Download fetal icd-10 codes quick reference guide

FETAL ICD-10 CODES
QUICK REFERENCE GUIDE
Page
CONTENTS
1
Cardiac Anomalies
3
Chromosome Abnormalities
4
Central Nervous System Anomalies
5
Extremity Anomalies
6
Face / Neck Anomalies
7
Gastrointestinal Anomalies
7
Pulmonary Anomalies
7
Renal Anomalies
8
Skeletal Dysplasia
ICD-10-CM Coding Rules
• All fetal anomaly codes begin with a maternal
code followed by a fetal code.
• All of the leading codes begin with the letter
O and not the number zero.
• Maternal Category O35 is used to designate maternal care for
known or suspected fetal abnormality and damage.
• Where applicable, a 7th character is to be assigned to the
maternal code to identify the fetus for which the complication
code applies.
DISCLAIMER: The Fetal ICD-10 Quick Reference Guide is intended
to serve as a resource but should not take place of personal
verification of all codes when used for billing purposes.
FETAL CARDIAC ANOMALIES ABNORMAL CONNECTIONS
Atrial isomerism Common arterial trunk
Corrected transposition of great vessels
Double inlet ventricle
Double outlet left ventricle
Double outlet right ventricle
Mirror image atrial arrangement
Transposition of great vessels
AORTIC/MITRAL VALVES
Aortic arch hypoplasia (w/HLHS)
Aortic valve atresia
Aortic valve insufficiency
Aortic valve stenosis
Bicuspid aortic valve
Hypoplastic left heart syndrome
Mitral atresia
Mitral stenosis
Mitral valve insufficiency
Other malformations; aortic or mitral valve
O35.8XX1/Q20.6
O35.8XX1/Q20.0
O35.8XX1/Q20.5
O35.8XX1/Q20.4
O35.8XX1/Q20.2
O35.8XX1/Q20.1
O35.8XX1/Q20.6
O35.8XX1/Q20.3
O35.8XX1/Q23.4
O35.8XX1/Q23.0
O35.8XX1/Q23.1
O35.8XX1/Q23.0
O35.8XX1/Q23.1
O35.8XX1/Q23.4
O35.8XX1/Q23.2
O35.8XX1/Q23.2
O35.8XX1/Q23.3
O35.8XX1/Q23.8
CARDIAC SEPTAL ANOMALIES
Aortopulmonary septal defect
Atrial septal defect
Common AV canal
Ostium primum defect
Tetralogy of Fallot
Ventricular septal defect
O35.8XX1/Q21.4
O35.8XX1/Q21.1
O35.8XX1/Q21.2
O35.8XX1/Q21.2
O35.8XX1/Q21.3
O35.8XX1/Q21.0
GREAT ARTERIES
Aneurysmal arterial duct
Aortic arch hypoplasia (isolated)
Aortic atresia
Aortic dilation
Aortic stenosis
O35.8XX1/Q25.4
O35.8XX1/Q25.4
O35.8XX1/Q25.2
O35.8XX1/Q25.4
O35.8XX1/Q25.3
1
Coarctation of the aorta
Double aortic arch
Pulmonary artery atresia
Pulmonary artery stenosis
Right sided aortic arch
Vascular ring anomaly
GREAT VEINS
Absent ductus venosus
Partial anomalous pulmonary veins
Persistent azygous vein
Persistent left superior vena cava
Total anomalous pulmonary veins
PULMONARY/TRICUSPID VALVES
Ebstein’s anomaly
Hypoplastic right heart syndrome
Other malformations, pulmonary valve
Other malformations, tricuspid valve
Pulmonary valve atresia
Pulmonary valve regurgitation
Pulmonary valve stenosis
Tricuspid atresia Tricuspid regurgitation Tricuspid stenosis
VENTRICLES
Congenital heart block
Dextrocardia
Levocardia
Endocardial fibroelastosis
Levocardia
Non-compacted myocardium
Ventricular aneurysm
2
O35.8XX1/Q25.1
O35.8XX1/Q25.4
O35.8XX1/Q25.5
O35.8XX1/Q25.6
