.41 L-Isoleucine0.64 L-Leucine1.09 L-Lysine0.74 L-Methionine0.17 L-Phenylalanine Nil Added L-Proline0.77 L-Serine0.47 L-Threonine0.54 L-Tryptophan0.22 L-Tyrosine 0.97 L-Valine0.7 L-Carnitine 0.007 Taurine0.014 L-Glutamine0.5 Phlexy-10 Drink Mix (tropical surprise): Sucrose, L-Lysine Aspartate, Artificial Flavours, L-Leucine, L-Tyrosine, L-Proline, L-Arginine, L-Valine, Citric Acid, Glycine, L-Isoleucine, L-Threonine, L-Glutamine, Corn Syrup Solids, L-Serine, L-Histidine, L-Alanine, L-Cystine, N-Acetyl L-Methionine, L-Tryptophan, Soy Lecithin, Artificial Sweetener: Acesulfame Potassium, Taurine, L-Carnitine, Artificial Color. Phlexy-10 Drink Mix Phlexy-10® Drink Mix Please see individual product label for exact order of ingredients. 67 Metabolics A phenylalanine-free powdered formula containing the remaining essential amino acids (large neutral amino acids and lysine) for the dietary management of phenylketonuria (PKU) in individuals over 12 years of age. 68 Main Features: Precautions: •Phenylalanine-free • Contains lysine and other large neutral amino acids • Contains carbohydrate, vitamins, minerals and trace elements • One sachet of Lanaflex provides 6 g of amino acids equivalent to 5.2 g of protein • Available in orange flavour • Osmolality (at a 1 to 4 dilution): 1350 mOsm/kg • Not for use when planning or during pregnancy • Seek medical advice before using with serotonergic medications Indications: •Phenylketonuria For details on administration, please see pages 146-161. Ordering Information: Product Code 12643 Product Packaging 40 x 15.8 g (0.6 oz) Calories Per Sachet 40 Per Sachet Nutrients (15.8 g) Per 100 g Calories 40253 Protein Equivalent, g 5.2 33 Fat, g 0.16 1 Carbohydrate g 4.4 28 Amino Acids, g L-Histidine 0.925.85 L-Isoleucine 0.462.92 L-Leucine 0.462.92 L-Lysine 0.462.92 L-Methionine 0.925.85 L-Threonine 0.462.92 L-Tryptophan 0.925.85 L-Tyrosine 0.925.85 L-Valine 0.462.92 Vitamins Vitamin A IU, (mcg R.E.) 892.(268)5644.(1695) Vitamin D IU, (mcg R.E.) 135.(3.4) 852 (21.3) 46.9 (31.5) Vitamin E IU, (mg α T.E.) 7.4 (5) Vitamin K, mcg 32.7 207 Thiamin, mg 0.36 2.3 Riboflavin, mg 0.38 2.4 0.65 4.1 Vitamin B6, mg 1.3 8 Vitamin B12, mcg Niacin, mg 2.2 14.2 Folic Acid, mcg 197 1246 Pantothenic Acid, mg 1.9 12.2 Biotin, mcg 9.8 61.9 Vitamin C, mg 25.1 159 Choline, mg 165 1045 Inositol, mg 32.1 203 Ingredients: Per Sachet Minerals (15.8 g) Per 100 g Calcium, mg 474 2998 Phosphorus, mg 456 2888 Magnesium, mg 122 775 Iron, mg 5.9 37.6 Zinc, mg 3.7 23.2 Manganese, mg 0.73 4.6 Copper, mcg 332 2100 Iodine, mcg 52.3 331 Molybdenum, mcg 14.9 94.2 Chromium, mcg 10.6 66.9 Selenium, mcg 23.1 146 Sodium, mg (mEq) 4.9 (0.21) 31.(1.3) Potassium, mg (mEq) 3.5 (0.09) 22.(0.56) Chloride, mg (mEq) 0.25 (0.008) 1.6 (0.05) Sugar, Calcium Phosphate, Artificial Flavours, L-Histidine, L-Tryptophan, L-Tyrosine, Tricalcium Phosphate, Magnesium Acetate, L-Lysine Acetate, N-Acetyl-L-Methionine, L-Leucine, L-Methionine, L-Threonine, L-Valine, L-Isoleucine, Choline Bitartrate, Guar Gum, Soy Lecithin, Citric Acid, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, Artificial Sweetener (Acesulfame Potassium), DL-Alpha-Tocopheryl Acetate, Zinc Sulfate, Nicotinamide, Manganese Sulfate, CalciumD-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Color (Beta Carotene), Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Cholecalciferol, Cyanocobalamin. Lanaflex Nutrition Information: Lanaflex® 69 MSUD Analog Metabolics An isoleucine-, leucine- and valine-free powdered infant formula for the dietary management of maple syrup urine disease (MSUD). 70 Main Features: Indications: • Isoleucine-, leucine- and valine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • MSUD Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Maple syrup urine disease (MSUD) For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Per Can Calories Per Can 118302 6 x 400 g (14 oz) 1900 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 475 365 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 5.2 6.8 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 Linoleic Acid, mg 3025 2330 Carbohydrate, g 59 45 Amino Acids, g L-Alanine0.76 0.58 L-Arginine1.34 1.03 L-Aspartic Acid0.85 1.11 L-Cystine0.49 0.38 L-Glutamic Acid 1.49 1.15 Glycine1.19 0.92 L-Histidine0.76 0.58 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine1.38 1.06 L-Methionine0.32 0.25 L-Phenylalanine0.90 0.69 L-Proline1.44 1.11 L-Serine0.89 0.68 L-Threonine1.00 0.77 L-Tryptophan0.40 0.31 L-Tyrosine0.90 0.69 L-Valine Nil Added Nil Added L-Carnitine0.01 0.01 Taurine0.02 0.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1760 (528) 1355 (406) Vitamin D, IU (mcg) 340 (8.5) 262 (6.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 3.8 (2.5) Vitamin K, mcg 21 16 Thiamin, mcg 500 385 Riboflavin, mcg 600 462 520 Vitamin B6, mcg 400 1.25 0.96 Vitamin B12, mcg Niacin, mcg 4500 3462 Folic Acid, mcg 38 29 Pantothenic Acid, mcg 2600 2000 Biotin, mcg 26 20 Vitamin C, mg 40 31 Choline, mg 50 38 Inositol, mg 100 77 Minerals Calcium, mg 600 462 Phosphorus, mg 500 385 Magnesium, mg 40 31 Iron, mg 10 8 Zinc, mg 8 6 Manganese, mcg 600 462 Copper, mcg 450 346 Iodine, mcg 47 36 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 12 Sodium, mg (mEq) 120 (5.2) 92 (4.0) Potassium, mg (mEq) 420 (10.8) 323 (8.3) Chloride, mg (mEq) 290 (8.2) 223 (6.3) Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, Calcium Phosphate Dibasic, L-Proline, L-Arginine, Glycine, L-Aspartic Acid, L-Threonine, L-Phenylalanine, L-Tyrosine, Galactose, L-Serine, Tripotassium Citrate, L-Histidine, L-Alanine, Calcium Phosphate Monobasic, Mono and Diglycerides, L-Cystine, L-Tryptophan, L-Methionine, Sodium Chloride, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, L-Glutamic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. MSUD Analog Nutrition Information: ™ 71 MSUD Maxamaid Metabolics An isoleucine-, leucine- and valine-free powdered formula for the dietary management of maple syrup urine disease (MSUD) in toddlers and young children. 72 Main Features: Indications: • Isoleucine-, leucine- and valine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • MSUD Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Maple syrup urine disease (MSUD) For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Per Can Calories Per Can 117781 6 x 454 g (1 lb) 1471 Per 10 g Nutrients Per 100 g Protein Equivalent 130 Calories 324 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 22 Carbohydrate, g 56 Amino Acids, g 0.59 L-Alanine1.48 1.04 L-Arginine2.60 L-Aspartic Acid 2.17 0.87 0.38 L-Cystine0.96 0.92 Glycine2.31 0.60 L-Histidine1.49 Nil Added L-Isoleucine Nil Added Nil Added L-Leucine Nil Added 1.08 L-Lysine2.69 0.25 L-Methionine0.63 0.70 L-Phenylalanine1.75 1.12 L-Proline2.81 0.69 L-Serine1.73 0.78 L-Threonine1.94 0.31 L-Tryptophan0.77 0.70 L-Tyrosine1.75 Nil Added L-Valine Nil Added 0.01 L-Carnitine0.02 0.06 Taurine0.14 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1665 (500) 666 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) 232 (10) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Ingredients: Sugar, Corn Syrup Solids, L-Arginine L-Aspartate, L-Lysine Acetate, Calcium Phosphate Dibasic, Citric Acid, L-Proline, Tripotassium Citrate, Glycine, L-Threonine, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Serine, Artificial Flavours, L-Histidine, L-Alanine, Maltodextrin, Disodium Hydrogen Phosphate, L-Cystine, Sodium Chloride, N-Acetyl L-Methionine, L-Tryptophan, Magnesium Acetate, Choline Bitartrate, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. MSUD Maxamaid Nutrition Information: ® 73 Metabolics An isoleucine-, leucine- and valine-free powdered formula for the dietary management of maple syrup urine disease (MSUD) in older children and adults, including pregnant women and women of child-bearing age. 74 Main Features: Indications: • Isoleucine-, leucine- and valine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • MSUD Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Maple syrup urine disease (MSUD) For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Per Can Calories Per Can 117789 6 x 454 g (1 lb) 1385 Per 10 g Nutrients Per 100 g Protein Equivalent 76 Calories 305 Protein Equivalent, g 40 10 Fat, g <1 <0.25 8.5 Carbohydrate, g 34 Amino Acids, g 0.60 L-Alanine2.4 1.03 L-Arginine4.1 L-Aspartic Acid 3.4 0.85 0.40 L-Cystine1.6 L-Glutamic Acid 4.6 1.15 0.93 Glycine3.7 0.58 L-Histidine2.3 Nil Added L-Isoleucine Nil Added Nil Added L-Leucine Nil Added 1.05 L-Lysine4.2 0.25 L-Methionine0.99 0.70 L-Phenylalanine2.8 1.13 L-Proline4.5 0.70 L-Serine2.8 0.78 L-Threonine3.1 0.33 L-Tryptophan1.3 0.70 L-Tyrosine2.8 Nil Added L-Valine Nil Added 0.01 L-Carnitine0.039 0.04 Taurine0.14 0.08 L-Glutamine0.32 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 2228 (669) 557 (167) Vitamin D, IU (mcg) 332 (8.3) 83 (2.1) Vitamin E, IU (mg α T.E.) 18.3 (12.3) 4.6 (3.1) Vitamin K, mcg 82 21 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 0.4 Vitamin B6, mg 3.1 0.8 Vitamin B12, mcg Niacin, mg 5.7 1.4 Folic Acid, mcg 491 123 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 Vitamin C, mg 62 16 Choline, mg 430 108 Inositol, mg 80 20 Minerals Calcium, mg 1183 296 Phosphorus, mg 1137 284 Magnesium, mg 306 77 Iron, mg 14.7 3.7 Zinc, mg 9 2 Manganese, mg 1.8 0.5 Copper, mcg 820 205 Iodine, mcg 131 33 Molybdenum, mcg 37 9 Chromium, mcg 26 7 Selenium, mcg 58 15 Sodium, mg (mEq) 560 (24.3) 140 (6.1) Potassium, mg (mEq) 700 (17.9) 175 (4.5) Chloride, mg (mEq) 560 (16) 140 (4) Ingredients: Sugar, L-Lysine L-Glutamate, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Proline, L-Arginine, Glycine, L-Aspartic Acid, L-Threonine, L-Phenylalanine, L-Tyrosine, L-Serine, Artificial Flavour, L-Histidine, L-Alanine, Citric Acid, Magnesium Acetate, L-Cystine, L-Tryptophan, Tripotassium Citrate, Choline Bitartrate, L-Methionine, Sodium Chloride, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, L-Glutamic Acid, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. MSUD Maxamum Nutrition Information: MSUD Maxamum® 75 Metabolics An isoleucine-, leucine- and valine-free* ready-to-drink formula containing amino acids, carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) with natural flavour; for the dietary management of proven maple syrup urine disease (MSUD) in individuals 4 years and older, including pregnant women and women of child-bearing age. 76 Main Features: Indications: • Isoleucine-, leucine- and valine-free • Low volume; provides 20 g PE in just 125 mL (4.2 fl oz) • Convenient ready-to-drink • Based on fruit juices (from concentrate) with natural flavour - no artificial flavours • Contains a balanced mixture of other essential and non-essential amino acids, carbohydrates, vitamins, minerals and DHA • Contains 150 mg of DHA per pouch • Available in mixed berry blast flavour • Osmolality: 2460 mOsm/kg • Maple syrup urine disease (MSUD) For details on administration, please see page 146-161. Ordering Information: Product Code 82112 Product Packaging 30 X 4.2 fl oz (125 mL) *May contain traces of leucine, isoleucine and valine from fruit juice (from concentrate). Calories Per Pouch 120 Per Pouch Per 10 g Per Pouch Per 10 g Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Calories 120.060.0 Vitamin A, IU (mcg R.E.) 949 (285) 475 (143) Protein Equivalent, g 20.0 10.0 Vitamin D, IU (mcg) 320 (8.0) 160 (4.0) Fat, g 0.44 0.22 Vitamin E, IU (mg α T.E.) 4.8 (3.2) 2.4 (1.6) DHA, mg 150 75.0 Vitamin K, mcg 24.9 12.5 Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 Amino Acids, g 0.58 0.29 Vitamin B6, mg L-Alanine 1.400.70 1.8 0.90 Vitamin B12, mcg L-Arginine 1.900.95 Niacin, mg 7.1 3.6 L-Aspartic Acid 1.45 0.73 Folic Acid, mcg 120 60.0 L-Cystine 1.200.60 Pantothenic Acid, mg 1.8 0.9 Glycine 1.900.95 Biotin, mcg 53.4 26.7 L-Histidine 1.000.50 Vitamin C, mg 17.8 8.9 L-Isoleucine TraceTrace Choline, mg 153 76.5 L-Leucine TraceTrace Inositol, mg 40.6 20.3 L-Lysine 1.780.89 Minerals L-Methionine 0.430.22 Calcium, mg 319 160 L-Phenylalanine1.18 0.59 Phosphorus, mg 244 122 L-Proline 2.381.19 Magnesium, mg 96.3 48.2 L-Serine 1.650.83 Iron, mg 5.1 2.6 L-Threonine 1.300.65 Zinc, mg 3.8 1.9 L-Tryptophan 0.530.27 Manganese, mg 0.56 0.28 L-Tyrosine 2.001.00 Copper, mcg 563 282 L-Valine TraceTrace Iodine, mcg 56.3 28.2 L-Carnitine 0.010.01 Molybdenum, mcg 25.0 12.5 Taurine 0.060.03 Chromium, mcg 10.8 5.4 Selenium, mcg 26.8 13.4 Sodium, mg (mmol) <25.0 (<10) <12.5 (<5) Potassium, mg (mmol) 90 (2.3) 45 (1.2) Chloride, mg (mmol) <25.0 (<10) <12.5 (<5) Ingredients: Water, Apple Juice from Concentrate (34.1%), Grape Juice from Concentrate (6.9%), Blackcurrant Juice from Concentrate (2.5%), L-Lysine Acetate, L-Proline, Citric Acid, L-Tyrosine, L-Arginine, Glycine, L-Serine, L-Aspartic Acid, L-Alanine, L-Threonine, Corn Syrup Solids, L-Cystine, L-Phenylalanine, Dicalcium Phosphate, L-Histidine, Elderberry Juice from Concentrate (0.6%), Maltodextrin, Magnesium Acetate, N-Acetyl L-Methionine, L-Tryptophan, Choline Bitartrate, C. Cohnii Oil*, Sugar, Microcrystalline Cellulose, Natural Flavour, Fruit Concentrate (Apple, Blackcurrant, Radish), L-Ascorbic Acid, Taurine, Guar Gum, Sunflower Lecithin, Xanthan Gum, M-Inositol, Potassium Sorbate (preservative to delay spoilage), Artificial Sweetener: Sucralose, Ferrous Lactate, Artificial Sweetener: Acesulfame Potassium, Sodium Benzoate (preservative to delay spoilage), Zinc Sulfate, L-Carnitine, Niacinamide, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Riboflavin, Folic Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. MSUD Lophlex LQ Nutrition Information: MSUD Lophlex® LQ *A Source of Docosahexaenoic Acid (DHA). Contains 44.1% juice. 77 Complex Junior MSD Drink Mix An isoleucine-, leucine-, and valine-free powdered formula for the dietary management of maple syrup urine disease (MSUD) in young children. Main Features: Indications: • Free from isoleucine, leucine and valine • Maple syrup urine disease (MSUD) or Beta-ketothiolase deficiency • 13 g of protein equivalent per 100 g of powder For details on administration and household measurements, please see pages 146-161. • DHA & ARA • Mild neutral flavour • Essential vitamins and minerals to help meet needs of young children with MSUD Metabolics • Displacement: 0.70 mL/g 78 Ordering Information: Product Code 5910 Product Packaging 4 x 400 g (14.1 oz) Calories Per Can 1976 Per 100 g Per 100 kcal NutrientsPowder Calories 494100 Protein Equivalent, g 13 2.6 Carbohydrate, g 46 9 Fat, g 29 6 Saturated Fat, g 8.3 1.7 Monounsaturated Fat, g 14.7 3 Polyunsaturated Fat, g 5.1 1 Linoleic Acid, mg 4296 870 DHA, mg 88 17.9 ARA, mg 88 17.9 Amino Acids, g L-Alanine 1.400.28 L-Arginine 0.660.13 L-Asparagine 0.750.15 L-Cystine 0.290.06 L-Glutamic Acid 0.45 0.09 L-Glutamine 3.710.75 Glycine 0.350.07 L-Histidine 0.920.19 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine 1.170.24 L-Methionine 0.380.08 L-Phenylalanine 1.140.23 L-Proline 0.760.16 L-Serine 0.580.12 L-Threonine 0.940.19 L-Tryptophan 0.690.14 L-Tyrosine 1.140.23 L-Valine Nil Added Nil Added L-Carnitine 0.030.01 Taurine 0.070.01 Ingredients: Per 100 g Per 100 Corn Syrup Solids, Maltodextrin, Modified kcal VitaminsPowder Corn Starch, Canola Oil, Safflower Oil, Vitamin A, IU (mcg R.E.) 1187 (356) 240 (72) Coconut Oil, L-Glutamine, Soybean Oil, (25% as beta-carotene) Tricalcium Phosphate, L-Lysine Acetate, Vitamin D, IU (mcg) 429 (10.7) 87 (2.2) L-Alanine, L-Phenylalanine, L-Tyrosine, Vitamin E, IU (mg α T.E.) 13.8 (9.2) 2.8 (1.9) Sodium Citrate, Dipotassium Phosphate, Vitamin K, mcg 62 12.6 L-Threonine, L-Histidine, L-Asparagine Thiamin, mg 1.1 0.22 Monohydrate, L-Proline, L-Tryptophan, Riboflavin, mg 0.81 0.16 Choline Bitartrate, L-Arginine, Ascorbyl Vitamin B6, mg 0.78 0.16 Palmitate, Mixed Tocopherols, Magnesium 2 0.4 Vitamin B12, mcg Chloride, Rosemary Extract, L-Serine, Niacin, mg 5.8 1.2 Potassium Citrate, Potassium Chloride, Folic Acid, mcg 140 28 L-Glutamic Acid, L-Methionine, Glycine, Pantothenic Acid, mg 3.4 0.69 Silicon Dioxide, L-Cystine, C. Cohnii Biotin, mcg 36 7.2 Oil*, Glucose Syrup Solids, Mono- and Vitamin C, mg 78 15.8 Diglycerides, M. Alpina Oil**, Inositol, Choline, mg 244 49 Ascorbic Acid, Zinc Sulfate, Taurine, Ferrous Inositol, mg 148 30 Sulfate, High Oleic Sunflower Oil, Mannitol, Minerals L-Carnitine, Vitamin E Acetate, Glycerol, Calcium, mg 596 121 Mono- and Distearate, Natural Flavour, Phosphorus, mg 444 90 Sodium Polyphosphate, Sunflower Lecithin, Magnesium, mg 68 13.8 Sodium Ascorbate, Vitamin K1, Niacinamide, Iron, mg 14.7 3 Vitamin A Palmitate, Vitamin D3, D-Calcium Zinc, mg 29 5.8 Pantothenate, D-Biotin, Copper Sulfate, Manganese, mg 0.44 0.09 Copper, mg 0.95 0.19 Manganese Sulfate, Thiamin Hydrochloride, Iodine, mcg 96 19.4 Potassium Iodide, Pyridoxine Hydrochloride, Molybdenum, mcg 15.8 3.2 Sodium Selenite, Riboflavin, Vitamin B12, Chromium, mcg 16.2 3.3 Folic Acid, Chromium Chloride and Sodium Selenium, mcg 44 8.9 Molybdate. Sodium, mg 303 61 * A source of Docosahexaenoic Acid (DHA) Potassium, mg 797 161 ** A source of Arachidonic Acid (ARA) Chloride, mg 384 78 Complex Junior MSD Drink Mix Nutrition Information: 79 Complex Essential MSD Drink Mix An isoleucine-, leucine-, and valine-free powdered formula for the dietary management of maple syrup urine disease (MSUD) in children and adults, including pregnant women and women of child bearing age. Main Features: Indications: • Free from isoleucine, leucine and valine • Maple syrup urine disease (MSUD) • Vanilla flavour For details on administration and household measurements, please see pages 146-161. • Complete with essential vitamins and minerals • Provides 25 g of protein equivalent per 100 g of powder Metabolics • Contains a 4:1 ratio of Omega-6 to Omega-3 80 • Osmolalilty (mOsm/kg): 813 Based on standard dilution of 40 g powder to 210 mL of water (7 fl oz) • Displacement: 0.75 mL/g Ordering Information: Product Code 5972 Product Packaging 4 x 454 g (1 lb) Calories Per Can 1725 Per 100 g Per 10 g Protein Equivalent (1 scoop) NutrientsPowder Calories 380152 Protein Equivalent, g 25 10 Carbohydrate, g 47 19 Fat, g 12 5 Saturated Fat, g 2.1 0.85 Monounsaturated Fat, g 6.8 2.7 Polyunsaturated Fat, g 2.6 1 Linoleic Acid, mg 1871 748 α-Linolenic Acid, mg 493 197 Amino Acids, g L-Alanine 2.701.08 L-Arginine 1.280.51 L-Asparagine 1.450.58 L-Cystine 0.560.22 L-Glutamic Acid 0.86 0.35 L-Glutamine 7.172.87 Glycine 0.670.27 L-Histidine 1.790.71 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine 2.270.91 L-Methionine 0.740.30 L-Phenylalanine 2.200.88 L-Proline 1.480.59 L-Serine 1.120.45 L-Threonine 1.810.72 L-Tryptophan 1.330.53 L-Tyrosine 2.200.88 L-Valine Nil Added Nil Added L-Carnitine 0.060.02 Taurine 0.140.06 Ingredients: Per 100 g Per 10 g Protein Equivalent (1 scoop) NutrientsPowder Vitamin A, IU (mcg R.E.) 1700 (637) 680 (255) (25% as beta-carotene) Vitamin D, IU (mcg) 600 (15) 240 (6) Vitamin E, IU (mg α T.E.) 18.4 (12.3) 7.3 (4.9) Vitamin K, mcg 50 20 Thiamin, mg 1.5 0.6 Riboflavin, mg 1.5 0.6 Vitamin B6, mg 1.3 0.52 2 0.8 Vitamin B12, mcg Niacin, mg 12 4.8 Folic Acid, mcg 250 100 Pantothenic Acid, mg 5.5 2.2 Biotin, mcg 30 12 Vitamin C, mg 60 24 Choline, mg 100 40 Inositol, mg 40 16 Minerals Calcium, mg 886 355 Phosphorus, mg 864 346 Magnesium, mg 200 80 Iron, mg 13 5 Zinc, mg 12 4.8 Manganese, mg 1.5 0.6 Copper, mg 1 0.4 Iodine, mcg 120 48 Molybdenum, mcg 75 30 Chromium, mcg 40 16.1 Selenium, mcg 100 40 Sodium, mg 600 240 Potassium, mg 1301 520 Chloride, mg 860 344 Sugar, L- Glutamine, Modified Food Starch, Dextrin, Canola Oil, Maltodextrin, Safflower Oil, L-Lysine Acetate, L-Alanine, Natural and Artificial Flavour, Tricalcium Phosphate, Potassium Citrate, L-Phenylalanine, L-Tyrosine, L-Threonine, L-Histidine, L-Asparagine Monohydrate, Magnesium Phosphate, Sodium Chloride, L-Proline, Dipotassium Phosphate, L-Tryptophan, L-Arginine, L-Serine, Coconut Oil, Soybean Oil, L-Glutamic Acid, L-Methionine, Glycine, L-Cystine, Flaxseed Oil, Titanium Dioxide, Choline Bitartrate, Ascorbyl Palmitate, Mixed Tocopherols, Rosemary Extract, Sodium Citrate, Taurine, Ascorbic Acid, L-Carnitine, Ferrous Sulfate, Inositol, Vitamin E Acetate, Zinc Sulfate, Calcium Phosphate, Niacinamide, Copper Gluconate, D-Calcium Pantothenate, Vitamin D3, Vitamin A Palmitate, Vitamin K1, Manganese Sulfate, Mono –and Diglycerides, D-Biotin, Beta-carotene, Chromium Chloride, Sodium Selenite, Pyridoxine Hydrochloride, Riboflavin, Potassium Iodide, Thiamin Mononitrate, Folic Acid, Sodium Molybdate and Vitamin B12. Complex Essential MSD Drink Mix Nutrition Information: Contains: Soy, Coconut. 81 Complex MSD Amino Acid Blend An isoleucine-, leucine-, and valine-free powdered formula for the dietary management of maple syrup urine disease (MSUD) in children and adults, including pregnant women and women of child bearing age. Main Features: Indications: • An isoleucine-, leucine- and valine-free powder • Maple syrup urine disease (MSUD) • Unflavoured For details on administration and household measurements, please see pages 146-161. • Does not contain fat, carbohydrate or vitamins and minerals • Only 40 calories per serving • Provides 81 g of protein equivalent per 100 g of powder Metabolics • Available in cans 82 Ordering Information: Product Code 5900 Product Packaging 4 x 454 g (1 lb) Calories Per Can 1466 Per 100 g Per 10 g Protein Equivalent (1 scoop) NutrientsPowder Calories 32340 Protein Equivalent, g 81 10 Carbohydrate, g 0 0 Fat, g 0 0 Ingredients: Per 100 g Per 10 g Amino Acids, g Powder Protein Equivalent L-Alanine 8.721.08 L-Arginine 4.130.51 L-Asparagine 4.670.58 L-Cystine 1.800.22 L-Glutamic Acid 2.79 0.35 L-Glutamine 23.122.87 Glycine 2.160.27 L-Histidine 5.760.71 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine 7.320.91 L-Methionine 2.380.30 L-Phenylalanine7.08 0.88 L-Proline 4.760.59 L-Serine 3.600.45 L-Threonine 5.830.72 L-Tryptophan 4.280.53 L-Tyrosine 7.080.88 L-Valine Nil Added Nil Added L-Carnitine 0.190.02 Taurine 0.460.06 L-Glutamine, L-Lysine Acetate, L-Alanine, L-Phenylalanine, L-Tyrosine, L-Threonine, L-Histidine, L-Asparagine Monohydrate, L-Proline, L-Tryptophan, L-Arginine, L-Serine, L-Glutamic Acid, L-Methionine, Glycine, L-Cystine, Taurine, Silicon Dioxide and L-Carnitine. Note: Must combine with an appropriate vitamin & mineral supplement when taken as the sole source of amino acid protein. Complex MSD Amino Acid Blend Nutrition Information: • Displacement: 0.48 mL/g 83 Complex MSD Amino Acid Bars An isoleucine-, leucine-, and valine-free, metabolic formula in bar format for the dietary management of maple syrup urine disease (MSUD) in children and adults. Main Features: Indications: • An isoleucine-, leucine- and valine-free bar • Great tasting chocolate flavour (artificially flavoured) • An alternative to liquid MSUD formula • 1 bar provides 10 g of protein equivalent • Maple syrup urine disease (MSUD) For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Packaging 12 x 47 g (1.66 oz) Calories Per Bar 262 Ingredients: Per 100 g Per 10 g Amino Acids, g Powder Protein Equivalent L-Alanine 2.311.08 L-Arginine 1.090.51 L-Asparagine 1.230.58 L-Cystine 0.480.22 L-Glutamic Acid 0.74 0.35 L-Glutamine 6.122.88 Glycine 0.570.27 L-Histidine 1.520.72 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine 1.940.91 L-Methionine 0.630.30 L-Phenylalanine 1.870.88 L-Proline 1.260.59 L-Serine 0.950.45 L-Threonine 1.540.73 L-Tryptophan 1.130.53 L-Tyrosine 1.870.88 L-Valine Nil Added Nil Added L-Carnitine 0.050.02 Taurine 0.120.06 Cocoa Butter, Sugar, Amino Acids (L-Glutamine, L-Lysine Acetate, L-Alanine, L-Phenylalanine, L-Tyrosine, L-Threonine, L-Histidine, L-Asparagine Monohydrate, L-Proline, L-Tryptophan, L-Arginine, L-Serine, L-Glutamic Acid, L-Methionine, Glycine, L-Cystine, Taurine, L-Carnitine), Artificial Color (Partially Hydrogenated Vegetable Oil, Red 40 Lake, Yellow 6 Lake, Blue 1 Lake, Soy Lecithin), Artificial Flavour and Soy Lecithin. Note: Must combine with an appropriate vitamin & mineral supplement when taken as the sole source of amino acid protein. Metabolics Product Code 5980 Per 100 g Per 10 g NutrientsPowder Protein Equivalent Calories 558262 Protein Equivalent, g 21 10 Carbohydrate, g 34 16 Sugars, g 33 16 Fat, g 39 18 Saturated Fat, g 23 11 Monounsaturated Fat, g 13 6 Polyunsaturated Fat, g 1 0.3 Trans Fat, g 0 0 Complex MSD Amino Acid Bars Nutrition Information: 84 85 MSUD Aid Metabolics A leucine-, isoleucine-, valine-free powdered formula for the dietary management of maple syrup urine disease in individuals over 1 year of age. 86 Main Features: Indications: • Leucine-, isoleucine-, valine-free • Contains a mixture of the other essential and non-essential amino acids, carbohydrate, and select vitamins, minerals and trace elements • Unflavoured powder • MSUD Aid provides 60 g of protein equivalent per 100 g of powder • Does not contain fat thereby allowing for greater flexibility in modifying energy intake • Maple syrup urine disease (MSUD) For general guidance on administration, please follow instructions for Maxamaid or Maxamum brands on page 153. Ordering Information: Product Code 10143 Product Packaging Calories Per Can 4 x 200 g (7 oz)500 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 25042 Protein Equivalent, g 60 10 Fat, g 0 0 Carbohydrate, g 3 0.5 Amino Acids, g L-Alanine 7.11.18 L-Arginine 5.10.85 L-Aspartic Acid 12.1 2.02 L-Cystine 2.10.35 L-Glutamic Acid 13.3 2.22 Glycine 3.90.65 L-Histidine 2.70.45 L-Isoleucine Nil Added Nil Added L-Leucine Nil Added Nil Added L-Lysine 7.11.18 L-Methionine 1.90.32 L-Phenylalanine3.8 0.63 L-Proline 2.30.38 L-Serine 2.40.40 L-Threonine 3.30.55 L-Tryptophan 1.20.20 L-Tyrosine 3.80.63 L-Valine Nil Added Nil Added Ingredients: Per 10 g Vitamins Per 100 g Protein Equivalent Thiamin, mg 2.0 0.3 Riboflavin, mg 2.5 0.4 2.0 0.3 Vitamin B6, mg 20 3.3 Vitamin B12, mcg Niacin, mg 25 4.2 Folic Acid, mcg 400 67 Pantothenic Acid, mcg 20 3.3 Biotin, mcg 600 100 Minerals Calcium, mg 2500 417 Phosphorus, mg 1500 250 Magnesium, mg 300 50 Iron, mg 25 4.2 Zinc, mg 15 2.5 Manganese, mg 3.5 0.58 Copper, mcg 2500 417 Iodine, mcg 150 25 Sodium, mg (mEq) 1400 (60.9) 233 (10.2) Potassium, mg (mEq) 2600 (66.7) 433 (11.1) Chloride, mg (mEq) 2800 (80) 467 (13.3) L-Lysine L-Glutamate, L-Aspartic Acid, L-Alanine, Tripotassium Citrate, L-Glutamic Acid, Calcium Phosphate Dibasic, L-Arginine, Glycine, Sodium Chloride, L-Phenylalanine, L-Tyrosine, Calcium Phosphate Tribasic, L-Threonine, Hydrolyzed Cornstarch, L-Histidine, L-Serine, L-Proline, L-Cystine, L-Methionine, Magnesium, Acetate, L-Tryptophan, Potassium Chloride, Calcium Chloride, Ferrous Sulfate, Zinc Sulfate, Niacinamide, Calcium-D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Hydrochloride, Biotin, Folic Acid, Potassium Iodide, Cyanocobalamine. MSUD Aid Nutrition Information: 87 XLeu Analog Metabolics A leucine-free powdered infant formula for the dietary management of isovaleric acidemia and other proven disorders of leucine metabolism. 88 Main Features: Indications: • Leucine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • XLeu Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Isovaleric acidemia • Other proven disorders of leucine metabolism For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118361 Product Packaging 6 x 400 g (14 oz) Calories Per Can 1900 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 475 365 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 6.8 5.2 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 Linoleic Acid, mg 3025 2330 Carbohydrate, g 59 45 Amino Acids, g L-Alanine0.6 0.46 L-Arginine1 0.77 L-Aspartic Acid 0.8 0.62 L-Cystine0.42 0.32 L-Glutamic Acid 1 0.77 Glycine2.05 1.58 L-Histidine0.66 0.51 L-Isoleucine0.49 0.38 L-Leucine Nil Added Nil Added L-Lysine1.18 0.91 L-Methionine0.28 0.22 L-Phenylalanine0.77 0.59 L-Proline2 1.54 L-Serine0.6 0.46 L-Threonine0.86 0.66 L-Tryptophan0.34 0.26 L-Tyrosine0.77 0.59 L-Valine0.55 0.42 L-Carnitine0.01 0.01 Taurine0.02 0.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent 1356 (406) Vitamin A, IU (mcg R.E.) 1760 (528) 262 (6.5) Vitamin D, IU (mcg) 340 (8.5) 3.8 (2.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 16 Vitamin K, mcg 21 385 Thiamin, mcg 500 462 Riboflavin, mcg 600 400 520 Vitamin B6, mcg 1.25 0.96 Vitamin B12, mcg 3462 Niacin, mcg 4500 29 Folic Acid, mcg 38 2000 Pantothenic Acid, mcg 2600 20 Biotin, mcg 26 31 Vitamin C, mg 40 38 Choline, mg 50 77 Inositol, mg 100 Minerals 462 Calcium, mg 600 385 Phosphorus, mg 500 31 Magnesium, mg 40 8 Iron, mg 10 6 Zinc, mg 8 462 Manganese, mcg 600 346 Copper, mcg 450 36 Iodine, mcg 47 12 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 92 (4.0) Sodium, mg (mEq) 120 (5.2) 323 (8.3) Potassium, mg (mEq) 420 (10.8) 223 (6.3) Chloride, mg (mEq) 290 (8.2) Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, L-Proline, Glycine, Calcium Phosphate Dibasic, L-Arginine, L-Aspartic Acid, Galactose, Tripotassium Citrate, L-Phenylalanine, L-Tyrosine, L-Alanine, Calcium Phosphate Monobasic, L-Threonine, L-Histidine, L-Serine, Mono and Diglycerides, L-Valine, L-Cystine, L-Isoleucine, Sodium Chloride, L-Methionine, L-Glutamic Acid, L-Tryptophan, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. XLeu Analog Nutrition Information: ™ 89 Metabolics A leucine-free, mildly-flavoured powdered formula for the dietary management of isovaleric acidemia in individuals over 1 year of age. 90 Main Features: Indications: • Leucine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate (including a multi-fiber blend), fat (including DHA), vitamins, minerals, and trace elements • Provides 28 g protein equivalent and 12.5 g fat per 100 g of powder • Available in Plain • Displacement: 0.72 mL/g • Isovaleric acidemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Packaging Calories Per Can 89471 6 x 400 g 1508 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 377 134.6 Protein Equivalent, g 28 10 Fat, g 12.5 4.5 DHA, mg 180 64 Carbohydrate, g 41.2 14.7 Fiber, g 11.2 4.0 of which Soluble, g 8.0 2.9 of which Insoluble, g 3.2 1.1 Amino Acids, g L-Alanine 1.350.48 L-Arginine 2.350.84 L-Aspartic Acid 2.0 0.71 L-Cystine 0.940.34 L-Glutamic acid 1.88 0.67 L-Glutamine 3.161.1 Glycine 4.61.6 L-Histidine 1.40.50 L-Isoleucine 0.920.33 L-Leucine Nil Added Nil Added L-Lysine 2.20.79 L-Methionine 0.640.23 L-Phenylalanine1.70.61 L-Proline 4.11.5 L-Serine 1.50.52 L-Threonine 1.50.54 L-Tryptophan 0.580.21 L-Tyrosine 1.70.61 L-Valine 1.00.37 L-Carnitine 0.020.01 Taurine 0.060.02 Per 10 g Vitamins Per 100 g Protein Equivalent Vit A, IU (mcg R.E.) 1748.(525)628.(187.5) Vit D, IU (mcg) 1052.(26.3)379.(9.4) Vit E, IU (mg-α-TE)15.6.(10.5)5.6.(3.8) Vit K, mcg 17.5 6.3 Thiamin, mg 1.2 0.43 Riboflavin, mg 0.91 0.33 0.91 0.33 Vit B6, mg 1.6 0.57 Vit B12, mcg Niacin, mg 2.5 0.89 Folic Acid, mcg 263 93.9 Pantothenic Acid, mg 5.3 1.9 Biotin, mcg 14 5 Vit C, mg 52.5 18.8 Choline, mg 280 100 Inositol, mg 70 25 Minerals Calcium, mg 1225 437.5 Phosphorus, mg 801 286.1 Magnesium, mg 140 50 Iron, mg 12.5 4.5 Zinc, mg 6.1 2.2 Manganese, mg 1.2 0.4 Copper, mcg 700 250 Iodine, mcg 174 62.1 Molybdenum, mcg 31.9 11.4 Chromium, mcg 12.8 4.6 Selenium, mcg 35.3 12.6 Sodium, mg 350 125 Potassium, mg 556 198.6 Chloride, mg 508 181.4 Ingredients: Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Chain Triglycerides (Palm Kernel and/or Coconut Oil), Sunflower), Glycine, L-Proline, Calcium Phosphate Dibasic, Fructo-oligosaccharides, L-Glutamine, Inulin, L-Lysine Acetate, Corn Starch, Microcrystalline Cellulose, L-Arginine, Artificial Flavour, Magnesium L-Aspartate, Gum Arabic, L-Glutamic Acid, L-Tyrosine, L-Phenylalanine, Tripotassium Citrate, L-Threonine, L-Serine, L-Histidine, L-Alanine, L-Valine, Trisodium Citrate, L-Cystine, L-Isoleucine, Maltodextrin, Choline Bitartrate, Calcium Chloride, L-Methionine, L-Tryptophan, CAEM (an emulsifier), C. Cohnii Oil**, L-Aspartic Acid, Sodium Chloride, L-Ascorbic Acid, M-Inositol, Soy Fiber, Taurine, Ferrous Sulfate, Sunflower Lecithin, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Ascorbyl Palmitate, Potassium iodide, Mixed Tocopherols, Sodium Molybdate, Sodium Selenite, Chromium Chloride, DL-alpha Tocopherol, Vitamin D3, Phylloquinone, D-Biotin, Cyanocobalamin. IVA Anamix Next Nutrition Information: IVA Anamix® Next **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) 91 Metabolics A leucine-free powdered formula for the dietary management of isovaleric acidemia and other proven disorders of leucine metabolism in toddlers and younger children. 92 Main Features: Indications: • Leucine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XLeu Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Isovaleric acidemia • Other proven disorders of leucine metabolism For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117791 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine1.36 0.54 L-Arginine2.22 0.89 L-Aspartic Acid 1.87 0.75 L-Cystine0.82 0.33 Glycine3.99 1.60 L-Histidine1.28 0.51 L-Isoleucine0.78 0.31 L-Leucine Nil Added Nil Added L-Lysine1.95 0.78 L-Methionine0.54 0.22 L-Phenylalanine1.5 0.60 L-Proline4.01 1.60 L-Serine1.24 0.50 L-Threonine1.32 0.53 L-Tryptophan0.5 0.20 L-Tyrosine1.45 0.58 L-Valine0.87 0.35 L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1665 (500) 666 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) 232 (10) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Ingredients: Sugar, Corn Syrup Solids, L-Proline, Glycine, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, Citric Acid, L-Lysine Acetate, Tripotassium Citrate, Artificial Flavours, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Alanine, L-Threonine, L-Histidine, L-Serine, Maltodextrin, Disodium Hydrogen Phosphate, L-Valine, L-Cystine, Sodium Chloride, L-Isoleucine, Magnesium Acetate, N-Acetyl L-Methionine, Choline Bitartrate, L-Tryptophan, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XLeu Maxamaid Nutrition Information: XLeu Maxamaid® 93 Metabolics A leucine-free powdered formula for the dietary management of isovaleric acidemia and other proven disorders of leucine metabolism in older children and adults, including pregnant women and women of child-bearing age. 94 Main Features: Indications: • Leucine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements (including iron, selenium and chromium) • Age-appropriate DRI formulation • XLeu Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Isovaleric acidemia • Other proven disorders of leucine metabolism For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117790 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1385 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 305 76 Protein Equivalent, g 40 10 Fat, g <1 <0.25 Carbohydrate, g 34 8.5 Amino Acids, g L-Alanine2.2 0.55 L-Arginine3.6 0.90 L-Aspartic Acid 3 0.75 L-Cystine1.3 0.33 L-Glutamic Acid 3.9 0.98 Glycine6.3 1.58 L-Histidine2.1 0.53 L-Isoleucine1.2 0.30 L-Leucine Nil Added Nil Added L-Lysine3 0.75 L-Methionine0.86 0.22 L-Phenylalanine2.3 0.58 L-Proline6.3 1.58 L-Serine1.9 0.48 L-Threonine2.1 0.53 L-Tryptophan0.79 0.20 L-Tyrosine2.3 0.58 L-Valine1.4 0.35 L-Carnitine0.039 0.01 Taurine0.14 0.04 L-Glutamine0.32 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 2228 (669) 557 (167) Vitamin D, IU (mcg) 332 (8.3) 83 (2.1) Vitamin E, IU (mg α T.E.) 18.3 (12.3) 4.6 (3.1) Vitamin K, mcg 82 21 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 0.4 Vitamin B6, mg 3.1 0.8 Vitamin B12, mcg Niacin, mg 5.7 1.4 Folic Acid, mcg 491 123 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 Vitamin C, mg 62 16 Choline, mg 430 108 Inositol, mg 80 20 Minerals Calcium, mg 1183 296 Phosphorus, mg 1137 284 Magnesium, mg 306 77 Iron, mg 14.7 3.7 Zinc, mg 9 2 Manganese, mg 1.8 0.5 Copper, mcg 820 205 Iodine, mcg 131 33 Molybdenum, mcg 37 9 Chromium, mcg 26 7 Selenium, mcg 58 15 Sodium, mg (mEq) 560 (24.3) 140 (6.1) Potassium, mg (mEq) 700 (17.9) 175 (4.5) Chloride, mg (mEq) 560 (16) 140 (4) Ingredients: Sugar, L-Lysine L-Glutamate, L-Proline, Glycine, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Arginine, L-Aspartic Acid, L-Phenylalanine, Artificial Flavour, L-Tyrosine, L-Alanine, L-Threonine, Citric Acid, L-Histidine, L-Serine, Magnesium Acetate, L-Valine, L-Cystine, L-Isoleucine, Tripotassium Citrate, Choline Bitartrate, Sodium Chloride, L-Methionine, L-Glutamic Acid, L-Tryptophan, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XLeu Maxamum Nutrition Information: XLeu Maxamum® 95 Metabolics A lysine- and tryptophan-free powdered infant formula for the dietary management of glutaric acidemia type I. 96 Main Features: Indications: • Lysine- and tryptophan-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • XLys, XTrp Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Glutaric acidemia type I For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Packaging Calories Per Can 118328 6 x 400 g (14 oz) 1900 Per 10 g Nutrients Per 100 g Protein Equivalent Calories475 365 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 6.8 5.2 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 Linoleic Acid, mg 3025 2330 Carbohydrate, g 59 45 Amino Acids, g L-Alanine0.61 0.47 L-Arginine1.1 0.85 L-Aspartic Acid 0.9 0.69 L-Cystine0.43 0.33 L-Glutamic Acid 1.1 0.85 Glycine1 0.77 L-Histidine0.65 0.50 L-Isoleucine1.03 0.79 L-Leucine1.75 1.35 L-Lysine Nil Added Nil Added L-Methionine0.27 0.21 L-Phenylalanine0.77 0.59 L-Proline1.24 0.95 L-Serine0.77 0.59 L-Threonine0.86 0.66 L-Tryptophan Nil Added Nil Added L-Tyrosine0.77 0.59 L-Valine1.12 0.86 L-Carnitine0.01 0.01 Taurine 0.020.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1760 (528) 1357 (406) Vitamin D, IU (mcg) 340 (8.5) 262 (6.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 3.8 (2.5) Vitamin K, mcg 21 16 Thiamin, mcg 500 385 Riboflavin, mcg 600 462 520 Vitamin B6, mcg 400 1.25 0.96 Vitamin B12, mcg Niacin, mcg 4500 3462 Folic Acid, mcg 38 29 Pantothenic Acid, mcg 2600 2000 Biotin, mcg 26 20 Vitamin C, mg 40 31 Choline, mg 50 38 Inositol, mg 100 77 Minerals Calcium, mg 600 462 Phosphorus, mg 500 385 Magnesium, mg 40 31 Iron, mg 10 8 Zinc, mg 8 6 Manganese, mcg 600 462 Copper, mcg 450 346 Iodine, mcg 47 36 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 12 Sodium, mg (mEq) 120 (5.2) 92 (4.0) Potassium, mg (mEq) 420 (10.8) 323 (8.3) Chloride, mg (mEq) 290 (8.2) 223 (6.3) Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), Calcium Phosphate Dibasic, L-Leucine, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, Galactose, L-Threonine, Tripotassium Citrate, L-Phenylalanine, L-Tyrosine, L-Serine, Calcium Phosphate Monobasic, L-Alanine, L-Histidine, Mono and Diglycerides, L-Cystine, Sodium Chloride, L-Methionine, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. XLys, XTrp Analog XLys, XTrp Analog Ingredients: Nutrition Information: ™ 97 Metabolics A lysine- and tryptophan-free powdered formula for the dietary management of glutaric acidemia type I in toddlers and young children. 98 Main Features: Indications: • Lysine- and tryptophan-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XLys, XTrp Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Glutaric acidemia type I For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Packaging Calories Per Can 117780 6 x 454 g (1 lb) 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine1.28 0.51 L-Arginine2.23 0.89 L-Aspartic Acid 1.86 0.74 L-Cystine0.83 0.33 Glycine2 0.80 L-Histidine1.27 0.51 L-Isoleucine2 0.80 L-Leucine3.42 1.37 L-Lysine Nil Added Nil Added L-Methionine0.53 0.21 L-Phenylalanine1.51 0.60 L-Proline2.42 0.97 L-Serine1.49 0.60 L-Threonine1.68 0.67 L-Tryptophan Nil Added Nil Added L-Tyrosine1.51 0.60 L-Valine2.18 0.87 L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Ingredients: Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 1665 (500) 666 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 14.5 5.8 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) (10) 232 Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Sugar, Corn Syrup Solids, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, L-Leucine, Citric Acid, Tripotassium Citrate, L-Proline, L-Valine, Glycine, L-Isoleucine, Artificial Flavours, L-Threonine, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Serine, L-Histidine, L-Alanine, Maltodextrin, Disodium Hydrogen Phosphate, L-Cystine, Sodium Chloride, Magnesium Acetate, N-Acetyl L-Methionine, Choline Bitartrate, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XLys, XTrp Maxamaid Nutrition Information: XLys, XTrp Maxamaid® 99 Metabolics A lysine- and tryptophan-free powdered formula for the dietary management of glutaric acidemia type I in older children and adults, including pregnant women and women of child-bearing age. 100 Main Features: Indications: • Lysine- and tryptophan-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XLys, XTrp Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Glutaric acidemia type I For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117788 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1385 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 305 76 Protein Equivalent, g 40 10 Fat, g <1 <0.25 Carbohydrate, g 34 8.5 Amino Acids, g L-Alanine2 0.50 L-Arginine3.5 0.88 L-Aspartic Acid 2.9 0.73 L-Cystine1.3 0.33 L-Glutamic Acid 3.9 0.98 Glycine3.1 0.78 L-Histidine2 0.50 L-Isoleucine3.1 0.78 L-Leucine5.3 1.33 L-Lysine Nil Added Nil Added L-Methionine0.82 0.21 L-Phenylalanine2.3 0.58 L-Proline3.7 0.93 L-Serine2.3 0.58 L-Threonine2.6 0.65 L-Tryptophan Nil Added Nil Added L-Tyrosine2.3 0.58 L-Valine3.4 0.85 L-Carnitine0.039 0.01 0.04 Taurine0.14 0.08 L-Glutamine0.32 Ingredients: Per 10 g Vitamins Per 100 g Protein Equivalent 5 57 (167) Vitamin A, IU (mcg R.E.) 2228 (669) 83 (2.1) Vitamin D, IU (mcg) 332 (8.3) 4.6 (3.1) α Vitamin E, IU (mg T.E.) 18.3 (12.3) 21 Vitamin K, mcg 82 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 0.4 Vitamin B6, mg 3.1 0.8 Vitamin B12, mcg 3.0 Niacin, mg 12 123 Folic Acid, mcg 491 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 16 Vitamin C, mg 62 108 Choline, mg 430 20 Inositol, mg 80 Minerals 296 Calcium, mg 1183 284 Phosphorus, mg 1137 77 Magnesium, mg 306 Iron, mg 14.7 3.7 2 Zinc, mg 9 Manganese, mg 1.8 0.5 205 Copper, mcg 820 33 Iodine, mcg 131 9 Molybdenum, mcg 37 7 Chromium, mcg 26 15 Selenium, mcg 58 140 (6.1) Sodium, mg (mEq) 560 (24.3) Potassium, mg (mEq) 700 (17.9) 175 (4.4) Chloride, mg (mEq) 560 (16) 140 (4) Sugar, L-Leucine, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, L-Threonine, Artificial Flavour, L-Phenylalanine, L-Tyrosine, L-Serine, Citric Acid, L-Alanine, L-Histidine, Magnesium Acetate, L-Cystine, Tripotassium Citrate, Choline Bitartrate, Sodium Chloride, L-Methionine, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XLys, XTrp Maxamum Nutrition Information: XLys, XTrp Maxamum® 101 GlutarAde Junior GA-1 Drink Mix Nutrients Metabolics A lysine-free and low tryptophan powdered formula for the dietary management of Glutaric Aciduria Type 1 (GA-1) in young children. 102 Main Features: Indications: • Lysine-free • Contains 60 mg of tryptophan per 100 g powder • Contains arginine • Complete with vitamins and minerals • Amino acid profile specifically designed for GA-1† • Provides 10 g of protein equivalent per 100 g of powder • Contains a source of Omega-3 fatty acids • Mild neutral flavour • Displacement: 0.60 mL/g • Glutaric acidemia type I Strauss KA, et al. Mol Genet Metab. 2011. † For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 7510 Product Packaging 4 x 400 g (14.1 oz) Calories Per Can 1640 Per 100 g Per 100 kcal Calories 410100 Protein Equivalent, g 10 2.5 Carbohydrate, g 69 17 Fat, g 10 2.5 Saturated Fat, g 2 0.48 Monounsaturated Fat, g 5.3 1.3 Polyunsaturated Fat, g 2.6 0.63 Linoleic Acid, mg 1901 463 α-Linolenic Acid, mg 721 176 Amino Acids, g L-Alanine 0.480.12 L-Arginine 1.080.26 L-Asparagine 0.72 0.18 L-Cystine 0.180.04 L-Glutamic Acid 0.36 0.09 L-Glutamine 1.800.44 Glycine 0.240.06 L-Histidine 0.360.09 L-Isoleucine 0.840.21 L-Leucine 1.380.34 L-Lysine Nil Added Nil Added L-Methionine 0.410.10 L-Ornithine 0.240.06 L-Phenylalanine 0.640.16 L-Proline 0.600.15 L-Serine 0.240.06 L-Threonine 0.640.16 L-Tryptophan 0.060.01 L-Tyrosine 0.720.18 L-Valine 0.960.23 L-Carnitine 0.030.01 Taurine 0.060.01 Ingredients: Vitamins Per 100 g Per 100 kcal Vitamin A, IU (mcg R.E.) 1373.(412335.(101) Vitamin D, IU (mcg) 525.(13.1)128.