O35.8XX1/Q25.4
O35.8XX1/Q25.4
O35.8XX1/Q26.5
O35.8XX1/Q26.3
O35.8XX1/Q26.8
O35.8XX1/Q26.1
O35.8XX1/Q26.2
O35.8XX1/Q22.5
O35.8XX1/Q22.6
O35.8XX1/Q22.3
O35.8XX1/Q22.8
O35.8XX1/Q
O35.8XX1/Q22.2
O35.8XX1/Q22.1
O35.8XX1/Q22.4
O35.8XX1/Q22.8
O35.8XX1/Q22.4
O35.8XX1/Q24.6
O35.8XX1/Q24.0
O35.8XX1/Q24.1
O35.8XX1/I42.4
O35.8XX1/Q24.1
O35.8XX1/Q24.8
O35.8XX1/Q24.8
RHYTHM DISTURBANCES
Atrial flutter
Atrial premature beats
Congenital heart block
Sick sinus syndrome
Sinus bradycardia
Supraventricular tachycardia
Ventricular premature beats
Ventricular tachycardia O35.8XX1/I48.3
O35.8XX1/I49.1
O35.8XX1/Q24.6
O35.8XX1/I49.5
O35.8XX1/R00.1
O35.8XX1/I47.1
O35.8XX1/I49.3
O35.8XX1/I47.2
FETAL CHROMOSOME ABNORMALITIES
MONOSOMIES
Monosomy, nonmosaicisim
Monosomy, mosaicism
SEX CHROMOSOMES
45 X (Turner’s)
46 X, iso
47, XXX
47, XXY
47, XYY
Mosaic 45 X, 46 XX or XY
TRISOMIES
Triploidy
Trisomy 13
Trisomy 13, mosaic
Trisomy 13, translocation
Trisomy 18 Trisomy 18, mosaic
Trisomy 18, translocation
Trisomy 21 Trisomy 21, mosaic
Trisomy 21, translocation
Other autosomal trisomy
Other autosomal trisomy, mosaic
Other autosomal trisomy, partial
O35.8XX1/Q93.0
O35.8XX1/Q93.1
O35.8XX1/Q96.0
O35.8XX1/Q96.1
O35.8XX1/Q97.0
O35.8XX1/Q98.0
O35.8XX1/Q98.5
O35.8XX1/Q96.3
O35.8XX1/Q92.7
O35.8XX1/Q91.4
O35.8XX1/Q91.5
O35.8XX1/Q91.6
O35.8XX1/Q91.0
O35.8XX1/Q91.1
O35.8XX1/Q91.2
O35.8XX1/Q90.0
O35.8XX1/Q90.1
O35.8XX1/Q90.2
O35.8XX1/Q92.0
O35.8XX1/Q92.1
O35.8XX1/Q92.2
3
OTHER CHROMOSOMES
Balanced rearrangement, abnormal phenotypeO35.8XX1/Q95.2
Balanced rearrangement, normal phenotype O35.8XX1/Q95.1
Fragile X
O35.8XX1/Q99.2
Microdeletions
O35.8XX1/Q93.88
FETAL CENTRAL NERVOUS SYSTEM ANOMALIES
CENTRAL DEFECTS
Agenesis of the corpus callosum
O35.0XX1/Q04.0
Porencephaly
O35.0XX1/Q04.6
Septo-optic dysplasia
O35.0XX1/Q04.4
Vein of Galen aneurysm
O35.0XX1/Q28.2
CRANIAL Acrania
O35.0XX1/Q00.0
Anencephaly
O35.0XX1/Q00.0
Craniosynostosis
O35.0XX1/Q75.0
Encephalocele (other)
O35.0XX1/Q01.8
Frontal encephalocele
O35.0XX1/Q01.0
Occiptial encephalocele
O35.0XX1/Q01.2
HYDROCEPHALUS
Aqueductal stenosis
O35.0XX1/Q03.0
Congenital hydrocephalus, other
O35.0XX1/Q03.8
Holoprosencephaly
O35.0XX1/Q04.2
Hydranencephaly
O35.0XX1/Q04.3
Ventriculomegaly
O35.0XX1/Q04.8
MIGRATION PROBLEMS
Agenesis of the corpus callosum
O35.0XX1/Q04.0
Lissencephaly
O35.0XX1/Q04.3
Macrogyria
O35.0XX1/Q04.8
Microcephaly
O35.0XX1/Q02
Schizencephaly
O35.0XX1/Q04.6
4
POSTERIOR FOSSA
Cerebellar hypoplasia
Dandy-Walker cyst
Dandy-Walker variant
Enlarged cisterna magnae
Vermian hypoplasia/agenesis
FETAL EXTREMITY ANOMALIES
FOOT
Absent foot and toes, bilateral
Absent foot and toes, left
Absent foot and toes, right
Polydactyly
Syndactyly, both feet
Syndactyly, left foot
Syndactyly, right foot
Talipes calcaneovalgus
Talipes calcaneovarus
Talipes equinovarus
HAND
Absent hand and fingers, bilateral
Absent hand and fingers, left
Absent hand and fingers, right
Polydactyly
Syndactyly, both hands
Syndactyly, left hand
Syndactyly, right hand
LOWER EXTREMITY