(3.2) Vitamin E, IU (mg α T.E.) 8.5 (5.7) 2.1 (1.4) Vitamin K, mcg 34 8.3 Thiamin, mg 0.83 0.2 Riboflavin, mg 0.69 0.17 Vitamin B6, mg 0.66 0.16 Vitamin B12, mcg 1.4 0.35 Niacin, mg 6.6 1.6 Folic Acid, mcg 150 37 Pantothenic Acid, mg 6 1.5 Biotin, mcg 31 7.6 Vitamin C, mg 56 13.6 Choline, mg 213 52 Inositol, mg 125 30 Minerals Calcium, mg 460 112 Phosphorus, mg 400 97 Magnesium, mg 60 14.6 Iron, mg 8 2 Zinc, mg 7 1.6 Manganese, mg 0.43 0.1 Copper, mg 0.5 0.12 Iodine, mcg 90 22 Molybdenum, mcg 18 4.4 Chromium, mcg 12 2.9 Selenium, mcg 40 9.7 Sodium, mg 221 54 Potassium, mg 589 144 Chloride, mg 332 81 Corn Syrup Solids, Modified Food Starch, Canola Oil, Maltodextrin, Safflower Oil, Natural and Artificial Flavour, L-Glutamine, L-Leucine, Tricalcium Phosphate, L-Arginine, L-Valine, Coconut Oil, Soybean Oil, L-Isoleucine, L-Asparagine Monohydrate, Dipotassium Phosphate, Flaxseed Oil, L-Tyrosine, L-Phenylalanine, L-Threonine, L-Proline, Choline Bitartrate, Potassium Chloride, L-Ornithine-Alpha Ketoglutarate, L-Alanine, Magnesium Phosphate, L-Methionine, L-Glutamic Acid, L-Histidine, Glycine, L-Serine, Ascorbyl Palmitate, Sodium Citrate, Mixed Tocopherols, Rosemary Extract, L-Cystine, Sodium Chloride, Inositol, Silicon Dioxide, Ascorbic Acid, L-Tryptophan, Taurine, Ferrous Sulfate, Calcium Phosphate, L-Carnitine, Zinc Sulfate, Vitamin E Acetate, Niacinamide, Calcium D-Pantothenate, Mono- and Diglycerides, Vitamin A Palmitate, Vitamin D3, Copper Gluconate, Vitamin K1, D-Biotin, Manganese Sulfate, Sodium Selenite, Thiamin Mononitrate, Pyroxidine Hydrochloride, Riboflavin, Potassium Iodide, Chromium Chloride, Folic Acid, Vitamin B12 and Sodium Molybdate. GlutarAde Junior GA-1 Drink Mix Nutrition Information: ™ 103 Metabolics A lysine-free and low tryptophan powdered formula for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults, including pregnant women and women of child bearing age. 104 Main Features: Indications: • 25 g of protein equivalent per 100 g of powder • Amino acid profile specifically designed for GA-1† • Lysine-free • Contains 150 mg of tryptophan per 100 g powder • Contains 275 mg of Omega-3 fatty acids per 10 g PE • Osmolalilty (mOsm/kg): 797 Based on standard dilution of 40 g powder to 210 mL of water (7 fl oz) • Vanilla flavour • Displacement: 0.75 mL/g • Glutaric acidemia type I Strauss KA, et al. Mol Genet Metab. 2011. † For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 7542 Product Packaging 4 x 454 g (1 lb) Calories Per Can 1748 Nutrition Information: Ingredients: Per 10 g Protein Equivalent Per 10 g Protein Equivalent Sugar, Modified Corn Starch, Canola Oil, Nutrients Per 100 g (1 scoop) Vitamins Per 100 g (1 scoop) Maltodextrin, Safflower Oil, Dextrin, Calories 385154 Vitamin A, IU (mcg R.E.) 1700.(637)680.(255) L-Glutamine, L-Leucine, Natural and Protein Equivalent, g 25 10 (25% as beta-carotene) Artificial Flavour, L-Arginine, Dicalcium Carbohydrate, g 45 18 Vitamin D, IU (mcg)600.(15)240.(6) Phosphate, L-Valine, L-Isoleucine, Fat, g 13 5 Vitamin E, IU (mg α T.E.) 19.1 (12.8) 7.6 (5.1) L-Asparagine Monohydrate, L-Tyrosine, Saturated Fat, g 2.3 0.92 Vitamin K, mcg 70 28 Tricalcium Phosphate, L-Phenylalanine, Monounsaturated Fat, g 7.6 3 Thiamin, mg 1.5 0.6 L-Threonine, L-Proline, Potassium Citrate, Polyunsaturated Fat, g 2.9 1.1 Riboflavin, mg 1.5 0.6 L-Ornithine-Alpha Ketoglutarate, L-Alanine, Linoleic Acid, mg 2232 893 Vitamin B6, mg 1.4 0.56 α-Linolenic Acid, mg 687 275 Coconut Oil, Soybean Oil, L-Methionine, Vitamin B12, mcg 3 1.2 Amino Acids, g Sodium Citrate, Potassium Chloride, Niacin, mg 15.5 6.2 L-Alanine 1.200.48 L-Glutamic Acid, L-Histidine, Choline Folic Acid, mcg 300 120 L-Arginine 2.71.08 Pantothenic Acid, mg 7.5 3 Bitartrate, Glycine, L-Serine, L-Cystine, L-Asparagine 1.8 0.72 Biotin, mcg 30 12 Flaxseed Oil, Magnesium Oxide, Ascorbyl L-Cystine 0.450.18 Vitamin C, mg 60 24 Palmitate, Mixed Tocopherols, Rosemary L-Glutamic Acid 0.9 0.36 Choline, mg 313 125 Extract, Silicon Dioxide, L-Tryptophan, L-Glutamine 4.511.8 Inositol, mg 50 20 Taurine, Sodium Chloride, Ascorbic Acid, Glycine 0.60.24 Minerals: L-Histidine 0.90.36 Inositol, Ferric Orthophosphate, Vitamin E Calcium, mg 1257 503 L-Isoleucine 2.10.84 Acetate, L-Carnitine, Niacinamide, Calcium Phosphorus, mg 787 315 L-Leucine 3.461.38 Phosphate, Zinc Oxide, Sucralose (4mg/40g Magnesium, mg 201 80 L-Lysine Nil Added Nil Added Iron, mg 11.3 4.5 Powder), D-Calcium Pantothenate, L-Methionine 1.020.41 Zinc, mg 10 4 Copper Gluconate, Vitamin K1, Vitamin D3, L-Ornithine 0.60.24 Manganese, mg 1.9 0.76 Manganese Sulfate, Vitamin A Palmitate, L-Phenylalanine1.59 0.64 Copper, mg 1 0.4 Mono- and Diglycerides, D-Biotin, L-Proline 1.50.6 Iodine, mcg 115 46 Beta-carotene, Pyridoxine Hydrochloride, L-Serine 0.60.24 Molybdenum, mcg 31 12.4 L-Threonine 1.590.64 Potassium Iodide, Riboflavin, Thiamin Chromium, mcg 21 8.6 L-Tryptophan 0.150.06 Mononitrate, Sodium Selenite, Folic Acid, Selenium, mcg 63 25 L-Tyrosine 1.80.72 Vitamin B12, Chromium Chloride and Sodium, mg 384 154 L-Valine 2.40.96 Potassium, mg 874 350 Sodium Molybdate. L-Carnitine 0.040.01 Chloride, mg 475 190 Taurine 0.150.06 GlutarAde Essential GA-1 Drink Mix GlutarAde Essential GA-1 Drink Mix ™ 105 GlutarAde GA-1 Amino Acid Blend A lysine-free and low trypophan powdered formula for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults. Main Features: Indications: • Amino acid protein that can be mixed with any low protein food or drink • Glutaric acidemia type I • Boost protein intake by adding to current GA-1 formula For details on administration and household measurements, please see pages 146-161. • Provides 81 g of protein equivalent per 100 g of powder Metabolics • Does not contain fat, carbohydrate or vitamins and minerals 106 • Amino acid profile specifically designed for GA-1† Ordering Information: Product Code 7500 Product Packaging 4 x 454 g (1 lb) Calories Per Can 1471 Ingredients: Per 10 g Protein Equivalent Per 10 g Protein Equivalent L-Glutamine, L-Leucine, L-Arginine, L-Valine, Nutrients Per 100 g (1 scoop) Amino Acids, g Per 100 g (1 scoop) L-Isoleucine, L-Asparagine Monohydrate, L-Tyrosine, L-Phenylalanine, L-Threonine, Calories 32440 L-Alanine 3.860.48 L-Proline, L-Ornithine-Alpha Ketoglutarate, Protein Equivalent, g 81 10 L-Arginine 8.691.07 L-Alanine, L-Methionine, L-Glutamic Acid, Carbohydrate, g 0 0 L-Asparagine 5.79 0.71 L-Histidine, Glycine, L-Serine, L-Cystine, Fat, g 0 0 L-Cystine 1.450.18 Taurine, L-Tryptophan, Silicon Dioxide and Sodium, mg 355 44 L-Glutamic Acid 2.90 0.36 L-Carnitine. L-Glutamine 14.481.79 Glycine 1.930.24 Note: Must combine with an appropriate L-Histidine 2.900.36 vitamin & mineral supplement when taken L-Isoleucine 6.760.83 as the sole source of amino acid protein. L-Leucine 11.101.37 L-Lysine Nil Added Nil Added L-Methionine 3.280.41 L-Ornithine 1.930.24 L-Phenylalanine 5.120.63 L-Proline 4.830.60 L-Serine 1.930.24 L-Threonine 5.120.63 L-Tryptophan 0.480.06 L-Tyrosine 5.790.71 L-Valine 7.720.95 L-Carnitine 0.200.03 Taurine 0.480.06 GlutarAde GA-1 Amino Acid Blend Nutrition Information: ™ • Displacement: 0.48 mL/g Strauss KA, et al. Mol Genet Metab. 2011. † 107 XMet Analog Metabolics A methionine-free powdered infant formula for the dietary management of vitamin B6 non-responsive homocystinuria or hypermethioninemia. 108 Main Features: Indications: • Methionine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • XMet Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Vitamin B6 non-responsive homocystinuria • Hypermethioninemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118327 Product Packaging 6 x 400 g (14 oz) Calories Per Can 1900 Per 10 g Nutrients Per 100 g Protein Equivalent 365 Calories 475 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 6.8 5.2 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 2330 Linoleic Acid, mg 3025 Carbohydrate, g 59 45 Amino Acids, g 0.38 L-Alanine0.50 0.77 L-Arginine1 L-Aspartic Acid 0.8 0.62 0.30 L-Cystine0.39 L-Glutamic Acid 1.14 0.88 0.72 Glycine0.93 0.46 L-Histidine0.6 0.72 L-Isoleucine0.93 1.22 L-Leucine1.59 0.83 L-Lysine1.08 Nil Added L-Methionine Nil Added 0.54 L-Phenylalanine0.70 0.86 L-Proline1.12 0.53 L-Serine0.69 0.62 L-Threonine0.78 0.24 L-Tryptophan0.31 0.62 L-Tyrosine0.8 0.78 L-Valine1.01 0.01 L-Carnitine0.01 0.02 Taurine0.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent 1358 (406) Vitamin A, IU (mcg R.E.) 1760 (528) 262 (6.5) Vitamin D, IU (mcg) 340 (8.5) 3.8 (2.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 16 Vitamin K, mcg 21 385 Thiamin, mcg 500 462 Riboflavin, mcg 600 400 520 Vitamin B6, mcg 1.25 0.96 Vitamin B12, mcg 3462 Niacin, mcg 4500 29 Folic Acid, mcg 38 2000 Pantothenic Acid, mcg 2600 20 Biotin, mcg 26 31 Vitamin C, mg 40 38 Choline, mg 50 77 Inositol, mg 100 Minerals 462 Calcium, mg 600 385 Phosphorus, mg 500 31 Magnesium, mg 40 8 Iron, mg 10 6 Zinc, mg 8 462 Manganese, mcg 600 346 Copper, mcg 450 36 Iodine, mcg 47 12 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 92 (4.0) Sodium, mg (mEq) 120 (5.2) 323 (8.3) Potassium, mg (mEq) 420 (10.8) 223 (6.3) Chloride, mg (mEq) 290 (8.2) Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, Calcium Phosphate Dibasic, L-Leucine, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, Galactose, L-Aspartic Acid, Tripotassium Citrate, L-Threonine, L-Phenylalanine, L-Tyrosine, L-Serine, Calcium Phosphate Monobasic, L-Alanine, L-Histidine, Mono and Diglycerides, L-Cystine, L-Tryptophan, Sodium Chloride, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, L-Glutamic Acid, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. XMet Analog Nutrition Information: ™ 109 Metabolics A methionine-free, mildly-flavoured powdered formula for the dietary management of homocystinuria in individuals over 1 year of age. 110 Main Features: Indications: • Methionine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate (including a multi-fiber blend), fat (including DHA), vitamins, minerals, and trace elements • Provides 28 g protein equivalent and 12.5 g fat per 100 g of powder • Available in Plain • Displacement: 0.72 mL/g • Homocystinuria For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Packaging Calories Per Can 89470 6 x 400 g 1540 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 385 137.5 Protein Equivalent, g 28 10 Fat, g 12.5 4.5 DHA, mg 180 64 Carbohydrate, g 43.2 15.4 Fiber, g 11.2 4 of which Soluble, g 8 2.9 of which Insoluble, g 3.2 1.1 Amino Acids, g L-Alanine 1.40.5 L-Arginine 2.250.8 L-Aspartic Acid 2 0.71 L-Cystine 1.50.54 L-Glutamine 2.60.93 Glycine 2.130.76 L-Histidine 1.220.44 L-Isoleucine 2.10.75 L-Leucine 3.461.24 L-Lysine 2.440.87 L-Methionine Nil Added Nil Added L-Phenylalanine1.50.54 L-Proline 2.520.9 L-Serine 1.570.56 L-Threonine 20.71 L-Tryptophan 0.50.18 L-Tyrosine 1.60.57 L-Valine 2.30.82 L-Carnitine 0.020.01 Taurine 0.050.02 Per 10 g Vitamins Per 100 g Protein Equivalent Vit A, IU (mcg R.E.) 1399.(420)500.(150) Vit D, IU (mcg) 840.(21)300.(7.5) Vit E, IU (mg-α-TE) 12.5 (8.4) 4.5 (3) Vit K, mcg 14 5 Thiamin, mg 0.93 0.33 Riboflavin, mg 0.73 0.26 0.73 0.26 Vit B6, mg 1.3 0.5 Vit B12, mcg Niacin, mg 2.0 0.71 Folic Acid, mcg 210 75 Pantothenic Acid, mg 4.2 1.5 Biotin, mcg 11.2 4 Vit C, mg 42 15 Choline, mg 224 80 Inositol, mg 56 20 Minerals Calcium, mg 980 350 Phosphorus, mg 641 229 Magnesium, mg 113 40 Iron, mg 10 3.6 Zinc, mg 4.9 1.8 Manganese, mg 0.92 0.33 Copper, mcg 560 200 Iodine, mcg 139 49.6 Molybdenum, mcg 25.5 9.1 Chromium, mcg 10.2 3.6 Selenium, mcg 28.2 10.1 Sodium, mg 280 100 Potassium, mg 445 158.9 Chloride, mg 406 145 Ingredients: Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Chain Triglycerides (Palm Kernel and/or Coconut Oil), Sunflower), L-Arginine L-Aspartate, L-Leucine, Fructo-oligosaccharides, L-Lysine Acetate, Inulin, Corn Starch, L-Glutamine, Calcium Phosphate Dibasic, L-Proline, Microcrystalline Cellulose, L-Valine, Artificial Flavour, Glycine, L-Isoleucine, L-Threonine, Gum Arabic, L-Tyrosine, L-Serine, L-Cystine, L-Phenylalanine, L-Alanine, Tripotassium Citrate, Trisodium Citrate, L-Histidine, Calcium Chloride, Magnesium Hydrogen Phosphate, Maltodextrin, Choline Bitartrate, CAEM (an emulsifier), L-Tryptophan, C. Cohnii Oil**, Magnesium L-Aspartate, Tricalcium Citrate, L-Ascorbic Acid, Soy Fiber, M-Inositol, Taurine, Ferrous Sulfate, Sunflower Lecithin, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Ascorbyl Palmitate, Folic Acid, Potassium iodide, Mixed Tocopherols, Sodium Molybdate, Sodium Selenite, Chromium Chloride, DL-alpha Tocopherol, Vitamin D3, Phylloquinone, D-Biotin, Cyanocobalamin HCU Anamix Next Nutrition Information: HCU Anamix® Next **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) 111 Metabolics A methionine-free powdered formula for the dietary management of vitamin B6 nonresponsive homocystinuria or hypermethioninemia in toddlers and young children. 112 Main Features: Indications: • Methionine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XMet Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Vitamin B6 non-responsive homocystinuria • Hypermethioninemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code Product Packaging Calories Per Can 117787 6 x 454 g (1 lb) 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine1.16 0.46 L-Arginine2.04 0.82 L-Aspartic Acid 1.70 0.68 L-Cystine0.75 0.30 Glycine1.81 0.72 L-Histidine1.16 0.46 L-Isoleucine1.81 0.72 L-Leucine3.1 1.24 L-Lysine2.1 0.84 L-Methionine Nil Added Nil Added L-Phenylalanine1.37 0.55 L-Proline2.19 0.88 L-Serine1.35 0.54 L-Threonine1.52 0.61 L-Tryptophan0.61 0.24 L-Tyrosine1.37 0.55 L-Valine1.97 0.79 L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g Protein Equivalent 666 (200) Vitamin A, IU (mcg R.E.)1665 (500) 192 (4.8) Vitamin D, IU (mcg) 480 (12) 5.7 (3.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 0.8 Vitamin B12, mcg Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 22 Inositol, mg 56 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 232 (10) Sodium, mg (mEq) 580 (25.2) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Ingredients: Sugar, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Arginine L-Aspartate, L-Leucine, L-Lysine Acetate, Citric Acid, Tripotassium Citrate, L-Proline, L-Valine, Artificial Flavours, Glycine, L-Isoleucine, L-Threonine, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Serine, L-Alanine, L-Histidine, Maltodextrin, Disodium Hydrogen Phosphate, Sodium Chloride, Magnesium Acetate, L-Cystine, Choline Bitartrate, L-Tryptophan, Taurine, Magnesium L-Aspartate, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XMet Maxamaid Nutrition Information: XMet Maxamaid® 113 Metabolics A methionine-free powdered formula for the dietary management of vitamin B6 non-responsive homocystinuria or hypermethioninemia in older children and adults, including pregnant women and women of child-bearing age. 114 Main Features: Indications: • Methionine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XMet Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Vitamin B6 non-responsive homocystinuria • Hypermethioninemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117795 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1385 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 305 76 Protein Equivalent, g 40 10 Fat, g <1 <0.25 Carbohydrate, g 34 8.5 Amino Acids, g L-Alanine1.8 0.45 L-Arginine3.2 0.80 L-Aspartic Acid 2.7 0.68 L-Cystine1.2 0.30 L-Glutamic Acid 3.6 0.90 Glycine2.8 0.70 L-Histidine1.8 0.45 L-Isoleucine2.8 0.70 L-Leucine4.9 1.23 L-Lysine3.3 0.83 L-Methionine Nil Added Nil Added L-Phenylalanine2.2 0.55 L-Proline3.4 0.85 L-Serine2.1 0.53 L-Threonine2.4 0.60 L-Tryptophan0.95 0.24 L-Tyrosine2.2 0.55 L-Valine3.1 0.78 L-Carnitine0.039 0.01 Taurine0.14 0.04 L-Glutamine0.32 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent Vitamin A, IU (mcg R.E.) 2228 (669) 557 (167) Vitamin D, IU (mcg) 332 (8.3) 83 (2.1) Vitamin E, IU (mg α T.E.) 18.3 (12.3) 4.6 (3.1) Vitamin K, mcg 82 21 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 0.4 Vitamin B6, mg 3.1 0.8 Vitamin B12, mcg Niacin, mg 5.7 1.4 Folic Acid, mcg 491 123 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 Vitamin C, mg 62 16 Choline, mg 430 108 Inositol, mg 80 20 Minerals Calcium, mg 1183 296 Phosphorus, mg 1137 284 Magnesium, mg 306 77 Iron, mg 14.7 3.7 Zinc, mg 9 2 Manganese, mg 1.8 0.5 Copper, mcg 820 205 Iodine, mcg 131 33 Molybdenum, mcg 37 9 Chromium, mcg 26 7 Selenium, mcg 58 15 Sodium, mg (mEq) 560 (24.3) 140 (6.1) Potassium, mg (mEq) 700 (17.9) 175 (4.5) Chloride, mg (mEq) 560 (16) 140 (4) Ingredients: Sugar, L-Lysine L-Glutamate, Corn Syrup Solids, L-Leucine, Calcium Phosphate Dibasic, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, L-Threonine, Artificial Flavour, L-Phenylalanine, L-Tyrosine, L-Serine, Citric Acid, Magnesium Acetate, L-Alanine, L-Histidine, Tripotassium Citrate, L-Cystine, Choline Bitartrate, L-Tryptophan, Sodium Chloride, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, L-Glutamic Acid, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XMet Maxamum Nutrition Information: XMet Maxamum® 115 HCU Lophlex LQ Metabolics A methionine-free*, ready-to-drink formula containing amino acids, carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) with natural flavour; for the dietary management of proven homocystinuria in individuals 4 years and older, including pregnant women and women of child-bearing age. 116 Main Features: Indications: • Methionine-free • Low volume; provides 20 g PE in just 125 mL (4.2 fl oz) • Convenient ready-to-drink • Based on fruit juices (from concentrate) with natural flavour - no artificial flavours • Contains a balanced mixture of other essential and non-essential amino acids, carbohydrates, vitamins, minerals and DHA • Contains 150 mg of DHA per pouch • Available in mixed berry blast flavour • Osmolality: 2460 mOsm/kg • Homocystinuria For details on administration, please see page 146-161. Ordering Information: Product Code 82111 *May contain traces of methionine from fruit juice (from concentrate). Product Packaging 30 X 4.2 fl oz (125 mL) Calories Per Pouch 120 Per Pouch Per 10 g Per Pouch Per 10 g Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Calories 120.060.0 Vitamin A, IU (mcg R.E.) 949 (285) 475 (143) Protein Equivalent, g 20.0 10.0 Vitamin D, IU (mcg) 320 (8.0) 160 (4.0) Fat, g 0.44 0.22 Vitamin E, IU (mg α T.E.) 4.8 (3.2) 2.4 (1.6) DHA, mg 150 75.0 Vitamin K, mcg 24.9 12.5 Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 Amino Acids, g Vitamin B6, mg 0.58 0.29 L-Alanine 1.180.59 Vitamin B12, mcg 1.8 0.90 L-Arginine 1.500.75 Niacin, mg 7.1 3.6 L-Aspartic Acid 1.73 0.87 Folic Acid, mcg 120 60.0 L-Cystine 0.980.49 Pantothenic Acid, mg 1.8 0.9 Glycine 1.600.80 Biotin, mcg 53.4 26.7 L-Histidine 0.850.43 Vitamin C, mg 17.8 8.9 L-Isoleucine 1.350.68 Choline, mg 153 76.5 L-Leucine 2.301.15 Inositol, mg 40.6 20.3 L-Lysine 1.550.78 Minerals L-Methionine TraceTrace Calcium, mg 319 160 L-Phenylalanine1.00 0.50 Phosphorus, mg 244 122 L-Proline 2.031.02 Magnesium, mg 96.3 48.2 L-Serine 1.380.69 Iron, mg 5.1 2.6 L-Threonine 1.130.57 Zinc, mg 3.8 1.9 L-Tryptophan 0.450.23 Manganese, mg 0.56 0.28 L-Tyrosine 1.650.83 Copper, mcg 563 282 L-Valine 1.450.73 Iodine, mcg 56.3 28.2 L-Carnitine 0.010.01 Molybdenum, mcg 25.0 12.5 Taurine 0.060.03 Chromium, mcg 10.8 5.4 Selenium, mcg 26.8 13.4 Sodium, mg (mmol) <25.0 (<10) <12.5 (<5) Potassium, mg (mmol) 90 (2.3) 45 (1.2) Chloride, mg (mmol) <25.0 (<10) <12.5 (<5) Ingredients: Water, Apple Juice from Concentrate (34.1%), Grape Juice from Concentrate (6.9%), Blackcurrant Juice from Concentrate (2.5%), L-Arginine L-Aspartate, L-Leucine, L-Lysine Acetate, Citric Acid, L-Proline, L-Tyrosine, Glycine, L-Valine, L-Serine, L-Isoleucine, Corn Syrup Solids, Dicalcium Phosphate, L-Alanine, L-Threonine, L-Phenylalanine, L-Cystine, L-Histidine, Elderberry Juice from Concentrate (0.6%), Maltodextrin, Magnesium L-Aspartate, Magnesium Acetate, L-Tryptophan, Choline Bitartrate, C. Cohnii Oil*, Sugar, Microcrystalline Cellulose, Natural Flavour, Fruit Concentrate (Apple, Blackcurrant, Radish), L-Ascorbic Acid, Taurine, Guar Gum, Sunflower Lecithin, Xanthan Gum, M-Inositol, Potassium Sorbate (preservative to delay spoilage), Artificial Sweetener: Sucralose, Artificial Sweetener: Acesulfame Potassium, Ferrous Lactate, Sodium Benzoate (preservative to delay spoilage), Zinc Sulfate, L-Carnitine, Niacinamide, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Riboflavin, Folic Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. HCU Lophlex LQ Nutrition Information: ® *A Source of Docosahexaenoic Acid (DHA). Contains 44.1% juice. 117 Metabolics A methionine-free powdered formula for the dietary management of vitamin B6 nonresponsive homocystinuria or hypermethioninemia in individuals over 1 year of age. 118 Main Features: Indications: • Methionine-free • Contains a mixture of the other essential and non-essential amino acids, carbohydrate, and select vitamins, minerals and trace elements • Unflavoured powder • Methionaid provides 60 g of protein equivalent per 100 g of powder • Does not contain fat thereby allowing for greater flexibility in modifying energy intake • Vitamin B6 non-responsive homocystinuria • Hypermethioninemia For general guidance on administration, please follow instructions for Maxamaid or Maxamum brands on page 131. Ordering Information: Product Code 10242 Product Packaging 10 x 200 g (7 oz) Calories Per Can 500 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 25042 Protein Equivalent, g 60 10 Fat, g 0 0 Carbohydrate, g 3 0.5 Amino Acids, g L-Alanine 5.60.93 L-Arginine 4.40.73 L-Aspartic Acid 9.5 1.58 L-Cystine 3.70.62 L-Glutamic Acid 11 1.83 Glycine 4.30.72 L-Histidine 2.80.47 L-Isoleucine 2.40.40 L-Leucine 3.10.52 L-Lysine 6.01.00 L-Methionine Nil Added Nil Added L-Phenylalanine4.30.72 L-Proline 1.60.27 L-Serine 1.70.28 L-Threonine 3.20.53 L-Tryptophan 0.90.15 L-Tyrosine 4.30.72 L-Valine 3.20.53 Per 10 g Vitamins Per 100 g Protein Equivalent Thiamine, mg 2 0.3 Riboflavin, mg 2.5 0.4 2.0 0.3 Vitamin B6, mg 20 3.3 Vitamin B12, mcg Niacin, mg 25 4.2 Folic Acid, mcg 400 67 Pantothenic Acid, mcg 20 3.3 Biotin, mcg 600 100 Minerals Calcium, mg 2500 417 Phosphorus, mg 1500 250 Magnesium, mg 300 50 Iron, mg 25 4.2 Zinc, mg 15 2.5 Manganese, mg 3.5 0.58 Copper, mcg 2500 417 Iodine, mcg 150 25 Sodium, mg (mEq) 1400 (60.9) 233 (10.2) Potassium, mg (mEq) 2600 (66.7) 433 (11.1) Chloride, mg (mEq) 2800 (80) 467 (13.3) Ingredients: L-Lysine L-Glutamate, L-Aspartic Acid, Tripotassium Citrate, L-Alanine, Calcium Phosphate Dibasic, L-Glutamic Acid, L-Arginine, Glycine, L-Phenylalanine, L-Tyrosine, Sodium Chloride, L-Cystine, Calcium Phosphate Tribasic, Hydrolyzed Cornstarch, L-Leucine,, L-Valine, L-Threonine, L-Histidine, L-Isoleucine, Magnesium Acetate, L-Serine, L-Proline, L-Tryptophan, Potassium Chloride, Calcium Chloride, Ferrous Sulfate, Zinc Sulfate, Niacinamide, Calcium-DPantothenate, Manganese Sulfate, Cupric Sulfate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Hydrochloride, Biotin, Folic Acid, Potassium Iodide, Cyanocobalamin. Methionaid Nutrition Information: Methionaid 119 Metabolics A methionine-, threonine-, valine-free and isoleucine-low powdered infant formula for the dietary management of vitamin B12 nonresponsive methylmalonic acidemia or propionic acidemia. 120 Main Features: Indications: • Methionine-, threonine-, valine-free and isoleucine-low • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • XMTVI Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Vitamin B12 non-responsive methylmalonic acidemia • Propionic acidemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118303 Product Packaging 6 x 400 g (14 oz) Calories Per Can 1900 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 475 365 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 6.8 5.2 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 Linoleic Acid, mg 3025 2330 Carbohydrate, g 59 45 Amino Acids, g L-Alanine1.48 1.14 L-Arginine1.33 1.02 L-Aspartic Acid 1.17 0.90 L-Cystine0.49 0.38 L-Glutamic Acid 1.47 1.13 Glycine0.59 0.45 L-Histidine0.9 0.69 L-IsoleucineTrace Trace L-Leucine2.00 1.54 L-Lysine1.36 1.05 L-Methionine Nil Added Nil Added L-Phenylalanine0.88 0.68 L-Proline0.59 0.45 L-Serine0.83 0.64 L-Threonine Nil Added Nil Added L-Tryptophan0.39 0.30 L-Tyrosine0.88 0.68 L-Valine Nil Added Nil Added L-Carnitine0.01 0.01 Taurine0.02 0.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g P rotein Equivalent 1359 (406) Vitamin A, IU (mcg R.E.) 1760 (528) 262 (6.5) Vitamin D, IU (mcg) 340 (8.5) 3.8 (2.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 16 Vitamin K, mcg 21 385 Thiamin, mcg 500 462 Riboflavin, mcg 600 400 520 Vitamin B6, mcg 1.25 0.96 Vitamin B12, mcg 3462 Niacin, mcg 4500 29 Folic Acid, mcg 38 2000 Pantothenic Acid, mcg 2600 20 Biotin, mcg 26 31 Vitamin C, mg 40 38 Choline, mg 50 77 Inositol, mg 100 Minerals 462 Calcium, mg 600 385 Phosphorus, mg 500 31 Magnesium, mg 40 8 Iron, mg 10 6 Zinc, mg 8 462 Manganese, mcg 600 346 Copper, mcg 450 36 Iodine, mcg 47 12 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 92 (4.0) Sodium, mg (mEq) 120 (5.2) 323 (8.3) Potassium, mg (mEq) 420 (10.8) 223 (6.3) Chloride, mg (mEq) 290 (8.2) Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, L-Leucine, Calcium Phosphate Dibasic, L-Alanine, L-Arginine, L-Aspartic Acid, Galactose , L-Histidine, L-Phenylalanine, L-Tyrosine, Tripotassium Citrate, L-Serine, Calcium Phosphate Monobasic, Glycine, L-Proline, Mono and Diglycerides, L-Cystine, L-Tryptophan, Sodium Chloride, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, L-Glutamic Acid, Soy Lecithin, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. XMTVI Analog Nutrition Information: XMTVI Analog™ 121 Metabolics A methionine-, threonine-, valine-free, low isoleucine, mildly-flavoured powdered formula for the dietary management of methylmalonic acidemia and propionic acidemia in individuals over 1 year of age. 122 Main Features: Indications: • Methionine-, threonine-, valine-free • Low isoleucine • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate (including a multi-fiber blend), fat (including DHA), vitamins, minerals, and trace elements • Provides 28 g protein equivalent and 12.5 g fat per 100 g of powder • Available in Plain • Displacement: 0.72 mL/g • Methylmalonic Acidemia • Propionic Acidemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 89472 Product Packaging 6 x 400 g Calories Per Can 1508 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 377 135 Protein Equivalent, g 28 10 Fat, g 12.5 4.5 DHA, mg 180 64 Carbohydrate, g 41.2 14.8 Fiber, g 11.2 4 of which Soluble, g 8 2.9 of which Insoluble, g 3.2 1.1 Amino Acids, g L-Alanine 3.421.22 L-Arginine 3.01.07 L-Aspartic Acid 2.72 0.97 L-Cystine 1.560.56 L-Glutamine 3.611.29 Glycine 1.370.49 L-Histidine 2.020.72 L-Isoleucine <0.03<0.03 L-Leucine 4.541.62 L-Lysine 3.051.09 L-Methionine Nil Added Nil Added L-Phenylalanine 1.990.71 L-Proline 1.370.49 L-Serine 1.980.71 L-Threonine Nil Added Nil Added L-Tryptophan 0.690.25 L-Tyrosine 1.990.71 L-Valine Nil Added Nil Added L-Carnitine 0.020.01 Taurine 0.060.02 Per 10 g Vitamins Per 100 g Protein Equivalent Vit A, IU (mcg RE) 1748.(525)628.(189) Vit D, IU (mcg) 1052.(26.3)379.(9.6) Vit E, IU (mg-α-TE) 15.6 (10.5) 5.6 (3.8) Vit K, mcg 17.5 6.4 Thiamin, mg 1.2 0.4 Riboflavin, mg 0.91 0.32 0.91 0.32 Vit B6, mg 1.6 0.56 Vit B12, mcg Niacin, mg 2.5 0.90 Folic Acid, mcg 263 94.8 Pantothenic Acid, mg 5.3 1.92 Biotin, mcg 14 5.2 Vit C, mg 52.5 18.8 Choline, mg 280 100 Inositol, mg 70 25.2 Minerals Calcium, mg 1225 440 Phosphorus, mg 801 288 Magnesium, mg 140 50.4 Iron, mg 12.5 4.4 Zinc, mg 6.1 2.2 Manganese, mg 1.2 0.44 Copper, mcg 700 252 Iodine, mcg 174 62.8 Molybdenum, mcg 31.9 11.4 Chromium, mcg 12.8 4.8 Selenium, mcg 35.3 12.8 Sodium, mg 350 126 Potassium, mg 556 200 Chloride, mg 508 183 Ingredients: Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Chain Triglycerides (Palm Kernel and/ or Coconut Oil), Sunflower), L-Leucine, L-Lysine Acetate, L-Glutamine, Fructooligosaccharides, L-Alanine, Inulin, Calcium Phosphate Dibasic, L-Arginine, Corn Starch, L-Aspartic Acid, Microcrystalline Cellulose, Artificial Flavour, L-Histidine, L-Tyrosine, L-Phenylalanine, L-Serine, Gum Arabic, Tripotassium Citrate, Trisodium Citrate, L-Cystine, Glycine, L-Proline, Calcium Chloride, Magnesium Hydrogen Phosphate, Maltodextrin, Choline Bitartrate, L-Tryptophan, Tricalcium Citrate, CAEM (an emulsifier), C. Cohnii Oil**, L-Ascorbic Acid, M-Inositol, Soy Fiber, Taurine, Ferrous Sulfate, Sunflower Lecithin, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Ascorbyl Palmitate, Potassium iodide, Mixed Tocopherols, Sodium Molybdate, Sodium Selenite, Chromium Chloride, DL-alpha Tocopherol, Vitamin D3, Phylloquinone, D-Biotin, Cyanocobalamin MMA/PA Anamix Next Nutrition Information: MMA/PA Anamix® Next **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) 123 Metabolics A methionine-, threonine-, valine-free and isoleucine-low powdered formula for the dietary management of vitamin B12 non-responsive methylmalonic acidemia or propionic acidemia in toddlers and young children. 124 Main Features: Indications: • Methionine-, threonine-, valine-free and isoleucine-low • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XMTVI Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.70 mL/g • Vitamin B12 non-responsive methylmalonic acidemia • Propionic acidemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117785 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine2.89 1.16 L-Arginine2.59 1.04 L-Aspartic Acid 2.3 0.92 L-Cystine0.95 0.38 Glycine1.16 0.46 L-Histidine1.75 0.70 L-Isoleucine<0.07 Trace L-Leucine3.9 1.56 L-Lysine2.65 1.06 L-Methionine Nil Added Nil Added L-Phenylalanine1.72 0.69 L-Proline1.16 0.46 L-Serine1.62 0.65 L-Threonine Nil Added Nil Added L-Tryptophan0.76 0.30 L-Tyrosine1.72 0.69 L-Valine Nil Added Nil Added L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g P rotein Equivalent Vitamin A, IU (mcg R.E.)1665 (500) 666 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) 232 (10) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Ingredients: Sugar, Corn Syrup Solids, L-Arginine L-Aspartate, L-Leucine, L-Lysine Acetate, Calcium Phosphate Dibasic, Citric Acid, L-Alanine, Tripotassium Citrate, Artificial Flavours, L-Histidine, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Serine, Glycine, L-Proline, Maltodextrin, Disodium Hydrogen Phosphate, L-Cystine, Sodium Chloride, L-Tryptophan, Choline Bitartrate, Magnesium Acetate, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XMTVI Maxamaid Nutrition Information: XMTVI Maxamaid® 125 Metabolics A methionine-, threonine-, valine-free and isoleucine-low formula for the dietary management of vitamin B12 non-responsive methylmalonic acidemia or propionic acidemia in older children and adults, including pregnant women and women of child-bearing age. 126 Main Features: Indications: • Methionine-, threonine-, valine-free and isoleucine-low • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XMTVI Maxamum provides 40 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Vitamin B12 non-responsive methylmalonic acidemia • Propionic acidemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117779 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1385 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 305 76 Protein Equivalent, g 40 10 Fat, g <1 <0.25 Carbohydrate, g 34 8.5 Amino Acids, g L-Alanine4.6 1.15 L-Arginine4.1 1.03 L-Aspartic Acid 3.6 0.90 L-Cystine1.5 0.38 L-Glutamic Acid 4.5 1.13 Glycine1.8 0.45 L-Histidine2.8 0.70 L-Isoleucine<0.14 Trace L-Leucine6.2 1.55 L-Lysine4.2 1.05 L-Methionine Nil Added Nil Added L-Phenylalanine2.7 0.68 L-Proline1.9 0.48 L-Serine2.6 0.65 L-Threonine Nil Added Nil Added L-Tryptophan1.2 0.30 L-Tyrosine2.7 0.68 L-Valine Nil Added Nil Added L-Carnitine0.039 0.01 Taurine0.14 0.04 L-Glutamine0.32 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent 557 (167) Vitamin A, IU (mcg R.E.)2228 (669) 83 (2.1) Vitamin D, IU (mcg) 332 (8.3) 4.6 (3.1) Vitamin E, IU (mg α T.E.) 18.3 (12.3) 21 Vitamin K, mcg 82 Thiamin, mg 0.91 0.23 Riboflavin, mg 0.97 0.24 1.6 0.4 Vitamin B6, mg 3.1 0.8 Vitamin B12, mcg Niacin, mg 5.7 1.4 123 Folic Acid, mcg 491 Pantothenic Acid, mg 4.9 1.2 Biotin, mcg 24.5 6.1 16 Vitamin C, mg 62 108 Choline, mg 430 20 Inositol, mg 80 Minerals 296 Calcium, mg 1183 284 Phosphorus, mg 1137 77 Magnesium, mg 306 Iron, mg 14.7 3.7 2 Zinc, mg 9 Manganese, mg 1.8 0.5 205 Copper, mcg 820 33 Iodine, mcg 131 9 Molybdenum, mcg 37 7 Chromium, mcg 26 15 Selenium, mcg 58 140 (6.1) Sodium, mg (mEq) 560 (24.3) 175 (4.5) Potassium, mg (mEq) 700 (17.9) 140 (4) Chloride, mg (mEq) 560 (16) Ingredients: Sugar, L-Lysine L-Glutamate, L-Leucine, Corn Syrup Solids, L-Alanine, Calcium Phosphate Dibasic, L-Arginine, L-Aspartic Acid, L-Histidine, L-Phenylalanine, L-Tyrosine, L-Serine, Artificial Flavour, Citric Acid, Magnesium Acetate, Glycine, L-Proline, L-Cystine, L-Tryptophan, Tripotassium Citrate, Choline Bitartrate, Sodium Chloride, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, L-Glutamic Acid, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamin Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XMTVI Maxamum Nutrition Information: XMTVI Maxamum® 127 XPhe, XTyr Analog Metabolics A phenylalanine- and tyrosine-free powdered infant formula for the dietary management of tyrosinemia when plasma methionine level is normal. 128 Main Features: Indications: • Phenylalanine- and tyrosine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium) • XPhe, XTyr Analog provides 13 g of protein equivalent per 100 g of powder • Osmolality (at 15% w/v): 377 mOsm/kg • Displacement: 0.70 mL/g • Tyrosinemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 118301 Product Packaging 6 x 400 g (14 oz) Calories Per Can 1900 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 475 365 Protein Equivalent, g 13 10 Fat, g 20.9 16 Saturated, g 6.8 5.2 Monounsaturated, g 9.5 7.3 Polyunsaturated, g 3.6 2.8 Linoleic Acid, mg 3025 2330 Carbohydrate, g 59 45 Amino Acids, g L-Alanine0.63 0.48 L-Arginine1.13 0.87 L-Aspartic Acid 0.93 0.72 L-Cystine0.42 0.32 L-Glutamic Acid 1.26 0.97 Glycine0.96 0.74 L-Histidine0.65 0.50 L-Isoleucine1.00 0.77 L-Leucine1.72 1.32 L-Lysine1.17 0.90 L-Methionine0.27 0.21 L-Phenylalanine Nil Added Nil Added L-Proline1.21 0.93 L-Serine0.74 0.57 L-Threonine0.84 0.65 L-Tryptophan0.34 0.26 L-Tyrosine Nil Added Nil Added L-Valine1.1 0.85 L-Carnitine0.01 0.01 Taurine0.02 0.02 L-Glutamine0.1 0.08 Per 10 g Vitamins Per 100 g Protein Equivalent 1361 (406) Vitamin A, IU (mcg R.E.) 1760 (528) 262 (6.5) Vitamin D, IU (mcg) 340 (8.5) 3.8 (2.5) Vitamin E, IU (mg α T.E.) 4.9 (3.3) 16 Vitamin K, mcg 21 385 Thiamin, mcg 500 462 Riboflavin, mcg 600 400 520 Vitamin B6, mcg 1.25 0.96 Vitamin B12, mcg 3462 Niacin, mcg 4500 29 Folic Acid, mcg 38 2000 Pantothenic Acid, mcg 2600 20 Biotin, mcg 26 31 Vitamin C, mg 40 38 Choline, mg 50 77 Inositol, mg 100 Minerals 462 Calcium, mg 600 385 Phosphorus, mg 500 31 Magnesium, mg 40 8 Iron, mg 10 6 Zinc, mg 8 462 Manganese, mcg 600 346 Copper, mcg 450 36 Iodine, mcg 47 12 Molybdenum, mcg 15 12 Chromium, mcg 15 12 Selenium, mcg 15 92 (4.0) Sodium, mg (mEq) 120 (5.2) 323 (8.3) Potassium, mg (mEq) 420 (10.8) 223 (6.3) Chloride, mg (mEq) 290 (8.2) Ingredients: Corn Syrup Solids, High Oleic Safflower Oil, Refined Vegetable Oil (Coconut, Soy), L-Lysine L-Glutamate, Calcium Phosphate Dibasic, L-Leucine, L-Proline, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, Galactose, L-Threonine, Tripotassium Citrate, L-Serine, Calcium Phosphate Monobasic, L-Alanine, L-Histidine, Mono and Diglycerides, L-Cystine, L-Tryptophan, Sodium Chloride, L-Methionine, Magnesium Acetate, Potassium Chloride, Diacetyl Tartaric Acid Esters of Monoglycerides, Tricalcium Citrate, L-Glutamine, Choline Bitartrate, M-Inositol, L-Ascorbic Acid, Soy Lecithin, L-Glutamic Acid, Calcium Phosphate Tribasic, Ferrous Sulfate, Zinc Sulfate, Taurine, L-Carnitine, Nicotinamide, DL-Alpha Tocopheryl Acetate, Calcium Pantothenate, Manganese Sulfate, Cupric Sulfate, Vitamin A Acetate, Pyridoxine Hydrochloride, Riboflavin, Thiamin Chloride Hydrochloride, Chromium Sulfate, Potassium Iodide, Folic Acid, Sodium Molybdate, Phylloquinone, Biotin, Sodium Hydrogen Selenite, Vitamin D3, Cyanocobalamin. XPhe, XTyr Analog Nutrition Information: ™ 129 TYR Anamix Next ® Metabolics A phenylalanine- and tyrosine-free mildly-flavoured powdered formula for the dietary management of tyrosinemia in individuals over 1 year of age. 130 Main Features: Indications: • Phenylalanine- and tyrosine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate (including a multi-fiber blend), fat (including DHA), vitamins, minerals and trace elements • Provides 28 g protein equivalent and 12.5 g fat per 100 g of powder • Available in Plain • Osmolality (mOsm/kg): 1460 (at 1 kcal/mL) • Displacement: 0.72 mL/g • Tyrosinemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 89479 Product Packaging 6 x 400 g (14 oz) Calories Per Can 1540 Per 10 g Protein Equivalent Nutrients Per 100 g Calories 385138 Protein Equivalent, g 28 10 Fat, g 12.5 4.5 Saturates, g 2 0.71 Monounsaturates, g 8.2 2.9 Polyunsaturates, g 1.8 0.64 DHA, mg 180 64.3 Carbohydrate, g 43.2 15.4 Of which Fiber, g 11.2 4 Soluble 8 2.9 Insoluble 3.2 1.1 Amino Acids, g L-Alanine 4.711.7 L-Arginine 1.670.6 L-Aspartic Acid 0.41 0.15 L-Cystine 2.710.97 L-Glutamine3.361.2 Glycine 3.941.4 L-Histidine 0.790.28 L-Isoleucine 1.660.59 L-Leucine 2.520.9 L-Lysine 2.240.8 L-Methionine0.56 0.2 L-Phenylalanine Nil Added Nil Added L-Proline 2.710.97 L-Serine 1.590.57 L-Threonine2.941.1 L-Tryptophan0.56 0.2 L-Tyrosine Nil Added Nil Added L-Valine 1.960.7 L-Carnitine 0.020.01 Taurine 0.050.02 Per 10 g Protein Equivalent Vitamins Per 100 g Vitamin A, IU (mcg RE) 1399.(420)499.(150) Vitamin D, IU (mcg) 840.(21)300.(7.5) Vitamin E, IU (mg α-TE) 12.5 (8.4) 4.5 (3) Vitamin K, mcg 14 5 Thiamin, mg 0.93 0.33 Riboflavin, mg 0.73 0.26 Vit. B6, mg 0.73 0.26 Vit. B12, mcg 1.3 0.46 Niacin, mg 2.0 0.71 Folic Acid, mg 0.21 0.08 Pantothenic Acid, mg 4.2 1.5 Biotin, mcg 11.2 4 Vitamin C, mg 42 15 Choline, mg 224 80 Inositol, mg 56 20 Minerals Calcium, mg 980 350 Phosphorus, mg 641 229 Magnesium, mg 113 40 Iron, mg 10 4 Zinc, mg 4.9 1.8 Manganese, mcg 920 329 Copper, mcg 560 200 Iodine, mcg 139 50 Molybdenum, mcg 25.5 9.1 Chromium, mcg 10.2 3.6 Selenium, mcg 28.2 10.1 Sodium, mg 280 100 Potassium, mg 445 159 Chloride, mg 406 145 Ingredients: Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Canola, Medium Chain Triglycerides (Palm Kernel and/or Coconut Oil), Sunflower), L-Alanine, Glycine, Fructo-oligosaccharides, L-Glutamine, L-Lysine Acetate, ]Inulin, L-Threonine, Corn Starch, L-Cystine, L-Proline, Calcium Phosphate Dibasic, L-Leucine, Microcrystalline Cellulose, Artificial Flavour, L-Valine, Gum Arabic, L-Arginine, L-Isoleucine, L-Serine, Tripotassium Citrate, Trisodium Citrate, Calcium Chloride, L-Histidine, Maltodextrin, Choline Bitartrate, Magnesium Hydrogen Phosphate, L-Methionine, L-Tryptophan, Magnesium L-Aspartate, CAEM (an emulsifier), C. Cohnii Oil**, Tricalcium Citrate, L-Ascorbic Acid, Soy Fiber, M-Inositol, Taurine, Ferrous Sulfate, Sunflower Lecithin, L-Carnitine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Niacinamide, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Ascorbyl Palmitate, Folic Acid, Potassium Iodide, Mixed Tocopherols, Sodium Molybdate, Sodium Selenite, Chromium Chloride, DL-alpha Tocopherol, Vitamin D3, Phylloquinone, D-Biotin, Cyanocobalamin TYR Anamix Next Nutrition Information: **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) 131 Metabolics A phenylalanine- and tyrosine-free flavoured powdered formula for the dietary management of tyrosinemia in toddlers and young children. 132 Main Features: Indications: • Phenylalanine- and tyrosine-free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • Age-appropriate DRI formulation • XPhe, XTyr Maxamaid provides 25 g of protein equivalent per 100 g of powder • Available in orange flavour • Contains <1 g of fat per 10 g PE thereby allowing greater flexibility in modifying energy intake • Displacement: 0.60 mL/g • Tyrosinemia For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 117786 Product Packaging 6 x 454 g (1 lb) Calories Per Can 1471 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 324 130 Protein Equivalent, g 25 10 Fat, g <0.1 0.04 Carbohydrate, g 56 22 Amino Acids, g L-Alanine1.25 0.50 L-Arginine2.21 0.88 L-Aspartic Acid 1.84 0.74 L-Cystine0.82 0.33 Glycine1.96 0.78 L-Histidine1.26 0.50 L-Isoleucine1.96 0.78 L-Leucine3.36 1.34 L- Lysine 2.28 0.91 L-Methionine0.54 0.22 L-Phenylalanine Nil Added Nil Added L-Proline2.38 0.95 L-Serine1.46 0.58 L-Threonine1.64 0.66 L-Tryptophan0.66 0.26 L-Tyrosine Nil Added Nil Added L-Valine2.14 0.86 L-Carnitine0.02 0.01 Taurine0.14 0.06 L-Glutamine1.5 0.60 Per 10 g Vitamins Per 100 g P rotein Equivalent Vitamin A, IU (mcg R.E.) 1665 (500) 666 (200) Vitamin D, IU (mcg) 480 (12) 192 (4.8) Vitamin E, IU (mg α T.E.) 14.3 (9.6) 5.7 (3.8) Vitamin K, mcg 48 19 Thiamin, mg 0.8 0.3 Riboflavin, mg 0.8 0.3 0.8 0.3 Vitamin B6, mg 2 Vitamin B12, mcg 0.8 Niacin, mg 5 2 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.2 1.3 Biotin, mcg 18 7.2 Vitamin C, mg 62.5 25 Choline, mg 250 100 Inositol, mg 56 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 128 51 Iron, mg 14 5.6 Zinc, mg 11 4.4 Manganese, mg 1.9 0.8 Copper, mcg 1000 400 Iodine, mcg 144 58 Molybdenum, mcg 33 13 Chromium, mcg 21.5 8.6 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) 232 (10) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.9) 180 (5.2) Ingredients: Sugar, Corn Syrup Solids, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, L-Leucine, L-Lysine Acetate, Citric Acid, Tripotassium Citrate, L-Proline, L-Valine, Artificial Flavours, Gylcine, L-Isoleucine, L-Threonine, L-Glutamine, L-Serine, L-Alanine, L-Histidine, Maltodextrin, Disodium Hydrogen Phosphate, L-Cystine, Sodium Chloride, Magnesium Acetate, N-Acetyl L-Methionine, Choline Bitartrate, L-Tryptophan, Taurine, Magnesium L-Aspartate, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. XPhe, XTyr Maxamaid Nutrition Information: XPhe, XTyr Maxamaid® 133 Metabolics An unflavoured, phenylalanine- and tyrosine-free powdered formula for the dietary management of tyrosinemia in toddlers and young children. 