Absence of leg (foot present), bilateral
Absence of leg (foot present), left
Absence of leg (foot present), right
Absence of limb, bilateral
Absence of limb, left
Absence of limb, right
Absence of lower leg and foot, bilateral
O35.0XX1/Q04.3
O35.0XX1/Q03.1
O35.0XX1/Q03.1
O35.0XX1/Q07.9
O35.0XX1/Q04.3
O35.8XX1/Q72.33
O35.8XX1/Q72.32
O35.8XX1/Q72.31
O35.8XX1/Q69.9
O35.8XX1/Q70.33
O35.8XX1/Q70.32
O35.8XX1/Q70.31
O35.8XX1/O66.4
O35.8XX1/O66.1
O35.8XX1/O66.0
O35.8XX1/Q71.33
O35.8XX1/Q71.32
O35.8XX1/Q71.31
O35.8XX1/Q69.0
O35.8XX1/Q70.13
O35.8XX1/Q70.12
O35.8XX1/Q70.11
O35.8XX1/Q72.13
O35.8XX1/Q72.12
O35.8XX1/Q72.11
O35.8XX1/Q72.33
O35.8XX1/Q72.22
O35.8XX1/Q72.21
O35.8XX1/Q72.33
5
Absence of lower leg and foot, left
Absence of lower leg and foot, right
Bowing of femur
Bowing of tibia/fibula
Reduction defect of femur, bilateral
Reduction defect of femur, left
Reduction defect of femur, right
Reduction of fibula, bilateral
Reduction of fibula, left
Reduction of fibula, right
Reduction of tibia, bilateral
Reduction of tibia, left
Reduction of tibia, right
UPPER EXTREMITY
Absence of arm (hand present), bilateral
Absence of arm (hand present), left
Absence of arm (hand present), right
Absence of forearm and hand, bilateral
Absence of forearm and hand, left
Absence of forearm and hand, right
Absence of limb, bilateral
Absence of limb, left
Absence of limb, right
Bowing of long bone
Reduction of radius, bilateral
Reduction of radius, left
Reduction of radius, right
Reduction of ulna, bilateral
Reduction of ulna, left
Reduction of ulna, right
Reduction of upper limb, bilateral
Reduction of upper limb, left
Reduction of upper limb, right
FETAL FACE/NECK ANOMALIES
Cervical teratoma
Cleft hard and soft palate
6
O35.8XX1/Q72.22
O35.8XX1/Q72.21
O35.8XX1/Q68.3
O35.8XX1/Q68.4
O35.8XX1/Q72.43
O35.8XX1/Q72.42
O35.8XX1/Q72.41
O35.8XX1/Q72.63
O35.8XX1/Q72.62
O35.8XX1/Q72.61
O35.8XX1/Q72.53
O35.8XX1/Q72.52
O35.8XX1/Q72.51
O35.8XX1/Q71.13
O35.8XX1/Q71.12
O35.8XX1/Q71.11
O35.8XX1/Q71.23
O35.8XX1/Q71.22
O35.8XX1/Q71.21
O35.8XX1/Q71.03
O35.8XX1/Q71.02
O35.8XX1/Q71.01
O35.8XX1/Q68.8
O35.8XX1/Q71.43
O35.8XX1/Q71.42
O35.8XX1/Q71.41
O35.8XX1/Q71.53
O35.8XX1/Q71.52
O35.8XX1/Q71.51
O35.8XX1/Q71.813
O35.8XX1/Q71.812
O35.8XX1/Q71.811
O35.8XX1/D48.7
O35.8XX1/Q35.5
Cleft hard palate
Cleft lip bilateral/cleft palate
Cleft lip unilateral/cleft palate
Cleft lip, bilateral
Cleft lip, median
Cleft lip, unilateral
O35.8XX1/Q35.1
O35.8XX1/Q37.0
O35.8XX1/Q37.1
O35.8XX1/Q36.0
O35.8XX1/Q36.1
O35.8XX1/Q36.9
Absent diaphragm
Anal atresia
Asplenia
Diaphragmatic hernia
Duodenal atresia
Esophageal atresia
Eventration of diaphragm Intestinal duplication
Omphalocele
Ovarian cyst
Situs inversus
Small bowel obstruction
Small stomach
Tracheo-esophageal fistula
O35.8XX1/Q79.1
O35.8XX1/Q42.3
O35.8XX1/Q89.01
O35.8XX1/Q79.0
O35.8XX1/Q41.0
O35.8XX1/Q39.0
O35.8XX1/Q79.1
O35.8XX1/Q43.4
O35.8XX1/Q79.2
O35.8XX1/Q50.1
O35.8XX1/Q89.3
O35.8XX1/Q41.9
O35.8XX1/Q40.2
O35.8XX1/Q39.1
Bronchial atresia
CHAOS
CPAM