134 Main Features: Indications: • Phenylalanine- and tyrosine- free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • XPHEN, TYR Maxamaid provides 25 g of protein equivalent per 100 g of powder • Does not contain fat thereby allowing greater flexibility in modifying energy intake • Osmolality (mOsm/kg): Dilution 1 to 5 690 1 to 7 490 • Tyrosinemia For details on administration and household measurements, please see pages 126-137. Ordering Information: Product Code 116189 Product Packaging 3 x 500 g (17.6 oz) Calories Per Can 1545 Per 10 g Nutrients Per 100 g Protein Equivalent Calories309 124 Protein Equivalent, g 25 10 Fat, g <0.5 0.04 Carbohydrate, g 51 20 Amino Acids, g L-Alanine1.32 0.53 L-Arginine2.31 0.92 L-Aspartic Acid 1.93 0.77 L-Cystine0.86 0.34 L-Glutamic Acid 2.59 1.04 Glycine 2.06 0.82 L-Histidine1.32 0.53 L-Isoleucine2.06 0.82 L-Leucine3.53 1.41 L-Lysine2.40 0.96 L-Methionine0.56 0.22 L-Phenylalanine Nil Added Nil Added L-Proline2.50 1.00 L-Serine1.54 0.62 L-Threonine1.73 0.69 L-Tryptophan0.69 0.28 L-Tyrosine Nil Added Nil Added L-Valine2.25 0.90 L-Carnitine0.02 0.01 Taurine0.1 0.04 L-Glutamine0.33 0.13 Per 10 g P rotein Equivalent Vitamins Per 100 g 699 (210) Vitamin A, IU (mcg R.E.) 1748 (525) 192 (4.8) Vitamin D, IU (mcg) 480 (12) 2.6 (1.7) Vitamin E, IU (mg a T.E.) 6.5 (4.35) 12 Vitamin K, mcg 30 Thiamine, mg 1.08 0.4 Riboflavin, mg 1.2 0.5 1.4 0.6 Vitamin B6, mg 3.9 1.56 Vitamin B12, mcg Niacin, mg 12 4.8 Folic Acid, mcg 240 96 Pantothenic Acid, mg 3.7 1.5 Biotin, mcg 120 48 Vitamin C, mg 135 54 Choline, mg 110 44 Inositol, mg 55.5 22 Minerals Calcium, mg 810 324 Phosphorus, mg 810 324 Magnesium, mg 200 80 Iron, mg 12 4.8 Zinc, mg 13 5.2 Manganese, mg 1.6 0.6 Copper, mcg 1800 720 Iodine, mcg 100 40 Molybdenum, mcg 100 40 Chromium, mcg 40 16 Selenium, mcg 40 16 Sodium, mg (mEq) 580 (25.2) 232 (10) Potassium, mg (mEq) 840 (21.5) 336 (8.6) Chloride, mg (mEq) 450 (12.7) 180 (5.1) Ingredients: Dried Glucose Syrup, L-Lysine L-Glutamate, L-Leucine, Calcium Phosphate Dibasic, L-Proline, Trisodium Citrate, L-Arginine, L-Valine, Glycine, L-Isoleucine, L-Aspartic Acid, L-Threonine, L-Serine, Magnesium Hydrogen Phosphate, L-Alanine, L-Histidine, Tripotassium Citrate, Potassium Chloride, L-Cystine, Soy Lecithine, L-Tryptophan, L-Methionine, Sugar, L-Glutamine, Choline Bitartrate, L-Glutamic Acid, Ascorbic Acid, Taurine, Tricalcium Phosphate, Ferrous Sulphate, M-Inositol, Zinc Sulphate, L-Carnitine, Nicotinamide, Copper Sulphate, Manganese Sulphate, DL-Alpha Tocopheryl Acetate, Calcium D-Pantothenate, Pyridoxine Hydrochloride, Thiamine Hydrochloride, Riboflavin, Vitamin A Acetate, Chromium Sulphate, Folic Acid, Sodium Molybdate, Potassium Iodide, D-Biotin, Sodium Hydrogen Selenite, Vitamin K1, Vitamin D3, Cyanocobalamine. XPHEN, TYR Maxamaid Nutrition Information: XPHEN, TYR Maxamaid 135 Metabolics An unflavoured phenylalanine- and tyrosine-free powdered formula for the dietary management of tyrosinemia in older children and adults, including pregnant women and women of child-bearing age. 136 Main Features: Indications: • Phenylalanine- and tyrosine- free • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements • XPHEN, TYR Maxamum provides 39 g of protein equivalent per 100 g of powder • Does not contain fat thereby allowing greater flexibility in modifying energy intake • Osmolality (mOsm/kg): Dilution 1 to 5 1000 1 to 7 690 • Tyrosinemia For details on administration and household measurements, please see pages 126-137. Ordering Information: Product Code 116196 Product Packaging 3 x 500 g (17.6 oz) Calories Per Can 1485 Per 10 g Nutrients Per 100 g Protein Equivalent Calories 297 76 Protein Equivalent, g 39 10 Fat, g <0.5 <0.25 Carbohydrate, g 34 8.7 Amino Acids, g L-Alanine1.9 0.49 L-Arginine3.5 0.90 L-Aspartic Acid 3.3 0.85 L-Cystine1.3 0.33 L-Glutamic Acid 5.3 1.36 Glycine3.3 0.85 L-Histidine2 0.51 L-Isoleucine3.1 0.79 L-Leucine5.3 1.36 L- Lysine 4 1.03 L-Methionine0.85 0.22 L-Phenylalanine Nil Added Nil Added L-Proline3.7 0.95 L-Serine2.3 0.59 L-Threonine2.6 0.67 L-Tryptophan1 0.26 L-Tyrosine Nil Added Nil Added L-Valine3.4 0.87 L-Carnitine0.02 0.01 Taurine0.15 0.04 L-Glutamine0.4 0.10 Per 10 g Vitamins Per 100 g Protein Equivalent 606 (182) Vitamin A, IU (mcg R.E.) 2364 (710) 80 (2.0) Vitamin D, IU (mcg) 312 (7.8) 2.0 (1.3) Vitamin E, IU (mg a T.E.) 7.7 (5.2) 18 Vitamin K, mcg 70 Thiamine, mg 1.4 0.36 Riboflavin, mg 1.4 0.36 2.1 0.5 Vitamin B6, mg 3.6 0.9 Vitamin B12, mcg Niacin, mg 13.6 3.5 128 Folic Acid, mcg 500 1.3 Pantothenic Acid, mg 5 35.9 Biotin, mcg 140 23 Vitamin C, mg 90 82 Choline, mg 321 Inositol, mg 85.7 22 Minerals 172 Calcium, mg 670 172 Phosphorus, mg 670 73 Magnesium, mg 285 Iron, mg 23.5 6.0 Zinc, mg 13.6 3 Manganese, mg 2.1 0.5 359 Copper, mcg 1400 27 Iodine, mcg 107 27 Molybdenum, mcg 107 13 Chromium, mcg 50 13 Selenium, mcg 50 144 (6.2) Sodium, mg (mEq) 560 (24.3) 179 (4.6) Potassium, mg (mEq) 700 (17.9) 144 (4.1) Chloride, mg (mEq) 560 (15.8) Ingredients: Dried Glucose Syrup, L-Lysine L-Glutamate, L-Leucine, L-Proline, L-Arginine, Calcium Glycerophosphate, L-Valine, Glycine, Aspartic Acid, L-Isoleucine, L-Threonine, L-Serine, L-Histidine, Tripotassium Citrate, L-Alanine, L-Cystine, Magnesium Hydrogen Phosphate, L-Glutamic Acid, L-Tryptophan, Sodium Chloride, L-Methionine, Trisodium Citrate, Sugar, Choline Bitartrate, Soy Lecithin, Magnesium Acetate, L-Glutamine, Taurine, Tricalcium Phosphate, Ferrous Sulphate, Ascorbic Acid, M-Inositol, Zinc Sulphate, L-Carnitine, Nicotinamide, Manganese Sulphate, DL-Alpha Tocopheryl, Calcium D-Pantothenate, Copper Sulphate, Pyridoxine Hydrochloride, Thiamine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Chromium Sulphate, Sodium Molybdate, Potassium Iodide, D-Biotin, Sodium Hydrogen Selenite, Vitamin K1, Vitamin D3, Cyanocobalamin. XPHEN, TYR Maxamum Nutrition Information: XPHEN, TYR Maxamum 137 TYR Lophlex LQ Metabolics A tyrosine- and phenylalanine-free*, ready-to-drink formula containing amino acids, carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) with natural flavour; for the dietary management of proven tyrosinemia in individuals 4 years and older, including pregnant women and women of child-bearing age. 138 Main Features: Indications: • Tyrosine- and phenylalanine-free • Low volume; provides 20 g PE in just 125 mL (4.2 fl oz) • Convenient ready-to-drink • Based on fruit juices (from concentrate) with natural flavour - no artificial flavours • Contains a balanced mixture of essential and non-essential amino acids, carbohydrates, vitamins, minerals and DHA • Provides 150 mg of DHA per pouch • Available in mixed berry blast flavour • Osmolality: 2460 mOsm/kg • Tyrosinemia For details on administration, please see page 146-161. Ordering Information: Product Code 82113 Product Packaging 30 X 4.2 fl oz (125 mL) *May contain traces of tyrosine and phenylalanine from fruit juice (from concentrate). Calories Per Pouch 120 Per Pouch Per Pouch Per 10 g Per Pouch Per 10 g Nutrients (4.2 fl oz) Protein Equivalent Vitamins (4.2 fl oz) Protein Equivalent Calories 12060.0 Vitamin A, IU (mcg R.E.) 949 (285) 475 (143) Protein Equivalent, g 20.0 10.0 Vitamin D, IU (mcg) 320 (8.0) 160 (4.0) Fat, g 0.44 0.22 Vitamin E, IU (mg α T.E.) 4.8 (3.2) 2.4 (1.6) DHA, mg 150 75.0 Vitamin K, mcg 24.9 12.5 Carbohydrate, g 9.3 4.7 Thiamin, mg 0.54 0.27 Fiber, g 0.50 0.25 Riboflavin, mg 0.50 0.25 Amino Acids, g Vitamin B6, mg 0.58 0.29 L-Alanine 1.130.57 Vitamin B12, mcg 1.8 0.90 L-Arginine 1.680.84 Niacin, mg 7.1 3.6 L-Aspartic Acid 1.63 0.82 Folic Acid, mcg 120 60.0 L-Cystine 0.830.42 Pantothenic Acid, mg 1.8 0.9 Glycine 1.630.82 Biotin, mcg 53.4 26.7 L-Histidine 0.950.48 Vitamin C, mg 17.8 8.9 L-Isoleucine 1.550.78 Choline, mg 153 76.5 L-Leucine 2.501.25 Inositol, mg 40.6 20.3 L-Lysine 1.750.88 Minerals L-Methionine 0.400.20 Calcium, mg 319 160 L-PhenylalanineTrace Trace Phosphorus, mg 244 122 L-Proline 2.031.02 Magnesium, mg 96.3 48.2 L-Serine 1.300.65 Iron, mg 5.1 2.6 L-Threonine 1.250.63 Zinc, mg 3.8 1.9 L-Tryptophan 0.500.25 Manganese, mg 0.56 0.28 L-Tyrosine Trace Trace Copper, mcg 563 282 L-Valine 1.650.83 Iodine, mcg 56.3 28.2 L-Carnitine 0.020.01 Molybdenum, mcg 25.0 12.5 Taurine 0.140.07 Chromium, mcg 10.8 5.4 Selenium, mcg 26.8 13.4 Sodium, mg (mmol) <25.0 (<10) <12.5 (<5) Potassium, mg (mmol) 90 (2.3) 45 (1.2) Chloride, mg (mmol) <25.0 (<10) <12.5 (<5) Ingredients: Water, Apple Juice from Concentrate (34.1%), Grape Juice from Concentrate (6.9%), Blackcurrant Juice from Concentrate (2.5%), L-Leucine, L-Lysine Acetate, Citric Acid, L-Proline, L-Arginine, L-Valine, L-Aspartic Acid, Glycine, L-Isoleucine, L-Serine, L-Threonine, Corn Syrup Solids, Dicalcium Phosphate, L-Alanine, L-Histidine, L-Cystine, Elderberry Juice from Concentrate (0.6%), Maltodextrin, Magnesium Acetate, Sugar, N-Acetyl L-Methionine, L-Tryptophan, Choline Bitartrate, C. Cohnii Oil*, Microcrystalline Cellulose, Natural Flavour, Taurine, Fruit Concentrate (Apple, Blackcurrant, Radish), L-Ascorbic Acid, Guar Gum, Sunflower Lecithin, Xanthan Gum, M-Inositol, Potassium Sorbate (preservative to delay spoilage), Artificial Sweetener: Sucralose, Ferrous Lactate, Artificial Sweetener: Acesulfame Potassium, L-Carnitine, Sodium Benzoate (preservative to delay spoilage), Zinc Sulfate, Niacinamide, DL-alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Riboflavin, Folic Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. TYR Lophlex LQ Nutrition Information: ® *A Source of Docosahexaenoic Acid (DHA). Contains 44.1% juice. 139 Metabolics A powdered formula containing essential amino acids (with increased levels of branched chain amino acids (BCAAs) and tryptophan), carbohydrates, fat, vitamins and minerals; for the dietary management of urea cycle disorders (UCD); hyperammonemia, hyperornithinemia, homocitrullinemia (HHH) syndrome; and gyrate atrophy in patients over 1 year of age. 140 Main Features: Indications: • Contains essential amino acids to help maintain a positive nitrogen balance in UCD • Amino acid profile rich in BCAAs for efficient and optimal protein synthesis for children with UCD • Sufficient non-protein calories to prevent protein being broken down for energy and toxic metabolites being produced • Essential micronutrients such as calcium, vitamin D, iron and zinc supplied to compensate for low intake from natural food • Available in unflavoured and vanilla flavour • Osmolality (at a 1 to 3.5 dilution): 1040 mOsm/kg • Displacement: 0.70 mL/g • Urea Cycle Disorders (UCD) • Hyperammonemia, Hyperornithinemia, Homocitrullinemia (HHH) syndrome • Gyrate atrophy For details on administration and household measurements, please see pages 146-161. Ordering Information: Product Code 59292 - Unflavoured 59293 - Vanilla Product Packaging 6 X 400 g (14 oz) 6 X 400 g (14 oz) Calories Per Can 1540 1540 Per 10 g Protein Nutrients Per 100 g Equivalent Calories 385321 Protein Equivalent, g 12.0 10.0 Fat, g 17.0 14.2 Carbohydrate, g 46.0 38.3 Amino Acids, g L-Alanine Nil Added Nil Added L-Arginine Nil Added Nil Added L-Asparagine Nil Added Nil Added L-Aspartic Acid Nil Added Nil Added L-Citrulline Nil Added Nil Added L-Cystine 0.430.36 L-Glutamic Acid Nil Added Nil Added L-Glutamine Nil Added Nil Added Glycine Nil Added Nil Added L-Histidine 0.510.43 L-Isoleucine 2.261.88 L-Leucine 3.823.18 L-Lysine 1.921.60 L-Methionine 0.400.33 L-Phenylalanine 0.670.56 L-Proline Nil Added Nil Added L-Serine Nil Added Nil Added L-Threonine 1.591.33 L-Tryptophan 0.480.40 L-Tyrosine 1.231.03 L-Valine 2.291.91 L-Carnitine 0.0090.008 Taurine 0.0690.058 Ingredients: Per 10 g Protein Unflavoured: Corn Syrup Solids, Refined Vitamins Per 100 g Equivalent Vegetable Oils (High Oleic Safflower, Canola, Fractionated Coconut), Sugar, L-Leucine, Vitamin A, IU (mcg R.E.) 3197 (960) 2664 (800) Sodium Phosphate Dibasic, Tripotassium Vitamin D, IU (mcg) 920 (23.0) 767 (19.2) Citrate, Tricalcium Citrate, Tricalcium Vitamin E, IU (mg α T.E.) 27.5 (18.5) 22.9 (15.4) Phosphate, L-Lysine Hydrochloride, L-Valine, Vitamin K, mcg 92.2 76.8 L-Isoleucine, Magnesium Hydrogen Thiamin, mg 1.9 1.6 Phosphate, L-Threonine, Choline Bitartrate, Riboflavin, mg 1.5 1.3 L-Tyrosine, Potassium Chloride, Citric Acid Ester of Mono- And Diglycerides (An 1.5 1.3 Vitamin B6, mg Emulsifier), L-Phenylalanine, L-Histidine, 3.8 3.2 Vitamin B12, mcg L-Tryptophan, L-Cystine, L-Methionine, Niacin, mg 9.6 8.0 L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, Folic Acid, mcg 461 384 Taurine, Zinc Sulfate, DL-alpha Tocopheryl Pantothenic Acid, mg 6.1 5.1 Acetate, Manganese Sulfate, Niacinamide, Biotin, mcg 34.6 28.8 L-Carnitine, Calcium-D-Pantothenate, Cupric Vitamin C, mg 120 100 Sulfate, Thiamin Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Choline, mg 480 400 Vitamin A Acetate, Folic Acid, Potassium Inositol, mg 108 90 MineralsIodide, Sodium Selenite, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Calcium, mg 1555 1296 Vitamin D3, Cyanocobalamin. Phosphorus, mg 1555 1296 Vanilla flavoured version also contains: Magnesium, mg 246 205 Artificial flavour. Iron, mg 26.9 22.4 Please see individual product label for exact Zinc, mg 21.1 17.6 order of ingredients. Manganese, mg 3.6 3.0 Copper, mcg 1900 1583 Iodine, mcg 276 230 Molybdenum, mcg 63.4 52.8 Chromium, mcg 41.3 34.4 Selenium, mcg 76.8 64.0 Sodium, mg (mmol) 1114 (48.4) 9 28 (40.3) Potassium, mg (mmol) 1613 (41.3) 1344 (34.4) Chloride, mg (mmol) 864 (24.3) 720 (20.3) UCD Anamix Junior Nutrition Information: UCD Anamix® Junior 141 Metabolics 142 Measure g Product g Protein Equivalent Measure g Product g Protein Equivalent Measure g Product g Protein Equivalent Measure g Product g Protein Equivalent Periflex Infant 1 scoop 4.75 1 tsp 2 1 Tbsp 7 1/4 cup 30 1/3 cup 35 1/2 cup 57 1 cup 114 PKU Periflex Junior Plus (Plain) 1 tsp 2.9 1 Tbsp 8.7 1/4 cup 34.8 1/3 cup 46.3 1/2 cup: 69.5 1 cup: 139 PKU Periflex Junior Plus (Flavours) 1 scoop 9 1 tsp 2.8 1 Tbsp 8.3 1/4 cup 33 1/2 cup 66 1 cup 132 Periflex Advance (Flavoured & Unflavoured) 1 tsp 3.1 1.1 1 Tbsp 9.4 3.3 1/4 cup 37.5 13 1/3 cup 50 18 1/2 cup 75 26 1 cup 150 53 PhenylAde Essential Drink Mix Enclosed scoop 40 10 One pouch 40 10 1 Tablespoon 10 2.5 1/4 cup 40 10 1/2 cup 80 20 1 cup 160 40 PhenylAde GMP Enclosed scoop 33.3 10 1 tsp 1.2 0.36 1 Tbsp 6.6 2.0 1/4 cup 31 9.3 1/3 cup 39 11.7 1/2 cup 67 20.1 1 cup 128 38.4 PhenylAde40 Drink Mix One Pouch 25 10 1 Tablespoon 10 4 1/4 cup 40 16 1/2 cup 80 32 1 cup 160 64 PhenylAde60 Drink Mix Enclosed scoop 16.7 10 One pouch 16.7 10 1 Tablespoon 9.8 5.9 1/4 cup 37 22.5 1/2 cup 74 45 1 cup 148 90 PhenylAde Amino Acid Blend Enclosed scoop 12.4 10 One pouch 12.4 10 1 Tablespoon 8.5 6.9 1/4 cup 29 23.5 1/2 cup 58 47 1 cup 116 94 PhenylAde MTE Amino Acid Blend Enclosed scoop 12.8 10 One pouch 12.8 10 1 Tablespoon 8.5 6.6 1/4 cup 29 22.6 1/2 cup 58 45 1 cup 116 90 Analog Range 1 scoop 5 0.65 1 Tbsp 8 1.0 1/4 cup 30 3.9 1/2 cup 55 7.2 1 cup 115 15 Maxamaid Range (Flavoured & Unflavoured) 1 Tbsp 9 2.3 1/4 cup 35 8.8 1/2 cup 70 18 1 cup 145 36 Maxamum Range (Flavoured & Unflavoured) 1 Tbsp 9 1/4 cup 35 1/2 cup 70 1 cup 145 UCD Anamix Junior Unflavoured 1 scoop 5.0 1 tsp 3.0 1 Tbsp 9.0 1/4 cup 35.8 1/3 cup 47.7 1/2 cup 71.5 1 cup 143 UCD Anamix Junior Vanilla 1 scoop 5.0 1 tsp 2.9 1 Tbsp 8.7 1/4 cup 34.8 1/3 cup 46.3 1/2 cup 69.5 1 cup 139 TYR Anamix Next 1 tsp 2.9 1 Tbsp 8.6 1/4 cup 34.3 1/3 cup 45.7 1/2 cup 68.5 1 cup 137 HCU Anamix Next Enclosed scoop 9.0 1 tsp 2.8 1 Tbsp 8.3 1/4 cup 33.3 1/3 cup 44.3 1/2 cup 66.5 1 cup 133 0.62 0.26 0.91 3.9 4.6 7.4 14.8 0.81 2.4 9.7 13 19.5 38.9 2.5 0.78 2.3 9.2 18.5 37 Household measures are based on standard dry measures.* All measures are level and unpacked. These values are approximations only and have been provided for convenience: results can vary significantly based on the individual, device, and method. Nutricia North America recommends using a scale for greatest accuracy. The scoops Nutricia provides are validated for use with Nutricia formulas, so are preferable to household measures. *Dry household measures: 1 cup = 240 mL; ½ cup = 120 mL; ⅓ cup = 80 mL; ¼ cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; ½ tsp = 2.5 mL Household measures are based on standard dry measures.* All measures are level and unpacked. These values are approximations only and have been provided for convenience: results can vary significantly based on the individual, device, and method. Nutricia North America recommends using a scale for greatest accuracy. The scoops Nutricia provides are validated for use with Nutricia formulas, so are preferable to household measures. *Dry household measures: 1 cup = 240 mL; ½ cup = 120 mL; ⅓ cup = 80 mL; ¼ cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; ½ tsp = 2.5 mL 3.6 14 28 58 0.60 0.36 1.1 4.3 5.7 8.6 17.2 0.60 0.35 1.0 4.2 5.6 8.3 16.7 0.81 2.4 9.6 12.8 19.2 38.4 2.5 0.78 2.3 9.3 12.4 18.6 37.2 Metabolic Household Measurements Household Measurements 143 Measure g Product g Protein Equivalent Metabolics IVA Anamix Next Enclosed scoop 1 tsp 1 Tbsp 1/4 cup 1/3 cup 1/2 cup 1 cup MMA/PA Anamix Next Enclosed scoop 1 tsp 1 Tbsp 1/4 cup 1/3 cup 1/2 cup 1 cup GlutarAde Junior GA-1 Drink Mix 1 Tablespoon Enclosed scoop 1/4 cup 1/2 cup 1 cup 144 9.0 2.9 8.8 35.0 46.7 70.0 140 2.5 0.82 2.5 9.8 13.1 19.6 39.2 9.0 2.9 8.8 35.0 46.7 70.0 140 2.5 0.82 2.5 9.8 13.1 19.6 39.2 9.3 9.8 36 73 146 0.93 0.98 3.6 7.3 14.6 Household measures are based on standard dry measures.* All measures are level and unpacked. These values are approximations only and have been provided for convenience: results can vary significantly based on the individual, device, and method. Nutricia North America recommends using a scale for greatest accuracy. The scoops Nutricia provides are validated for use with Nutricia formulas, so are preferable to household measures. *Dry household measures: 1 cup = 240 mL; ½ cup = 120 mL; ⅓ cup = 80 mL; ¼ cup = 60 mL; 1 Tbsp = 15 mL; 1 tsp = 5 mL; ½ tsp = 2.5 mL Measure g Product g Protein Equivalent GlutarAde Essential GA-1 Drink Mix 1 Tablespoon 10 1/4 cup 40 Enclosed scoop 40 1/2 cup 80 1 cup 160 GlutarAde GA-1 Amino Acid Blend 1 Tablespoon 8.5 Enclosed scoop 12.3 1/4 cup 29 1/2 cup 58 1 cup 116 Complex Junior MSD Drink Mix 1 Tablespoon 8.4 Enclosed scoop 8.5 1/4 Cup 29 1/2 Cup 59 1 Cup 118 Complex Essential MSD Drink Mix 1 Tablespoon 9.8 1/4 Cup 40 Enclosed scoop 40 1/2 Cup 80 1 Cup 160 Complex MSD Amino Acid Blend 1 Tablespoon 8.2 Enclosed scoop 12.4 1/4 Cup 31 1/2 Cup 62 1 Cup 124 2.5 10 10 20 40 6.9 10 23.5 47 94 1.1 1.1 3.8 7.6 15.2 2.4 10 10 20 40 Metabolic Household Measurements Household Measurements 6.6 10 25 50 100 145 PKU Periflex® Junior Plus and Anamix® Next Infant formula containing iron, DHA & ARA, for the dietary management of phenylketonuria. Formulas for the dietary management of metabolic disorders in individuals over one year of age. Administration: • Periflex Infant formula must be consumed in conjunction with a whole protein source (e.g. breast milk or standard infant formula) in quantities prescribed by a dietitian or physician to meet complete protein requirements and ensure normal growth. • Formula dosage and dilution will vary depending on the age, body weight, medical condition and protein tolerance of the infant. Metabolics Mixing Instructions: 146 1. Wash hands with soap and water. 2. Clean and sanitize working surface. 3. Sterilize bottles, nipples, caps and other equipment by placing in water which is then brought to a rolling boil for 2 minutes. Store covered until ready to use. 4. Bring fresh water to a rolling boil for 2 minutes and cool. For healthy, full-term infants cool to room temperature. For low birth weight or immunocompromised infants consult your healthcare professional. 5. At standard dilution (0.67 kcal/mL), 1 level unpacked scoop (4.75 g powder) makes 30 mL of prepared formula. 6. Measure the required amount of powder into bottle(s) with provided scoop (see table). 7. Add the appropriate amount of water. Cap bottle(s). 8. Shake well for 15-20 seconds or until powder dissolves. 9. Use immediately after preparation or refrigerate promptly at 4º C or less and use within 24 hours. 10. Shake immediately before use. 11. Once feeding has started, use within 1 hour. Discard any leftover formula. 12. Do not use a microwave oven to prepare or warm formula. 13. Do not boil prepared formula. Water to Add 105 ml 215 ml 800 ml Amount of Powder Water Added 4 level unpacked scoops (19 g) 8 level unpacked scoops (38 g) 30 level unpacked scoops (142.5 g) 120 ml 240 ml 900 ml Storage: • Store unopened cans at room temperature. Avoid extreme temperatures. Cover opened can with provided lid and store in a cool, dry place. Use within one (1) month. Administration: Dilution Amount of Water Final (kcal/mL)Powder Added Volume 0.6 18 g (approx 2 scoops) 3.5 fl oz (100 mL) 3.9 fl oz (114 mL) 0.9 27 g (approx 3 scoops) 3.5 fl oz (100 mL) 4.0 fl oz (120 mL) 1.1 36 g (approx 4 scoops) 3.5 fl oz (100 mL) 4.3 fl oz (126 mL) • Products must be consumed in conjunction with natural protein and other nutrients in quantities prescribed by a dietitian or physician to supply whole protein, fluid and general nutrition requirements. • Intake is dependent on the age, body weight and medical condition of the individual. • Periflex and Anamix should be divided into equal portions and distributed throughout the day. Freshly prepared formula is best. Refrigerate premixed formula immediately and use within 24 hours of mixing. Shake immediately before use. Mixing Instructions: Precautions: • Add the desired volume of water to a shaker or other container with a tight fitting lid. Then add the prescribed amount of powder and shake until fully blended together. Periflex and Anamix are best served chilled. • Standard dilution is 100 mL (3.5 fl oz) water plus 36 g powder (approx. 4 scoops) made up to a final volume of approx. 126 mL (4.3 fl oz). Storage: • Must only be consumed by individuals with a proven metabolic disorder. Not intended for infants. Not intended as sole source of nutrition. Not for parenteral use. Metabolic Mixing Instructions Periflex® Infant • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not refrigerator) and use within 14 days of opening. 147 Analog™ Age-specific formulas for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and women of child-bearing age. Infant formulas for the dietary management of metabolic disorders. Administration: • Periflex LQ: Shake well before use. Best served chilled. • Analog metabolic infant formulas must be consumed in conjunction with a whole protein source (e.g. breast milk or standard infant formula) in quantities prescribed by a dietitian or physician to meet complete protein requirements and ensure normal growth. • Formula dosage will vary depending on the age, body weight, medical condition and protein tolerance of the infant. Precautions: Mixing Instructions: • Use only under the direction of a physician or dietitian. Periflex must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine and general nutritional requirements. • Intake of Periflex is dependent on the age, bodyweight and medical condition of the individual. Periflex should be divided into equal portions and distributed throughout the day. Metabolics Mixing Instructions: 148 • Periflex Advance: Add the desired volume of water to a shaker or other container with a tight fitting lid. Then add the prescribed amount of powder and shake until fully blended together. Dilution guidelines are shown in the tables below. Periflex Advance is best served chilled. • Periflex Advance tastes great when blended with 30 mL (1 fl oz) of water for every 5 to 6 grams of powder. • Once prepared, store formula in a refrigerator for no longer than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. Dilution Guidelines for Periflex Advance Volume of Water Prescribed Amount Approx. Protein Equiv. 60-90 mL (2 to 3 fl oz) 16 g 6g 120-150 mL (4 to 5 fl oz) 32 g 11 g 240-300 mL (8 to 10 fl oz) 64 g 22 g 480-600 mL (16 to 20 fl oz) 128 g 45 g • Must only be consumed by individuals with proven phenylketonuria. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month of opening. • Store Periflex LQ in a cool dry place away from sunlight. Dilutions are guidelines only. Periflex Advance may be given in a more concentrated form (e.g., a paste or concentrated drink) by using less water. If consumed in a concentrated form, water or other drinks should also be consumed at the same time. Administration: 1.Wash hands thoroughly and clean preparation area. Sterilize bottle feeding system. 2.Boil water for 5 minutes and allow to cool for at least 30 minutes so that it feels warm to the wrist. 3.Add the prescribed amount of Analog powder and a protein source to the sterilized feeding bottle. For accuracy, Analog should be weighed on a gram scale. If using the provided scoop, fill it and level off with a clean, dry knife. Do not press the powder into the scoop. 4.Pour the required amount of cooled, boiled water into feeding bottle. To make the recommended dilution (21 kcal/fl oz), Analog requires 30 mL (1 fl oz) of water for every 5 g (1 unpacked, level scoop) of powder. Place cap on bottle and shake until powder has dissolved. 5.Make sure the formula is lukewarm by placing a few drops on your wrist. Formula prepared in advance must be cooled rapidly, stored in the refrigerator (35°F to 40°F) and used within 24 hours of preparation. Shake immediately before use. Formula remaining in the bottle after one hour of feeding should be discarded. Tube feeding “hang time” should not exceed 4 hours. Caution: Metabolic Mixing Instructions Periflex® Advance and Periflex® LQ • Do not boil formula. Do not use a microwave oven to prepare or warm formula. Precautions: • Must only be given under strict medical supervision to infants with a proven metabolic disorder. Not intended as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not refrigerator) and use within one month of opening. 149 PhenylAde™: Essential, GMP, 40, 60 and AA Blends Age-specific formulas for the dietary management of metabolic disorders in individuals over 1 year of age, including pregnant women and women of child-bearing age. Formulas for the dietary management of phenylketonuria (PKU) in children and adults, including pregnant women and woman of child-bearing age. Administration: Administration: • Must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrition requirements. • Recommended intake will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. For accuracy, weigh on a scale. The daily intake should be divided into equal portions and distributed throughout the day. • Maxamaid products are intended for toddlers and younger children; Maxamum products are intended for older children and adults, including pregnant women and women of child-bearing age. Metabolics Mixing Instructions: 150 • Best served with meals. • Make a paste of the prescribed amount of powder with a small volume of chilled water. Gradually add sufficient water to make the desired volume. • For best taste, consume immediately. Larger volumes of prepared formula should be refrigerated and used within 24 hours of preparation. • It is recommended that Maxamaid and Maxamum be prepared at a 1 to 7 dilution initially and advanced to a 1 to 5 dilution. These dilutions Dilution Guidelines for Maxamaid Dilution Amount of Powder Volume of Water Approx. PE 1 to 7 35 g 245 mL (approx. 8 fl oz) 8.8 g 1 to 5 35 g 175 mL (approx. 6 fl oz) 8.8 g Dilution Guidelines for Maxamum Dilution Amount of Powder Volume of Water Approx. PE 1 to 7 35 g 245 mL (approx. 8 fl oz) 14 g 1 to 7 1 sachet (50 g) 350 mL (approx. 12 fl oz) 20 g 1 to 5 35 g 175 mL (approx. 6 fl oz) 14 g 1 to 5 1 sachet (50 g) 250 mL (approx. 8 fl oz) 20 g are guidelines only. May be given in a more concentrated form (e.g. drink or paste). If so, water or diluted drinks should be offered at the same time. Precautions: • Must only be given under strict medical supervision to patients with proven phenylketonuria. Not intended for children under one year of age. Not suitable as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened cans/sachets at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month. • PhenylAde40 Drink Mix • Use only under the direction of a physician or dietitian. PhenylAde must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet the phenylalanine and general nutrient requirements. Add contents of 1 pouch (25 g) to approx. 120-180 mL (4-6 fl oz) of Mixing Instructions: • PhenylAde Amino Acid Blends 1. Add prescribed amount of PhenylAde Powder to cold water, shake or stir until completely mixed together. 2. Dilution may be adjusted to taste. See recommended dilution below for a guideline. 3. Once prepared, store formula in a refrigerator for no more than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. 4. Do not heat, bake or add to food or beverages above 54°C (130°F). Recommended Dilution: • PhenylAde Essential Drink Mix Add contents of 1 scoop or pouch (40 g) to approx. 210 mL (7 fl oz) of cold water. • PhenylAde GMP Drink Mix Add contents of 1 scoop or pouch (33.3 g) to approx. 150-180 mL (5-6 fl oz) of cold water. • PhenylAde60 Drink Mix Add contents of 1 scoop or pouch (16.7 g) to approx 90 mL (3 fl oz) of cold water. Simply add one serving to single portion of low protein food, beverage or other PKU formula. The appropriate serving size must be established and consumed to meet prescribed amino acid protein requirements. Not intended to be added to plain water. Metabolic Mixing Instructions Maxamaid® and Maxamum® Precautions: • Must be consumed by individuals with proven phenylketonuria. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month of opening for all PhenylAde products except PhenylAde GMP Drink Mix. PhenylAde GMP Drink Mix must be used within 2 weeks after being opened. 151 Lanaflex® and PhenylAde™ PheBLOC™ LNAA A phenylalanine-free formula for the dietary management of phenylketonuria (PKU) in individuals over 1 year of age, including pregnant women and women of child-bearing age. Phenylalanine-free powdered formulas containing the remaining essential amino acids (large neutral amino acids and lysine). For the dietary management of phenylketonuria (PKU) in individuals over 12 years of age. Administration: Precautions: Administration: • The Phlexy-10 Drink Mix must be consumed in • Must only be given under strict medical supervision • Use only under the direction of a physician or dietitian. The products must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine and general nutrition requirements. • Intake is dependent on the age, bodyweight and medical condition of the individual. Metabolics conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine and general nutrition requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements. • Intake of the Phlexy-10 Drink Mix will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. One packet of the drink mix is equivalent to 8.33 g of protein. • The Phlexy-10 Drink Mix do not contain vitamins, minerals, or trace elements. It is essential that these nutrients are supplied separately. 152 Mixing Instructions: • Mix the contents of one packet with a small amount of water, stirring into a thick paste. Continue stirring while adding water to make up a final volume of approximately 100 mL (~3.5 fl oz). to patients with proven phenylketonuria. Not intended for use as the sole source of nutrition. Not intended for infants under 1 year of age. Not for parenteral use. Storage: • Phlexy-10 Drink Mix should be stored in a cool, dry place. Once reconstituted, Phlexy-10 Drink Mix should be stored in a refrigerator and must be used within 24 hours of preparation. Mixing Instructions: Lanaflex • It is recommended that the product is prepared at an approximate 1 to 4 dilution. In a screw top container, add 60 mL (2 fl oz or 1⁄4 cup) of chilled water. Add the contents of one sachet and shake well until dissolved. The product is best consumed immediately. • If taken in a more concentrated form, water or diluted drinks should be consumed immediately afterwards. • Opened sachets should be stored in an airtight container and used within 24 hours. PhenylAde PheBLOC LNAA • Add contents of 1 pouch (3 g) to ~1/2 cup of any semi-solid food (i.e., applesauce, mashed potatoes, pudding, sorbet, etc). Precautions: • Must only be consumed by individuals with proven phenylketonuria. Suitable for individuals over 12 years of age. Not suitable as the sole source of nutrition. Not for parenteral use. • Not for use when planning or during pregnancy. • Seek medical advice before using with serotonergic medications or any kind of psychotropic medications. Metabolic Mixing Instructions Phlexy-10® Drink Mix Storage: • Store unopened sachets in a cool, dry place. 153 Complex MSD: Junior, Essential and AA Blends Low volume, amino acid-based formulas for the dietary management of metabolic disorders in children and adults, including pregnant women and women of child-bearing age. Formulas for the dietary management of Maple Syrup Urine Disease (MSUD) in children and adults, including pregnant women and woman of child-bearing age. Administration: Mixing Instructions (Lophlex): • Use only under the direction of a physician or • Mix the contents of one sachet with a small Metabolics dietitian. Lophlex and Lophlex LQ must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet amino acid and general nutrition requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements. • Intake of Lophlex and Lophlex LQ will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. Lophlex and Lophlex LQ should be divided into equal portions and distributed throughout the day. 154 amount of water to make a paste. Continue stirring while adding water to make up a final volume of approximately 70 mL (2.5 fl oz). This would be a 1 to 5 dilution. Lophlex may be taken in a more concentrated form, either as a drink or paste. If so, water or diluted drinks should be offered at the same time. Lophlex is best prepared with chilled water and consumed immediately after preparation. Precautions: • Must only be given under strict medical supervision in individuals with a proven metabolic disorder. Not intended as a sole source of nutrition. Not for parenteral use. Preparation (Lophlex LQ) Storage: • Lophlex LQ is ready-to-drink and tastes best • Store in a cool, dry place, below 30°C (86°F) (not in when served chilled. Shake vigorously before use. the refrigerator) and away from sunlight. Administration: Dilution of approx. 30 calories per 1 fl oz (30 mL) • Use only under the direction of a physician or dietitian. Complex MSD must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet the branched-chain and general nutrient requirements. Mixing Instructions: • Add prescribed amount of Complex MSD Powder to cold water, shake or stir until completely mixed together. • Dilution may be adjusted to taste. See recommended dilution below for a guideline. • Once prepared, store formula in a refrigerator for no more than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. • Do not heat, bake or add to food or beverages above 54°C (130°F). Recommended Dilution: • Complex Junior MSD Drink Mix Dilution of approx. 20 calories per 30 mL (1 fl oz) To Make Approx. 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Water 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Amount of Powder 8.5 g 17 g 26 g 34 g To Make Approx. 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Water 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Amount of Powder 12.2 g 24.3 g 36.5 g 48.6 g • Complex Essential MSD Drink Mix Add contents of 1 scoop (40 g) to approx. 210 mL (7 fl oz) of cold water. • Complex MSD Amino Acid Blend Simply add one serving to single portion of low protein food, beverage or other MSUD powder formula. The appropriate serving size must be established and consumed to meet prescribed amino acid protein requirements. Not intended to be added to plain water. Precautions: • Must be consumed by individuals with proven maple syrup urine disease. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month of opening. 1 level, unpacked scoop provides approx. 8.5 g of powder. For better accuracy use a scale. Metabolic Mixing Instructions Lophlex® Powder and Lophlex® LQ 155 UCD Anamix® Junior Formulas for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults, including pregnant women and woman of child-bearing age. A formula for the dietary management of urea cycle disorders in individuals over 1 year of age. Dilution of approx. 30 calories per 30 mL (1 fl 0z) Administration: • Use only under the direction of a physician or dietitian. GlutarAde must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet the lysine and general nutrient requirements. Mixing Instructions: • Add prescribed amount of GlutarAde Powder to cold water, shake or stir until completely mixed together. • Dilution may be adjusted to taste. See recommended dilution below for a guideline. • Once prepared, store formula in a refrigerator for no more than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. • Do not heat, bake or add to food or beverages above 54°C (130°F). Metabolics Recommended Dilution 156 • GlutarAde Junior GA-1 Drink Mix Dilution of approx. 20 calories per 30 mL (1 fl oz) To Make Approx. 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL( 8 fl oz) Water 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Amount of Powder 9.8 g 19.5 g 29 g 39 g To Make Approx. 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Water 60 mL (2 fl oz) 120 mL (4 fl oz) 180 mL (6 fl oz) 240 mL (8 fl oz) Amount of Powder 14.7 g 29.4 g 44.1 g 58.8 g • GlutarAde GA-1 Essential Drink Mix Add contents of 1 scoop (40g) to approx. 7 fl oz (210 mL) of cold water. • GlutarAde GA-1 Amino Acid Blend Simply add one serving to single portion of low protein food, beverage or other GA-1 formula. The appropriate serving size must be established and consumed to meet prescribed amino acid protein requirements. Not intended to be added to plain water. Precautions: • Must be consumed by individuals with proven glutaric aciduria type 1. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use. Storage: • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month of opening. 1 level, unpacked scoop provides approx. 9.8 g of powder. For better accuracy use a scale. Administration: • Must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrition requirements. • Recommended intake of UCD Anamix Junior is dependent on age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. For accuracy, weigh on a scale. The daily intake should be divided into equal portions and distributed throughout the day. Mixing Instructions: • Best served chilled with meals. • Pour the required volume of cold water into a glass or cup. • Add the prescribed amount of UCD Anamix Junior powder to the water and stir. For accuracy it is recommended to use a scale. • It is recommended that UCD Anamix Junior be prepared at a 1 to 3.5 dilution. This dilution is a guideline only. An alternative dilution may be recommended by a physician or dietitian (e.g. drink or paste). If given in a more concentrated form, water or diluted drinks should be offered at the same time. Dilution Guidelines for UCD Anamix Junior Dilution Amount of Powder Volume of Water Approx. PE 1 to 3.5 50 g (10 scoops) 175 mL (approx. 6 fl oz) 6.0 g Precautions: • Must only be given under strict medical supervision to patients with proven urea cycle disorders. Not intended for children under one year of age. Not suitable as the sole source of nutrition. Not for parenteral use. Storage: • Once reconstituted store in a refrigerator and Metabolic Mixing Instructions GlutarAde™ GA-1: Junior, Essential and AA Blends use within 24 hours. • Store unopened cans in a cool, dry place. Do not store at extreme temperatures. Once opened, cover opened can with provided lid and store in a cool, dry place (not in refrigerator) and use within one month. 157 158 Metabolics ei n Fo od s Low Protein Foods ot Pr Low 159 Low Protein Foods Low Protein Foods Loprofin, Milupa & Wel-Plan® Low Protein Foods Maddy’s® Low Protein Foods A line of low protein foods including: baking mixes, cake mix, pasta, rice, cereals, drink mix, cookies, energy bars, and other snacks. A line of low protein foods including baking mixes, cake mixes and other snacks. Main Features: Indications: • A wide range of products to add variety to a protein-restricted diet • Dietary management of inherited metabolic disorders • Renal or liver failure requiring a low protein diet • Other medical conditions where a low protein diet is indicated For more information, visit www.MedicalFood.com 160 Main Features: Indications: • A wide range of products to add variety to a protein-restricted diet • Dietary management of inherited metabolic disorders • Renal or liver failure requiring a low protein diet • Other medical conditions where a low protein diet is indicated For more information, visit www.DietForLife.com 161 162 Low Protein Foods ol og y Neurology ur Ne 163 KetoCal 4:1 Powder Neurology A nutritionally complete, ketogenic formula in a 4:1 ratio (fat:carbohydrate + protein) for the dietary management of intractable epilepsy; designed for individuals over 1 year of age. 164 Main Features: Indications: •Nutritionally complete • 4:1 ratio • Vanilla flavour • Convenient one step preparation with a non-modular approach • Nutrient dense for children with low energy requirements • Appropriate for enteral or oral feedings • Standard dilution = 1.44 kcal/mL •Osmolality (at 1.44 kcal/mL): 197 mOsm/kg • Energy distribution: Protein 8.4% Carbohydrate3.1% 90% Fat (LCT 100%) • Displacement 1 mL/g • • • • Intractable epilepsy Pyruvate dehydrogenase deficiency (PDH) Glucose transporter type-1 deficiency (GLUT1) Other disorders where the ketogenic diet is indicated For details on administration, please see pages 170-171. Ordering Information: Product Code 16671 Product Packaging 6 x 300 g Calories Per Can 2160 Nutrients Per 100 g Per 100 ml* Energy, kcal (kJ) 720 (2970) 144 (594) Protein, g 15 3 Carbohydrate, g 3 0.6 Dietary Fibre, g 0 0 Fat, g 72.0 14.4 Linoleic Acid, g 9.2 1.84 Vitamins Vitamin A, IU 1500 300 208 41.6 Vitamin D3, IU Vitamin E, IU 11 2.2 Vitamin C, mg 60 12 Thiamin, mg 0.64 0.13 Riboflavin, mg 0.64 0.13 Niacin, mg 7.5 1.5 0.640.13 Vitamin B6 Folic Acid, mg 0.19 0.038 0.0013 0.0003 Vitamin B12, mg Pantothenic Acid, mg 2.6 0.052 Vitamin K, mg 0.04 0.008 Biotin, mg 0.0125 0.0025 Choline, mg 480 96 Inositol, mg 135 27 Ingredients: Minerals/Trace Elements Per 100 g Per 100 ml* Calcium, mg 800 160 Phosphorus, mg 650 130 Magnesium, mg 110 22 Iron, mg 11 2.2 Zinc, mg 5.8 1.2 Iodine, mg 0.082 0.0164 Manganese, mg 1.6 0.32 Copper, mg 0.8 0.16 Molybdenum, mg 0.026 0.0052 Chromium, mg 0.019 0.0038 Selenium, mg 0.034 0.0068 Sodium, mg 300 60 Potassium, mg 1080 216 Chloride, mg 500 100 Hydrogenated Soybean Oil, Dry Whole Milk, Refined Soybean Oil, Soy Lecithin, Corn Syrup Solids, Tripotassium Citrate, Tricalcium Citrate, Potassium Chloride, Tricalcium Phosphate, Choline Bitartrate, Magnesium Hydrogen Phosphate, Calcium Phosphate, Magnesium Acetate, Trisodium Citrate, M-Inositol, L-Isoleucine, L-Tryptophan, Artificial Flavour (Ethyl Vanillin), L-Ascorbic Acid, Aspartame* (Contains Phenylalanine), L-Carnitine, Ferrous Sulphate, Taurine, Zinc Sulphate, DL-Alpha Tocopheryl Acetate, Nicotinamide, Mananese Sulphate, Calcium-DPantothenate, Copper Sulphate, Artificial Colour (Beta Carotene), Potassium Iodide, Thiamine Hydrochloride, Pyridoxine Hydrochloride, Sodium Selenite, Riboflavin, Vitamin A Acetate, Folic Acid, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. KetoCal 4:1 Powder Nutrition Information: ® * Contains Aspartame 10 mg/100 mL * Recommended dilution of 4 mL of water to 1 g of powder 165 Neurology A nutritionally complete, ketogenic formula in a 4:1 ratio (fat:carbohydrate + protein) for the dietary management of intractable epilepsy; designed for individuals over 1 year of age. 166 Main Features: Indications: •Nutritionally complete • 4:1 ratio • Vanilla flavour • Convenient one step preparation with a non-modular approach • DHA and ARA • Contains multi-fibre blend • Contains sucralose • Nutrient dense for children with low energy requirements • Appropriate for enteral or oral feedings • Standard dilution = 1 kcal/mL • Osmolality (at 1 kcal/mL): 170 mOsm/kg • Energy distribution: Protein 8.2% Carbohydrate3.1% Fiber 1.5% 88.7% Fat (LCT 100%) • Displacement 1 mL/g • • • • Intractable epilepsy Pyruvate dehydrogenase deficiency (PDH) Glucose transporter type-1 deficiency (GLUT1) Other disorders where the ketogenic diet is indicated For details on administration, please see pages 170-171. Ordering/Reimbursement Information: Product Code 101777 Product Packaging 6 x 300 g (11 oz) Calories Per Can 2103 Nutrients Per 100 g Per 100 mL Energy, kcal (kJ) 705 (2950)100 (411) Protein, g 14.4 2 Carbohydrate, g 8.2 1.2 Fibre, g 5.3 0.75 Soluble, g 3.2 0.45 Insoluble, g 2.1 0.3 Fat, g 69.2 9.8 Saturated, g 26.7 3.8 + Trans, g 0 0 Monounsaturated, g 22.8 3.2 Polyunsaturated, g 19.7 2.8 Arachidonic Acid, mg 120 17 Docosahexaenoic Acid, mg110 15.6 Vitamins Vitamin A, IU (mcg) 1232 (370) 175 (52.5) Vitamin D, IU (mcg) 420 (10.5) 59.6 (1.5) Vitamin E, IU (mg α TE) 15.9 (10.7) 2.3 (1.5) Vitamin K, mg 0.031 0.0044 Thiamin, mg 0.89 0.13 Riboflavin, mg 0.7 0.1 Vitamin B6, mg 0.7 0.1 Vitamin B12, mg 0.0013 0.00018 Niacin, mg 4.9 0.7 Folic Acid, mg 0.116 0.0165 Pantothenic acid, mg 2.9 0.41 Biotin, mg 0.0191 0.0027 Vitamin C, mg 40 5.7 Choline, mg 320 45.5 Inositol, mg 19.1 2.7 Ingredients: Minerals, Trace Elements Calcium, mg Phosphorus, mg Magnesium, mg Iron, mg Zinc, mg Manganese, mg Copper, mg Iodine, mg Molybdenum, mg Chromium, mg Selenium, mg Sodium, mg Potassium, mg Chloride, mg L-Carnitine, mg Taurine, mg Per 100 g Per 100 mL 700 99.3 420 59.6 96.3 13.7 7 0.99 3.6 0.51 0.83 0.12 0.5 0.071 0.0862 0.0122 0.0287 0.0041 0.0148 0.0021 0.027 0.0038 481 68.2 771 109 726 103 45 6.4 33 4.7 Refined Vegetable Oils (Palm, Soy, High Oleic Sunflower), Casein (Milk), Soy Lecithin, Whey (Milk), Microcrystalline Cellulose, Chicory Root Inulin, Calcium Carbonate, Corn Syrup Solids, Fructooligosaccharide (FOS), Silicon Dioxide, Gum Arabic, Tripotassium Citrate, Potassium Chloride, Sodium Chloride, Calcium Phosphate Tribasic, High Amylose Corn Starch, Artificial Flavor (Vanilla), L-Arginine, L-Cystine, Choline Bitartrate, M. Alpina Oil*, C. Cohnii Oil**, Soy Fiber, L-Tryptophan, Magnesium Oxide, Sodium Caseinate (Milk), Sodium Ascorbate, L-Phenylalanine, Maltodextrin, L-Ascorbic