Pulmonary sequestration
O35.8XX1/Q32.4
O35.8XX1/Q31.8
O35.8XX1/Q33.0
O35.8XX1/Q33.2
Horseshoe kidney
Infantile polycystic kidney
Multicystic kidney
Renal agenesis, bilateral
Renal agenesis, unilateral
Renal hypoplasia, bilateral
Renal hypoplasia, unilateral
O35.8XX1/Q63.1
O35.8XX1/Q61.11
O35.8XX1/Q61.4
O35.8XX1/Q60.1
O35.8XX1/Q60.0
O35.8XX1/Q60.4
O35.8XX1/Q60.3
FETAL GASTROINTESTINAL ANOMALIES
FETAL PULMONARY ANOMALIES
FETAL RENAL ANOMALIES
7
URETER/BLADDER
Extrophy of bladder, cloacal
O35.8XX1/Q64.12
Extrophy of bladder, unspecified
O35.8XX1/Q64.10
Hydronephrosis
O35.8XX1/Q62.0
Posterior urethral valves
O35.8XX1/Q64.2
Prune belly syndrome
O35.8XX1/Q79.4
Ureteral duplication
O35.8XX1/Q62.5
Ureterocele
O35.8XX1/Q64.6
Ureteropelvic obstruction
O35.8XX1/Q62.11
Ureterovesical obstruction
O35.8XX1/Q62.12
GENITALIA Ambiguous genitalia O35.8XX1/Q56.4
Cloaca
O35.8XX1/Q43.7
Hypospadia
O35.8XX1/Q54.1
Micropenis
O35.8XX1/Q55.62
Urethral stricture
O35.8XX1/Q64.32
SKELETAL DYSPLASIAS
Achondroplasia
O35.8XX1/Q77.4
Diastropic dysplasia
O35.8XX1/Q77.5
Osteogenesis imperfecta
O35.8XX1/Q78.0
Short rib syndrome
O35.8XX1/Q77.2
Thanatophoric dysplasia
O35.8XX1/Q77.1
Unspecified skeletal dysplasia
O35.8XX1/Q77.9
FETAL SPINE ANOMALIES
Arnold-Chiari w/hydrocephalus
O35.0XX1/Q07.02
Arnold-Chiari w/spina bifida
O35.0XX1/Q07.01
Arnold-Chiari w/spina bifida and hydrocephalusO35.0XX1/Q07.03
Cervical SB w/hydrocephalus
O35.8XX1/Q05.0
Cervical SB w/o hydrocephalus
O35.8XX1/Q05.5
Craniorachischisis
O35.8XX1/Q00.1
Hemivertebrae
O35.8XX1/Q76.49
Kyphosis (cervical)
O35.8XX1/Q76.412
Kyphosis (cerv-thoracic)
O35.8XX1/Q76.413
Kyphosis (thoracic)
O35.8XX1/Q76.414
Kyphosis (thoraco-lumbar)
O35.8XX1/Q76.415
8
Kyphosis (unspecified)
Lumbar SB w/hydrocephalus
Lumbar SB w/o hydrocephalus
Sacral SB w/hydrocephalus
Sacral SB w/o hydrocephalus
Sacrococcygeal teratoma
Scoliosis
Talipes calcaneovalgus
Talipes calcaneovarus
Talipes equinovarus
Thoracic SB w/hydrocephalus
Thoracic SB w/o hydrocephalus
Unspecified SB w/hydrocephalus
O35.8XX1/Q76.419
O35.8XX1/Q05.2
O35.8XX1/Q05.7
O35.8XX1/Q05.3
O35.8XX1/Q05.8
O35.8XX1/D48.0
O35.8XX1/Q76.3
O35.8XX1/O66.4
O35.8XX1/O66.1
O35.8XX1/O66.0
O35.8XX1/Q05.1
O35.8XX1/Q05.6
O35.8XX1/Q05.4
The Fetal Center at Children’s Memorial Hermann Hospital, affiliated
with the physicians at McGovern Medical School at UTHealth, is a
national leader in fetal diagnosis, fetal intervention and comprehensive fetal care for babies with congenital anomalies or
genetic abnormalities requiring treatment before or after birth.
A national referring center, The Fetal Center offers patients a
complete range of prenatal testing and fetal interventions with
a multidisciplinary, coordinated program for mother and child
before, during and after birth.
Contact Us:
Call: 832.325.7288
Email: [email protected]
Visit: childrens.memorialhermann.org/fetal/physician-resources
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Houston, TX 77030
9
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