Acid, L-Valine, L-Tyrosine, L-Carnitine, Taurine, Ferrous Sulfate, Monoand Diglycerides, DL-alpha Tocopheryl Acetate, Sucralose§,M-Inositol, L-Histidine, Zinc Sulfate, Niacinamide, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Ascorbyl Palmitate, Mixed Tocopherols, Folic Acid, Potassium Iodide, Sodium Molybdate, Chromium Chloride, Sodium Selenite, Phylloquinone, D-Biotin, Cholecalciferol, Cyanocobalamin. KetoCal 4:1 Powder Nutrition Information: KetoCal® 4:1 Powder *A SOURCE OF ARACHIDONIC ACID (ARA) **A SOURCE OF DOCOSAHEXAENOIC ACID (DHA) § Contains sucralose 14.2 mg/100 mL * Standard Dilution = 1 kcal/mL Fiber is not included in calculating the ketogenic ratio 167 Neurology A nutritionally complete, ready-to-feed ketogenic formula in a 4:1 ratio (fat:carbohydrate + protein) for the dietary management of intractable epilepsy; designed for individuals over 1 year of age. 168 Main Features: Indications: • • • • • • • • • Nutritionally complete 4:1 ratio Convenient ready-to-feed liquid Great vanilla flavour or unflavoured Contains a multi-fibre blend of insoluble and soluble fibre • DHA and ARA • Appropriate for enteral or oral feedings • Contains sucralose • Nutrient dense for children with low energy requirements • Osmolality (at 1.5 kcal/mL): Vanilla 260 mOsm/kg Unflavoured 280 mOsm/kg • Energy distribution: Protein 8.2% Carbohydrate3.1% Fibre 1.5% 88.7% Fat (LCT 100%) • Free water 77.8% •Density 1.01g/mL Intractable epilepsy Pyruvate dehydrogenase deficiency (PDH) Glucose transporter type-1 deficiency (GLUT1DS) Other disorders where the ketogenic diet is indicated For details on administration, please see pages 170-171. Ordering Information: Product Code 80180 – Vanilla 80183 – Unflavored Product Packaging 27 x 237 mL (8 fl oz) 27 x 237 mL (8 fl oz) Calories Per Box 356 356 Nutrients Per 100 mL Per 237 mL Minerals/Trace Elements Per 100 mL Per 237 mL Energy, kcal (kJ) 150 (620) 3 56 (1469) Calcium, mg 88.4 210 Protein, g 3.09 7.32 Phosphorus, mg 88.4 210 Carbohydrate, g 1.73 4.10 Magnesium, mg 22.7 53.8 Dietary Fibre, g 1.12 2.65 Iron, mg 1.5 3.6 Soluble, g 0.56 1.33 Zinc, mg 1.2 2.8 Insoluble, g 0.56 1.33 Manganese, mg 0.180 0.427 Fat, g 14.8 35.1 Copper, mg 0.120 0.284 Saturated, g 2.2 5.2 Iodine, mg 0.0185 0.0438 + Trans, g 00 Molybdenum, mg 0.0062 0.0147 Monounsaturated, g 8.3 19.7 Chromium, mg 0.0032 0.0076 Polyunsaturated, g 3.7 8.8 Selenium, mg 0.0071 0.0168 Arachidonic Acid, mg 55.0 131 Sodium, mg 103 244 Docosahexaenoic Acid, mg 55.0 131 Potassium, mg 165 391 Long Chain Tryglycerides (LCT)%100 100 Chloride, mg 155 367 Vitamins Carnitine, mg 8.3 19.7 Vitamin A, IU 264 626 Taurine, mg 6.3 14.9 92 220 Vitamin D3, IU Vitamin E, IU 2.3 5.5 Vitamin K, mg 0.0056 0.0132 Thiamin, mg 0.15 0.36 Riboflavin, mg 0.15 0.36 0.15 0.36 Vitamin B6, mg 0.00017 0.00040 Vitamin B12, mg Niacin, mg 1.5 3.6 Folic Acid, mg 0.0287 0.0680 Pantothenic Acid, mg 0.62 1.50 Biotin, mg 0.0041 0.0097 Vitamin C, mg 9.3 22.0 Choline, mg 51.5 122 Inositol, mg 4.1 9.7 Ingredients (Unflavoured and Vanilla): Water, Refined Vegetable Oil (High Oleic Sunflower, Soy, Palm), Sodium Caseinate (Milk), Whey Protein Concentrate (Milk), Soy Fibre, Corn Starch, Chicory Root Inulin, Citric Acid Esters of Mono- and Diglycerides, Dipotassium Phosphate, Gum Arabic, Calcium Chloride, Mortierella Alpina Oil*, Magnesium Acetate, Potassium Chloride, Crypthecodinium Cohnii Oil**, Microcrystalline Cellulose, Fructooligosaccharide (FOS), Ascorbic Acid, Calcium Phosphate Monobasic, Mono- and Diglycerides, Trisodium Citrate, Sodium Hydroxide, Choline Chloride, L-Cystine, Calcium Phosphate Dibasic, Propylene Glycol Alginate, Ferrous Lactate, L-Carnitine, Taurine, Inositol, L-Tryptophan, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Soy Lecithin, Niacinamide, Calcium D-Pantothenate, Manganese Sulfate, Ascorbyl Palmitate, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Mixed Tocopherols, DL-Alpha Tocopherol, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, Biotin, Cholecalciferol, Cyanocobalamin. KetoCal 4:1 LQ Nutrition Information: KetoCal® 4:1 LQ Unflavoured version also contains Sugar. Vanilla flavoured version also contains Artificial Sweetener: Sucralose 43 mg/237mL. *A source of Arachidonic Acid (ARA) **A source of Docosahexaenoic Acid (DHA) 169 Directions for Preparation: For oral and tube feeding: KetoCal 4:1 Powder 1.Measure the required amount of warm water into a container that seals with a screw top lid. To completely dissolve the powder, the water must be at a temperature of 45-50°C (113-122°F). 2. Add the prescribed amount of KetoCal to the water. 3.Cover and shake until the powder has dissolved. 4.Once prepared, the formula should be stored in a refrigerator and kept no longer than 24 hours. KetoCal 4:1 Powder Dilution to be determined by medical prescription: Neurology Directions for Use: 170 Volume and Ordering Guide Mixing Guide: 1.For oral feeding, best served chilled and consumed immediately. 2.For tube feeding, hang time not to exceed 4 hours. It is recommended that the tube is flushed with lukewarm water (approximately 37°C or 98°F) between each feed. 3.Do not boil or microwave formula. 4.Do not freeze. Recommended storage between 4°C-25°C (39°F-77°F). 5.Once powdered formula is prepared or liquid formula is open, use immediately or refrigerate promptly at 4°C/39°F or less and use within 24 hours. Water 80 mL 400 mL 800 mL Powder 20 g 100 g 200 g Final Volume 100 mL 500 mL 1000 mL kcal/mL 1.44 1.44 1.44 A scale is necessary for proper preparation of formula. Coming Soon! KetoCal 4:1 Powder Reformulation Dilution Powder 0.67 kcal/mL 9.5 g 0.8 kcal/mL 11.4 g 1 kcal/mL 14.3 g 1.5 kcal/mL 21.4 g KetoCal 4:1 Powder Water 91 mL 89 mL 86 mL 79 mL Final Volume 100 mL 100 mL 100 mL 100 mL Osmolality 110 mOsm/kg 130 mOsm/kg 170 mOsm/kg 260 mOsm/kg Storage Calories/day Calories/month 60018000 70021000 80024000 90027000 1000 30000 1100 33000 1200 36000 1300 39000 1400 42000 1500 45000 1600 48000 1700 51000 1800 54000 1900 57000 2000 60000 Cans/month Cases/month 9 2 10 2 12 2 13 3 15 3 16 3 18 3 19 4 20 4 22 4 23 4 25 5 26 5 28 5 29 5 KetoCal 4:1 LQ (Vanilla or Unflavoured) Drink boxes/month Cases/month 51 2 59 3 68 3 76 3 85 4 93 4 102 4 110 5 118 5 127 5 135 5 144 6 152 6 161 6 169 7 KetoCal 4:1 Powder and KetoCal 4:1 LQ: *Number of cans and cases per month are rounded up to the nearest whole number. Store unopened product in a cool, dry place and away from sunlight. Caution: KetoCal 4:1 Powder: Once can has been opened, replace lid and store in a cool, dry place (not in a refrigerator) and use within one month. KetoCal 4:1 LQ: Once opened, store in refrigerator. Discard if not consumed within 24 hours. Do not freeze. • • • • KetoCal Directions for Use KetoCal® Family Do not boil or microwave formula. Monitor for hypoglycemia, renal stones, hyperlipidemia, and adequate growth. USE ONLY UNDER STRICT MEDICAL SUPERVISION. NOT FOR PARENTERAL USE. Intake to be determined by a medical professional and is dependent on the age, body weight, and medical condition of the patient. 171 172 Neurology tri tio na ls Other Nutritionals u Oth N er 173 Monogen® Other Nutritionals A milk protein-based powder, low in fat, and high in medium chain triglycerides (MCT). A product for individuals over 1 year of age. 174 Main Features: Indications: • 24% of calories from fat • 80% of fat as MCT • Excellent ratio of essential fatty acids (n6:n3 ratio of 6.2:1) • Contains complete profile of vitamins and minerals including trace elements • Osmolality (mOsm/kg): Dilution 22 kcal/fl oz: 250 mOsm/kg 30 kcal/fl oz: 370 mOsm/kg • Displacement: 0.67 mL/g • Long chain fatty acid oxidation disorders • Hyperlipoproteinemia type 1 • Other lipid and lymphatic disorders where a low fat, high MCT diet is indicated Ordering Information: Product Code 667097 Product Packaging 6 x 400 g (14.1 oz) Calories Per Can 1680 Nutrients Per 100 g Calories420 Protein Equivalent, g 12.5 Fat, g 11.0 LCT 20% MCT 80% Linolenic Acid, mg 530 a-Linolenic acid, mg 80 Carbohydrate, g 68 Vitamins Vitamin A, IU (mcg RE) 1082 (325) 264 (6.6) Vitamin D3, IU (mcg) 4.1 (2.75) Vitamin E, IU (mg a-TE) Vitamin K, mcg 21 Thiamin, mg 0.35 Riboflavin, mg 0.52 0.4 Vitamin B6, mg 0.86 Vitamin B12, mcg Niacin, mg 7.4 Folic Acid, mcg 47 Pantothenic Acid, mg 1.46 Biotin, mcg 22.3 Vitamin C, mg 35 Choline, mg 56 Inositol, mg 85.7 Minerals Calcium, mg Phosphorus, mg Magnesium, mg Iron, mg Zinc, mg Manganese, mg Copper, mcg Iodine, mcg Molybdenum, mcg Chromium, mcg Selenium, mcg Sodium, mg Potassium, mg Chloride, mg Per 100 g 257 200 35 4.2 3.3 0.33 340 40.6 21.4 10.0 10.8 200 360 214 Ingredients: Corn Syrup Solids, Whey Protein Concentrate (milk, soy lecithin), Fractionated Coconut Oil, Calcium Phosphate Dibasic, Tripotassium Citrate, Walnut Oil, Citric Acid Esters of Mono- and Diglycerides of Fatty Acids, Trisodium Citrate, L-Threonine, Magnesium Chloride, Sodium Chloride, L-Phenylalanine, Choline Bitartrate, L-Lysine Acetate, L-Tyrosine, L-Glutamine, L-Isoleucine, L-Valine, L-Leucine, M-Inositol, L-Ascorbic Acid, L-Histidine, L-Methionine, L-Cystine, Taurine, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Niacinamide, Calcium D-Pantothenate, Manganese Sulfate, Copper Sulfate, Riboflavin, Vitamin A Acetate, Pyridoxine Hydrochloride, Thiamine Hydrochloride, Sodium Molybdate, Potassium Iodide, Chromium Chloride, Folic Acid, Sodium Selenite, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin. • Intake is determined by a medical professional and is dependent on the age, body weight and medical condition of the patient. • Not intended for use as the sole source of nutrition. Consider supplementation of essential fatty acids and micronutrients depending on individual’s needs. • Not for parenteral use. Monogen Precautions: Nutrition Information: Administration: For oral or tube feeding: 1. Measure the required amount of warmed water into a container. 2. Add the prescribed amount of Monogen to the water. The scoop provided in the can measures 5 g. 3. Cover and shake until the powder has dissolved. The following are guidelines for achieving desired concentrations: Concentration Powder Water Final Volume 22 kcal/30 mL 17.5 g 90 mL 100 mL (3 1/2 Scoops) (3 fl oz) 30 kcal/30 mL 24 g 80 mL 100 mL (5 Scoops) (2 1/2 fl oz) Unpacked, level scoops are approximations only. For accuracy, use a scale. • Once prepared, the formula should be stored in a refrigerator and kept no longer than 24 hours from the time of preparation. Shake or stir Monogen immediately before use. Storage: Store in a cool, dry place. Once opened, use contents within one month. Replace lid firmly after use. 175 Nutrition Information: Monogen® Other Nutritionals A milk protein-based powder, low in fat, and high in medium chain triglycerides (MCT). A product for individuals over 1 year of age. 176 Main Features: Indications: • • • • • Long chain fatty acid oxidation disorders • Hyperlipoproteinemia type 1 • Other lipid and lymphatic disorders where a low fat, high MCT diet is indicated 26% of calories from fat 84% of fat as MCT Now contains DHA and ARA Contains complete profile of vitamins and minerals including trace elements • Osmolality (mOsm/kg): Dilution .73 kcal/mL: 235 mOsm/kg 1 kcal/mL: 289 mOsm/kg • Displacement: 0.67 mL/g Ordering Information: Product Code 106033 Product Packaging 6 x 400 g (14.1 oz) Calories Per Can 1776 Nutrients Per 100 g Per 100 kcal Calories, kcal (kJ) 444 (1871) 100 (421) Protein Equivalent, g 12.9 2.9 Fat, g 12.9 2.9 MCT, g 10.8 2.4 LCT, g 2.10 0.5 Linoleic acid, g 0.90 0.2 a-Linolenic acid, g 0.17 0.04 ARA, mg 60 13.5 DHA, mg 60 13.5 Carbohydrate, g 69.1 15.6 Vitamins Vitamin A, IU (mcg R.E.) 974 (293) 219 (66.0) 428 (10.7) 96.4 (2.4) Vitamin D3, IU (mcg) 1.5 (0.99) Vitamin E, IU (mg a T.E.) 6.6 (4.4) Vitamin K, mcg 16.1 3.6 Thiamin, mg 0.41 0.09 Riboflavin, mg 0.44 0.10 0.4 0.09 Vitamin B6, mg Vitamin B12, mcg (mg) 0.6 (0.0006) 0.14 (0.00014) Niacin, mg 2.7 0.61 Folic Acid, mcg (mg) 61 (0.061) 13.7 (0.0137) Nutrients Per 100 g Per 100 kcal Pantothenic Acid, mg 2 0.45 Biotin, mcg (mg) 12.8 (0.0128) 2.9 (0.0029) Vitamin C, mg 54.1 12.2 Choline, mg 90.9 20.5 Inositol, mg 79.8 18.0 Minerals Calcium, mg 321 72.3 Phosphorous, mg 193 43.5 Magnesium, mg 39.6 8.9 Iron, mg 6 1.4 Zinc, mg 4.1 0.92 Manganese, mg 0.32 0.07 Copper, mcg (mg) 324 (0.324) 73.0 (0.073) Iodine, mcg (mg) 72.3 (0.0723)16.3 (0.0163) Molybdenum, mcg (mg)18.8 (0.0188) 4.2 (0.0042) Chromium, mcg (mg) 9.5 (0.0095) 2.1 (0.0021) Selenium, mcg (mg) 10.4 (0.0104) 2.3 (0.0023) Sodium, mg 192 43.2 Potassium, mg 372 83.8 Chloride, mg 284 64.0 Ingredients: Maltodextrin, Skim Milk, Refined Vegetable Oil (Modified Palm Kernel And/Or Coconut Oil [Medium Chain Triglycerides]), Whey (Milk), Caseinate (Milk), Walnut Oil, Corn Syrup Solids, Sodium Citrate, Potassium Chloride, Calcium Carbonate, Magnesium Hydrogen Phosphate, Choline Chloride, M. Alpina Oil, C. Cohnii Oil, L-Valine, Inositol, L-Tryptophan, L-Ascorbic Acid, Sodium L-Ascorbate, Taurine, L-Isoleucine, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Niacinamide, DL-Alpha Tocopherol, Calcium D-Pantothenate, Copper Sulfate, Manganese Sulfate, Pyridoxine Hydrochloride, Thiamin Chloride Hydrochloride, Vitamin A Acetate, Riboflavin, Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Sodium Selenite, Vitamin D3. Contains: Milk, Walnut Oil, Coconut Oil. • Intake is determined by a medical professional and is dependent on the age, body weight and medical condition of the patient. • Not intended for use as the sole source of nutrition. Consider supplementation of essential fatty acids and micronutrients depending on individual’s needs. • Not for parenteral use. Monogen Important Information: ing Comon! So Administration: For oral or tube feeding: 1. Measure the required amount of warmed water into a container. 2. Add the prescribed amount of Monogen to the water. The scoop provided in the can measures 5.6 g (level and unpacked). 3. Cover and shake until the powder has dissolved. The following are guidelines for achieving desired concentrations: Concentration 22 kcal/30 mL (.73 kcal/mL) 30 kcal/30 mL (1 kcal/mL) Powder 16.8 g Water 90 mL Final Volume 100 mL 22.8 g 80 mL 100 mL (3 Scoops) (3 fl oz) (4 Scoops) (2 1/2 fl oz) Unpacked, level scoops are approximations only. For accuracy, use a scale. • Once prepared, the formula should be stored in a refrigerator and kept no longer than 24 hours from the time of preparation. Shake or stir Monogen immediately before use. Storage: Store in a cool, dry place. Once opened, use contents within one month. Replace lid firmly after use. 177 Other Nutritionals A high energy medium chain triglyceride (MCT) emulsion. 178 Main Features: Indications: • • • • • • • • • • • • • Simplifies addition of MCTs to the diet Emulsified for better mixing 50% MCT and 50% water Unflavored High energy: 4.5 kcal/mL Osmolality: 10 mOsm/kg Density: 0.97 g/mL For oral or enteral use Can be used in beverages and foods Conditions where MCTs are part of dietary management Conditions managed by the ketogenic diet Long-chain fatty acid oxidation disorders Other inborn errors of metabolism where MCTs may be beneficial Nutrition Information: Administration: Storage: Nutrients Energy, kcal (kJ) Protein, g Carbohydrate, g Fat, g Saturated, g + Trans, g MCT, g (%) Sodium, mg • The quantity of Liquigen should be determined by a healthcare professional only and is dependent on the age, bodyweight and medical condition of the patient. Liquigen may require dilution for children less than 5 years of age. • Shake well before use. • Store between 4°-25°C (39°-77°F). • Once opened store in a refrigerator and use within 14 days. • Always replace the bottle lid after use. Per 100 mL Per 250 mL 450 (1880) 1125 (4700) 0 0 0 0 50.0 125 47.0 118 0 0 45.4 (96.4) 118 (96.4) 5.0 13 Ingredients: Precautions: Refined Vegetable Oil (Modified Palm Kernel and/or Coconut Oil (Medium Chain Triglycerides)), Water, Citric Acid Esters of Mono- and Diglycerides, Mono and Diglycerides, Citric Acid. • Use under medical supervision. • Not suitable for use as a sole source of nutrition. • Not for parenteral use. Liquigen Liquigen ® Ordering Information: Product Code 71957 (Case) 71957-3 (Unit) Product Packaging 3 x 4 x 250 mL (8.5 fl oz) 4 x 250 mL (8.5 fl oz) Calories Per Bottle 1125 1125 179 Other Nutritionals A powdered product providing fat and carbohydrate for increased caloric intake. 180 Main Features: Indications: • Calorically dense – 1 scoop (5 g) provides 25 kcal • Tolerance – unique dual energy source of fat and carbohydrate • Super soluble without altering the taste or texture of foods and beverages • Milk protein-free • Osmolality (1:3 dilution): 310 mOsm/kg • 1 gram contributes approximately 0.93 mOsm when added to a solution • PRSL of less than 0.017 mOsm/g • Energy distribution: Carbohydrate 59% Fat (MCT 35% / LCT 65%)41% • Displacement 0.77 mL/g • Conditions where a high energy, low fluid, low electrolytes diet is indicated • Protein restricted diets • Disorders of protein and amino acid metabolism • Malabsorptive states • Modular diets • Catabolic states (e.g. burns, trauma, post-operative stress) • Suitable for oral and tube feedings Ordering Information: Product Code 118262 Product Packaging 6 x 400 g (14.1 oz) Calories Per Can/Sachet 1968 Nutrition Information: Household Measures: Nutrients Per 100 g Calories 492 Protein, g None Fat, g 22.3 Saturated, g 13.8 + Trans, g 0 Monounsaturated, g 2.5 Polyunsaturated, g 4.8 Carbohydrate, g 72.7 Minerals Sodium, mg ≤ 20 Potassium, mg ≤ 5 Chloride, mg ≤ 20 Calcium, mg ≤ 5 Phosphorus, mg ≤ 5 (All measures are level and unpacked) Ingredients: Hydrolyzed Cornstarch, Blend of Refined Vegetable Oils (Corn, Coconut), Medium Chain Triglycerides (Fractionated Coconut Oil, Palm Kernel Oil), Mono and Diglycerides, Diacetyl Tartaric Acid Esters of Monoglycerides. Measure 1 Scoop 1 tsp 1 Tbsp 1/4 cup 1/2 cup 1 cup 1 sachet Weight 5 g 2.6 g 8.5 g 30 g 56 g 117 g 10 g Calories 25 13 42 148 276 576 49 Based on standard dry, household measurements. All measurements are level and unpacked. Household measurements are approximations only. For accuracy use a scale. (1 cup = 240 mL; 1/2 cup = 120 mL; 1/3 cup = 80 mL; 1/4 cup = 60 mL) Displacement Factor: 0.77 mL/g Precautions: • Not for parenteral use. • Not suitable as a sole source of nutrition. Administration: • Intake to be determined by a medical professional and is dependent on the age, body weight and medical condition of the patient. Duocal Duocal® For oral or tube feeding: 1.Measure the prescribed amount of Duocal. 2.Add powder to the required volume of liquid and/or soft food and stir continuously until the powder has dissolved. 3.Unused foods mixed with Duocal should be refrigerated and used within 24 hours. Shake or stir immediately before serving. Storage: • Store unopened can at room temperature. Once opened, replace lid on can and store in a cool, dry place (not in refrigerator) and use within one month. 181 Other Nutritionals A powdered, concentrated source of energy (maltodextrin). 182 Main Features: Indications: • Concentrated carbohydrate energy source – 1 scoop provides approximately 5 g (~20 kcal) • Easily digestible maltodextrin • Completely soluble in foods and drinks • Neutral taste – does not alter the taste of foods and drinks • Manufactured in a dairy-free environment • Osmolality (10% solution): 104 mOsm/kg • 1 gram contributes approximately 1.04 mOsm when added to a solution • PRSL < 0.01 mOsm/10 g • Displacement: 0.57 mL/g • Conditions where a high energy, low fluid or modular diet is indicated. • For the dietary management of energy needs. Nutrition Information: Household Measures: Nutrients Per 100 g Calories384 Carbohydrate, g 96.0 Protein, g 0 Fat, g 0 Minerals Sodium, mg 2.0 Potassium, mg 0 (All measures are level and unpacked) Ingredients: Maltodextrin. Measure 1 Scoop ½ tsp 1 tsp 1 Tbsp ¼ cup ⅓ cup ½ cup 1 cup Weight 5 g 1.2 g 2.4 g 7.3 g 29.0 g 38.7 g 58.0 g 116 g Calories ~20 kcal 4.6 kcal 9.3 kcal 27.8 kcal 111 kcal 148 kcal 223 kcal 445 kcal Based on standard dry, household measurements. All measurements are level and unpacked. Household measurements are approximations only. For accuracy use a scale. (For standard dry measures, 1 cup = 240 mL) Ordering Information: Product Code 89461 Product Packaging 12 x 400 g (14.1 oz) Calories Per Can 1536 Precautions: • Not for parenteral use. • Not suitable as a sole source of nutrition. Administration: Intake to be determined by a medical professional and is dependent on the age, body weight and medical condition of the patient. Polycal Polycal™ A scoop is provided in the can and holds approximately 5 g of powder (~20 kcal). • Beverages: Sprinkle the required amount of powder into the beverage and stir well. • Foods: For best results, mix powder with sufficient liquid to form a smooth paste before stirring into hot or cold food. Storage: Store unopened can in a cool, dry place. Once opened, replace lid on can and store in a cool, dry place (not in refrigerator) and use contents within 1 month. Unfinished beverages and foods should be stored in a refrigerator for up to 24 hours. 183 Complete Amino Acid Mix Other Nutritionals An unflavored, powdered mixture of essential and non-essential amino acids. 184 Main Features: Indications: • Balanced mixture of essential and non-essential amino acids • Supplements increased protein needs in enteral formulas • Complete Amino Acid Mix provides 4 g of protein equivalent per 5 g of powder • Osmolality (5% w/v): 360 mOsm/kg • Approximate displacement: 0.75 mL/g • Conditions in which a nutritionally complete feeding is not suitable or a modular approach is required • Conditions where an oligoallergenic diet is indicated (e.g. individuals with intolerance to milk protein or other whole protein) • Intractable malabsorption • Feeding difficulties in post-operative conditions • Chronic intestinal diseases (e.g. Crohn’s disease) • Short bowel syndrome following intestinal resection Ordering Information: Product Code 553341 Product Packaging 6 x 200 g (7 oz) Calories Per Can 656 Ingredients: L-Lysine L-Glutamate, L-Leucine, L-Arginine, Nutrients Per 100 g L-Proline, L-Valine, L-Aspartic Acid, Glycine, Calories328 L-Isoleucine, L-Threonine, L-Phenylalanine, Protein Equivalent, g 82 L-Histidine, L-Serine, L-Tyrosine, L-Alanine, Fat, g None L-Cystine, L-Tryptophan, L-Methionine, Carbohydrate, g None L-Glutamine, L-Glutamic Acid. Amino Acids, g L-Alanine 3.5 Household Measures: L-Arginine 7.66 (all measures are level and unpacked) L-Aspartic Acid 6.39 L-Cystine 2.4 Measure Weight Protein Equivalent L-Glutamic Acid 8.17 1/2 tsp 1.4 g 1.15 Glycine 6.0 1 tsp 2.9 g 2.38 L-Histidine 4.38 1/2 Tbsp 4.4 g 3.61 L-Isoleucine 5.95 1 Tbsp 9.5 g 7.79 L-Leucine 10.22 Based on standard dry, household L-Lysine 7.55 measurements. All measurements are level L-Methionine 1.65 and unpacked. Household measurements are approximations only. For accuracy use a scale. L-Phenylalanine 4.5 L-Proline 7.0 Precautions: L-Serine 4.29 • Intake should be determined L-Threonine 5.0 by a doctor or dietitian and is L-Tryptophan 2.0 dependent on the age, body L-Tyrosine 4.3 weight and medical condition L-Valine 6.5 of the patient. Complete L-Glutamine 0.7 Amino Acid Mix must not be used as the sole source of nutrition. Micronutrients and energy must be supplied to meet nutrient needs and to ensure proper growth. • Not for parenteral use. Administration: • The recommended feeding concentration is 5% w/v (e.g. 5 g powder to 100 mL of water). Per 5 g of powder, Complete Amino Acid Mix provides 4 g of protein. • Complete Amino Acid Mix should be weighed on a scale that reads in grams. • It is best served as a chilled drink, mixed with water, fruit juices or other formulas. Complete Amino Acid Mix may also be added to soft, moist foods, such as applesauce. Complete Amino Acid Mix Nutrition Information: Storage: • Store in a cool, dry place. Once opened, use within one month. Always replace container lid after use. • Once reconstituted, the prepared feeding should be stored in a refrigerator and must not be kept longer than 24 hours from the time of preparation. Stir or shake immediately before serving. 185 Essential Amino Acid Mix Other Nutritionals An unflavored, powdered mixture of essential amino acids, including cystine and histidine. 186 Main Features: Indications: • Balanced mixture of essential amino acids • Essential Amino Acid Mix provides 4 g of protein equivalent per 5 g of powder • Osmolality (5% w/v): 360 mOsm/kg • Approximate displacement: 0.75 mL/g • Dietary management of urea cycle disorders • Conditions in which a nutritionally complete feeding is not suitable or a modular approach is required L-Histidine3.78 Based on standard dry, household L-Isoleucine10.4 measurements. All measurements are level L-Leucine16.17 and unpacked. Household measurements are L-Lysine13.25 approximations only. For accuracy use a scale. L-Methionine3.78 L-Phenylalanine5.67 L-Threonine11.35 Precautions: L-Tryptophan2.36 • Intake should be determined L-Tyrosine9.46 by a doctor or dietitian and is L-Valine14.56 dependent on the age, body Ordering Information: Product Code 553342 Product Packaging 6 x 200 g (7 oz) Calories Per Can 632 Household Measures: (all measures are level and unpacked) Nutrients Per 100 g Calories316 Measure Weight Protein Equivalent Protein Equivalent, g 79 1/2 tsp 1.4 g 1.11 Fat, g None 1 tsp 2.7 g 2.13 Carbohydrate, g None 1/2 Tbsp 4.1 g 3.24 Amino Acids, g 1 Tbsp 9.0 g 7.11 L-Cystine3.78 Ingredients: L-Lysine Acetate, L-Leucine, L-Valine, L-Threonine, L-Isoleucine, L-Tyrosine, L-Phenylalanine, L-Histidine, L-Cystine, L-Methionine, L-Tryptophan. weight and medical condition of the patient. Essential Amino Acid Mix must not be used as the sole source of nutrition. Micronutrients and energy must be supplied to meet nutrient needs and to ensure proper growth. • Not for parenteral use. Administration: • The recommended feeding concentration is 5% w/v (e.g. 5 g powder to 100 mL of water). Per 5 g of powder, Essential Amino Acid Mix provides 4 g of protein. • Essential Amino Acid Mix should be weighed on a scale that reads in grams. • It is best served as a chilled drink, mixed with water, fruit juices or other formulas. It may also be added to soft, moist foods, such as applesauce. Essential Amino Acid Mix Nutrition Information: Storage: • Store in a cool, dry place. Once opened, use within one month. Always replace container lid after use. • Once reconstituted, the prepared feeding should be stored in a refrigerator and must not be kept longer than 24 hours from the time of preparation. Stir or shake immediately before serving. 187 A concentrated, powdered vitamin, mineral and trace element preparation designed to help meet the micronutrient requirements of older children (11 years and older) and adults. Main Features: Indications: • One 7 g packet supplies the majority of vitamins and minerals needed to help meet the DRI of individuals 11 years and older • Restrictive therapeutic diets Other Nutritionals Ordering Information: 188 Product Code 10685 Product Packaging 30 x 7 g Calories Per Packet 0.2 Ingredients: Administration: Nutrients Per 7 g packet Calories0.2 Protein, g 0.02 Fat, g None Carbohydrate, g 0.04 Vitamins Vitamin A, IU (mcg R.E.) 2664 (800) Vitamin D, IU (mcg) 400 (10) Vitamin E, IU (mg a T.E.) 13.5 (9) Vitamin K, mcg 70 Thiamin, mg 1.2 Riboflavin, mg 1.4 Vitamin B6, mg 1.6 Vitamin B12, mcg 5 Niacin, mg 20 Folic Acid, mcg 700 Pantothenic Acid, mg 5 Biotin, mcg 150 Vitamin C, mg 50 Minerals Calcium, mg 1000 Phosphorus, mg 775 Magnesium, mg 300 Iron, mg 15.1 Zinc, mg 11.1 Manganese, mg 1.5 Copper, mcg 1505 Iodine, mcg 150 Molybdenum, mcg 70 Chromium, mcg 30 Selenium, mcg 75 Sodium, mg 8.8 Potassium, mg <1.4 Chloride, mg <0.35 Calcium Phosphate Dibasic, Magnesium Acetate, Guar Gum, L-Ascorbic Acid, Ferrous Sulfate, Dextrose, Zinc Sulfate, Nicotinamide, DL-Alpha Tocopheryl Acetate, Copper Gluconate, Calcium D-Pantothenate, Manganese Sulfate, Pyridoxine Hydrochloride, Thiamin Mononitrate, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Sodium Molybdate, Sodium Selenite, D-Biotin, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin. • Mix one sachet of Phlexy-Vits with one sachet of dry powdered Phlexy-10 Drink Mix. Add a small amount of water and mix to a smooth paste. Add the remaining water to give a final volume of approximately 100 mL. Alternatively, mix one sachet of Phlexy-Vits to a smooth paste with a small amount of lemonade or fruit juice (approx. 45 mL (1.5 fl oz). Dilute to a final volume of 150 mL (5 fl oz). The amount of lemonade/juice and water used will vary according to taste. Storage: Household Measures: (all measures are level and unpacked) MeasureWeight 1/4 tsp 0.7 g 1/2 tsp 1.4 g 1 tsp 3g 1 Tbsp 10 g Based on standard dry, household measurements. All measurements are level and unpacked. Household measurements are approximations only. For accuracy use a scale. Precautions: • Intake should be determined by a doctor or dietitian and is dependent on the age, body weight and medical condition of the patient. Phlexy-Vits must not be used as the sole source of nutrition. Phlexy-Vits Phlexy-Vits Nutrition Information: • Store in a cool, dry place. Once opened, a sachet should be stored in an airtight container and used within 2-3 days. 189 Single Amino Acids Other Nutritionals Pure amino acid powder. 190 Main Features: Directions for Use: • An amino acid product for the dietary management of inborn errors of metabolism. • Important: For use under medical supervision. This product is nutritionally incomplete. Not for parenteral use. • Warning: Do not heat, bake or add to hot food or beverages above 54°C (130°F). • Storage: Keep at controlled room temperature 20º-25ºC (68º-77ºF). Protect from heat, humidity and light. After opening, cover with resealable lid and store in a cool dry place. • Use as directed by physician or dietitian. • Suggest Mixing Dilution: A 10% solution can be made by mixing 1 g of amino acids into 100 mL of sterilized water. Every 1 mL of solution provides 10 mg of amino acids. Ordering Information: Product Code L-ARGININE GLYCINE L-ISOLEUCINE L-LEUCINE L-TYROSINE L-VALINE Product Code 0120A 0130G 0140I 0150L 0160T 0170V Product Packaging 1 - 50g bottle 1 - 50g bottle 1 - 50g bottle 1 - 50g bottle 1 - 50g bottle 1 - 50g bottle ur ce s Resources so Re 191 ELIMINATE COW’S MILK PROTEIN AND/OR OTHER APPROPRIATE ALLERGENS FROM DIET Resources Cow Milk Allergy / Multiple Food Protein Intolerance Cow Milk Allergy / Multiple Food Protein Intolerance References: 1. de Boissieu et al. Allergy to Extensively Hydrolyzed Cow Milk Proteins in Infants: Identification and Treatment with an Amino AcidBased Formula. J Pediatr 1997;131:744-747. YES IS PATIENT AT HIGH RISK OF ANAPHYLACTIC REACTION TO AN OFFENDING ALLERGEN?* a NO 2. de Boissieu et al. Allergy to Extensively Hydrolyzed Cow’s Milk Proteins in Infants: Safety and Duration of Amino Acid-Based Formula. J Pediatr 2002;141:271-73. <2 YEARS OLD? 2+YEARS OLD? a AABF as a sole source or supplement to diet as directed by healthcare professional Elimination diet and a hypoallergenic formula as directed by healthcare professional Hypoallergenic formula as sole source or supplement as directed by healthcare professional 3. de Boissieu et al. Time Course of Allergy to Extensively Hydrolyzed Cow’s Milk Proteins in Infants. J Pediatr 2000;136:119 – 20. 4. Fiocchi et al. Diagnosis and Rationale for Action against Cow’s Milk Allergy (DRACMA): A summary report. J Allergy Clin Immunol 2010;1119 -1128. NO MEETING NUTRIENT REQUIREMENTS? 6. Vanderhoof et al. Intolerance to Protein Hydrolyzed Infant Formulas: an Under Recognized cause of Gastrointestinal Symptoms in Infants J Pediatr 1997;131:741-744. CONSIDER NEOCATE® Resources 5. Sampson et al. Safety of An Amino Acid-Derived Infant Formula in Children Allergic to Cow Milk. Pediatrics 1992;90:463 – 465. 0-1 year: Neocate® DHA / ARA 6+ months: Neocate® Nutrab 1+ years: Neocate® Junior with Prebiotic Fibre (Unflavoured, Vanilla, Strawberry) Neocate® Junior (Unflavoured, Chocolate) Neocate® Splash (Unflavoured, Grape, Orange-Pineapple, Tropical Fruit) YES IS COST OF FORMULA AN c ISSUE? * Individual requirements as directed by healthcare professional NO Continue with Elimination diet YES NO IS extensively hydrolyzed formula (eHF) TOLERATED? YES Continue with eHF as directed by healthcare professional Monitor nutritional status TM a Hypoallergenic formula includes AABF (Amino Acid-Based Formula) and eHF (Extensively Hydrolyzed Formula) Neocate Nutra is a supplemental semi-solid elemental food for 6+ months c In settings where the cost of an AABF is lower, the use of an AABF may be equally reasonable. * DRACMA Guidelines (Fiocchi et al, J Allergy Clin Immunol 2010) b 192 193 COMBINE IF MEDICALLY APPROPRIATE NUTRITION THERAPY ELIMINATION DIET Empiric* or Tailored PHARMACOLOGIC THERAPY 7 References: 1. American Dietetic Association. Pediatric Nutrition Care Manual®. Eosinophilic Esophagitis http://www.peds.nutritioncaremanual.org Accessed July 6, 2011. ELEMENTAL DIET 3. Feuling and Noel. Medical and Nutritional Management of Eosinophilic Esophagitis in Children. Nutr Clin Pract 2010;(25):166 – 174. Nutritional status, age and social needs of patient are key in determining appropriate treatment. 4. Haas. Development, Mealtime Dynamics and Nutrition: Use of an Amino Acid-Based Semi-Solid Supplement in a Child with Eosinophilic Esophagitis. Nutr Clin Pract 2011;(26)19. CONSIDER NEOCATE® MEETING NUTRIENT REQUIREMENTS? 0-1 year: Neocate DHA / ARA 6+ months: Neocate® Nutrab 1+ years: Neocate® Junior with Prebiotic Fibre (Unflavoured, Vanilla, Strawberry) Neocate® Junior (Unflavoured, Chocolate) Neocate® Splash (Unflavoured, Grape, Orange-Pineapple, Tropical Fruit) ® Supplement with AABFb NO YES MEETING NUTRIENT REQUIREMENTS? Supplement with AABFb NO YES Individual requirements as directed by healthcare professional Resources Eosinophilic Esophagitis 2. Boyce et al. Guidelines for the Diagnosis and Management of Food Allergy in the United States: Report of the NIAID-Sponsored Expert Panel. J Allergy Clin Immunol.2010;S1 – 58. COMBINATION OF ELEMENTAL AND ELIMINATION DIET * 2-7 food elimination > Routine medical and nutritional assessments. > Reintroduce food individually as medically feasible/tolerated. 5. Liacouras et al. Eosinophilic Esophagitis: Updated Consensus Recommendations for Children and Adults. J Allergy Clin Immunol 2011;(128) 3 – 20 e6. Epub 2011 Apr 7. 6. Putnam. Evaluation of the Child who has Eosinophilic Esophagitis. In Furuta GT, Atkins D & Alam R, eds. Eosinophilic Gastrointestinal Diseases, Immunol Allergy Clin North Am Philadelphia, PA: Elsevier 2009; 19–27. 7. Hait et al. Neocate® Nutra is as effective as sucralose as a delivery vehicle for oral viscous budesonide to treat eosinophilic esophagitis in children. J Pediatr Gastroenterol Nutr. 2013; 57 (S1): E4. > Routine medical and nutritional assessments. > Consider nutritional therapy as long-term situation. TM TM a b 194 Resources Eosinophilic Esophagitis Neocate Nutra is a supplemental semi-solid elemental food for 6+ months AABF – Amino Acid-Based Formula 195 Resources Short Bowel Syndrome FUNCTIONAL GI TRACT? YES NO Short Bowel Syndrome References: 1. Andorsky et al. Nutritional and Other Postoperative Management of Neonates with Short Bowel Syndrome Correlates with Clinical Outcomes. J Pediatr 2001;139:27-33. 2. Becker. Cow’s Milk Allergy in a Preterm Infant: A Case Presentation ICAN: Infant, Child, & Adolescent Nutrition 2009;214 - 219. TRANSITION TO ENTERAL NUTRITION AS TOLERATED FULL ENTERAL NUTRITION INFANT AGE OF PATIENT? Resources CONSIDER NEOCATE® Neocate® DHA / ARA 6+ months: Neocate® Nutrab Individual requirements as directed by healthcare professional 3. Bines et al. Reducing Parenteral Requirement in Children with Short Bowel Syndrome: Impact of an Amino Acid-Based Complete Infant Formula. J Pediatr Gastroenterol Nutr 1998;26:123-8. PARENTERAL NUTRITION 4. De Greef et al. The Influence of Neocate in Paediatric Short Bowel Syndrome on PN Weaning. J Nutr Metab 2010; pii: 297575. Epub 2010 May 31. 1+ YEARS Age-appropriate hypoallergenic formula as a sole source or supplement to the diet as directed by a a healthcare professional YES GI FUNCTION RETURNS? NO CONSIDER NEOCATE® 1+ years: Neocate® Junior with Prebiotic Fibre (Unflavoured, Vanilla, Strawberry) Neocate® Junior (Unflavoured, Tropical) Neocate® Splash (Unflavoured, Grape, Orange-Pineapple, Tropical Fruit)) p 6+ months: Neocate® Nutrab Individual requirements as directed by healthcare professional TM TM 196 TRANSITION TO ENTERAL NUTRITION AS TOLERATED COMBINATION OF ENTERAL AND PARENTERAL NUTRITION Breastmilk and/or hypoallergenic formula as a sole source or supplement to the diet as directed by a a healthcare professional 0-1 year: PARTIALLY a Hypoallergenic formula includes AABF (Amino Acid-Based Formula) and eHF (Extensively Hydrolyzed Formula) b Neocate Nutra is a supplemental semi-solid elemental food for 6+ months 197 Food and Nutrition Board, Institute of Medicine, National Academies (1997-2005) * Note: The tables (taken from the DRI reports, see www.nap.edu) present Recommended Dietary Allowances (RDAs) in bold type and Adequate Intakes (AIs) in ordinary type followed by an asterisk (*). RDAs and AIs may both be used as goals for individual intake. RDAs are set to meet the needs of almost all (97 to 98 percent) individuals in a group. For healthy breastfed infants, the AI is the mean intake. The AI for other life stage and gender groups is believed to cover needs of all individuals in the group, but lack of data or uncertainty in the data prevent being able to specify with confidence the percentage of individuals covered by this intake. Individual patient recommendations may vary. a Total Water includes all water contained in food, beverages, and drinking water Resources b 198 Based on g protein per kg body weight: • • • • • • • 1.52 g/kg/day for infants 0-6 months 1.5 g/kg/day for infants 7-12 months 1.1 g/kg/day for 1-3 0.95 g/kg/day for 4-13 y 0.85 g/kg/day for 14-18 y 0.80 g/kg/day for adults 1.1 g/kg/day for pregnant (using pre-pregnancy weight) and lactating women Life Stage Total Watera Carbohydrate Total Fiber Fat Linoleic Acid a-Linolenic Acid Protein Group (L/d) (g/d) (g/d) (g/d) (g/d) (g/d) (g/d) Infants 0-6 mo 7-12 mo 0.7* 0.8* 60* 95* ND ND 31* 30* 1.3* 1.7* 130 130 19* ND 25*ND 2.4* 3.3* 3.7* 3.7* 3.7* 3.7* 130 130 130 130 130 130 2.1* 2.3* 2.7* 2.7* 2.7* 2.7* 4.4* 4.6* 0.5* 0.5* 9.1* 11.0+ 7* 10* 0.7* 0.9* 13 19 31* ND 38* ND 38*ND 38* ND 30* ND 30* ND 12* 16* 17* 17* 14* 14* 1.2* 1.6* 1.6* 1.6* 1.6* 1.6* 34 52 56 56 56 56 130 130 130 130 130 130 26* 26* 25* 25* 21* 21* ND ND ND ND ND ND 10* 11* 12* 12* 11* 11* 1.0* 1.1* 1.1* 1.1* 1.1* 1.1* 34 46 46 46 46 46 3.0* 3.0* 3.0* 175 175 175 28* 28* 28* ND ND ND 13* 13* 13* 1.4* 1.4* 1.4* 71 71 71 3.8* 3.8* 3.8* 210 210 210 29* 29* 29* ND ND ND 13* 13* 13* 1.3* 1.3* 1.3* 71 71 71 Children 1-3 y 4-8 y Males 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y > 70 y Females 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y >70 y Pregnancy 14-18 y 19-30 y 31-50 y Lactation 14-18 y 19-30 y 31-50 y Vitamins Life Stage Vitamin A Group (mcg/d) Vitamin D Vitamin E Vitamin K Thiamin Riboflavin Niacin Vitamin B6 Folate Vitamin B12 Pantothenic Biotin Choline Vitamin C (mcg/d) (mcg/d) Acid (mg/d) (mcg/d) (mg/d) (mg/d) (mcg/d) (mg/d) (mcg/d) (mg/d) (mg/d) (mg/d) (mg/d) Infants 0-6 mo 7-12 mo 0.2* 0.3* 0.3* 0.4* 2* 4* 0.1* 0.3* 30* 55* 0.5 0.6 0.5 0.6 6 8 0.5 0.6 11 15 15 15 15 15 60* 75* 120* 120* 120* 120* 0.9 1.2 1.2 1.2 1.2 1.2 0.9 1.3 1.3 1.3 1.3 1.3 12 16 16 16 16 16 1.0 1.3 1.3 1.3 1.7 1.7 15 15 15 15 15 20 11 15 15 15 15 15 60* 75* 90* 90* 90* 90* 0.9 1.0 1.1 1.1 1.1 1.1 0.9 1.0 1.1 1.1 1.1 1.1 12 14 14 14 14 14 750 770 770 15 15 15 15 15 15 75* 90* 90* 1.4 1.4 1.4 1.4 1.4 1.4 1,200 1,300 1,300 15 15 15 19 19 19 75* 90* 90* 1.4 1.4 1.4 1.6 1.6 1.6 400* 500* 10* 10* 4* 5* 300 400 15 15 6 7 600 900 900 900 900 900 15 15 15 15 15 20 600 700 700 700 700 700 2.0* 2.5* 65* 80* 0.4* 0.5* 1.7* 1.8* 5* 6* 125* 150* 40* 50* 150 200 0.9 1.2 2* 3* 8* 12* 200* 250* 15 25 300 400 400 400 400 400 1.8 2.4 2.4 2.4 2.4 2.4 4* 5* 5* 5* 5* 5* 20* 25* 30* 30* 30* 30* 375* 550* 550* 550* 550* 550* 45 75 90 90 90 90 1.0 1.2 1.3 1.3 1.5 1.5 300 400 400 400 400 400 1.8 2.4 2.4 2.4 2.4 2.4 4* 5* 5* 5* 5* 5* 20* 25* 30* 30* 30* 30* 375* 400* 425* 425* 425* 425* 45 65 75 75 75 75 18 18 18 1.9 1.9 1.9 600 600 600 2.6 2.6 2.6 6* 6* 6* 30* 30* 30* 450* 450* 450* 80 85 85 17 17 17 2.0 2.0 2.0 500 500 500 2.8 2.8 2.8 7* 7* 7* 35* 35* 35* 550* 550* 550* 115 120 120 Resources § Dietary Reference Intakes (DRIs): Recommended Dietary Allowances and Adequate Intakes, Total Water, Macro-Nutrients, Vitamins and Elements Macronutrients Resources Resources Children 1-3 y 4-8 y Males 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y > 70 y Females 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y > 70 y Pregnancy 14-18 y 19-30 y 31-50 y Lactation 14-18 y 19-30 y 31-50 y 199 Life Stage Group Acceptable Macronutrient Distribution Ranges Copper Iodine Calcium Phosphorus Magnesium Fluoride Selenium Chromium (mcg/d) (mcg/d) (mg/d) (mg/d) (mg/d) (mg/d) (mcg/d) (mcg/d) Infants 0-6 mo 7-12 mo Iron Manganese Molybdenum Zinc (mg/d) (mg/d) (mcg/d) (mg/d) 200* 260* 100* 275* 30* 75* 0.01* 0.5* 15* 20* 0.2* 5.5 200* 110* 0.27* 220*130* 11 700 1,000 460 500 80 130 0.7* 1* 20 30 11* 15* 340 9071.2* 173 440 90101.5* 225 1,300 1,300 1,000 1,000 1,000 1,200 1,250 1,250 700 700 700 700 240 410 400 420 420 420 2* 3* 4* 4* 4* 4* 40 55 55 55 55 55 25* 35* 35* 35* 30* 30* 700120 81.9* 348 890 150112.2* 4311 900150 82.3* 4511 900150 82.3* 4511 900150 82.3* 4511 900150 82.3* 4511 1,300 1,300 1,000 1,000 1,200 1,200 1,250 1,250 700 700 700 700 240 360 310 320 320 320 2* 3* 3* 3* 3* 3* 40 55 55 55 55 55 21* 24* 25* 25* 20* 20* 700120 81.6* 348 890 150151.6* 439 900 150181.8* 458 900 150181.8* 458 900150 81.8* 458 900150 81.8* 458 1,300 1,000 1,000 1,250 700 700 400 350 360 3* 3* 3* 60 60 60 29* 30* 30* 1,000 220272.0+*5012 1,000 220272.0+*5011 1,000 220272.0+*5011 1,300 1,000 1,000 1,250 700 700 360 310 320 3* 3* 3* 70 70 70 44* 45* 45* 1,300 290102.6* 5013 1,300290 92.6* 5012 1,300290 92.6* 5012 0.003* 0.6* 2* 3* 2* 3 Children 1-3 y 4-8 y Macronutrient Fat n-6 polyunsaturated fatty acids* (linoleic acid) n-3 polyunsaturated fatty acids* (a-linolenic acid) Carbohydrate Protein Children, 1-3 y 30 - 40 5 -10 0.6 -1.2 45 - 65 5 - 20 Range (percent of energy) Children, 4-18 y 25 - 35 5 -10 0.6 -1.2 45 - 65 10 - 30 Adults 20 - 35 5 - 10 0.6 -1.2 45 - 65 10 - 35 Resources Minerals * Approximately 10% of the total can come from longer-chain n-3 or n-6 fatty acids. Males 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y > 70 y Females 9-13 y 14-18 y 19-30 y 31-50 y 51-70 y > 70 y Resources Pregnancy 200 14-18 y 19-30 y 31-50 y Lactation 14-18 y 19-30 y 31-50 y 201 www.Nutricia-NA.com • Provides an overview of Nutricia North America. www.Neocate.com/Canada • Provides educational information about dairy and soy milk allergies. • Educates doctors and caregivers about our hypoallergenic, 100% free amino acid-based products developed and tailored for infants and children. Resources www.MedicalFood.com and www.DietForLife.com • Interactive, online resources for the metabolic community with news, recipes, and community forums. • Feature online metabolic shops including convenient low protein foods, integral to low protein diets. 202 NOTES ................................................................................................................................................................................................................................................................. ................................................................................................................................................................................................................................................................. 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Product Reference Guide FOR CLINICIANS To order or for additional information, call (877) 636-2283 440 Armand-Frappier #230 • Laval, QC H7V 4B4 © 2016 Nutricia North America. All rights reserved. ZNAPG2016 07/16 9497350-30589
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